Leon Rosenberg - Publications

Affiliations: 
1965-1991 Yale University Medical School, New Haven, CT, United States 
 1997- Molecular Biology Princeton University, Princeton, NJ 
Area:
Medical Genetics, Hematology, Oncology
Website:
https://molbio.princeton.edu/people/leon-rosenberg

119 high-probability publications. We are testing a new system for linking publications to authors. You can help! If you notice any inaccuracies, please sign in and mark papers as correct or incorrect matches. If you identify any major omissions or other inaccuracies in the publication list, please let us know.

Year Citation  Score
2014 Rosenberg LE. Four children and Yale: the making of a human geneticist: the Grover Powers lecture 2014. The Yale Journal of Biology and Medicine. 87: 379-87. PMID 25191153  1
2014 Rosenberg LE. DNA and other strands: the making of a human geneticist. Annual Review of Genomics and Human Genetics. 15: 1-26. PMID 24387667 DOI: 10.1146/annurev-genom-090413-025505  1
2008 Rosenberg LE. Legacies of Garrod's brilliance. One hundred years--and counting. Journal of Inherited Metabolic Disease. 31: 574-9. PMID 18836847 DOI: 10.1007/s10545-008-0985-8  0.01
2006 Rosenberg LE. 2005 William Allan Award address. Introductory speech for Francis S. Collins. American Journal of Human Genetics. 79: 419-20. PMID 16909377 DOI: 10.1086/500276  0.01
2005 Ley TJ, Rosenberg LE. The physician-scientist career pipeline in 2005: build it, and they will come. Jama. 294: 1343-51. PMID 16174692 DOI: 10.1001/jama.294.11.1343  1
2005 Rosenberg LE. 2004 Curt Stern Award Address. Introductory speech for Neil Risch. American Journal of Human Genetics. 76: 219-20. PMID 15714697  0.01
2002 Guelich JM, Singer BH, Castro MC, Rosenberg LE. A gender gap in the next generation of physician-scientists: medical student interest and participation in research. Journal of Investigative Medicine : the Official Publication of the American Federation For Clinical Research. 50: 412-8. PMID 12425427  1
2002 Rosenberg LE. Exceptional economic returns on investments in medical research. The Medical Journal of Australia. 177: 368-71. PMID 12358580  0.01
2002 Ley TJ, Rosenberg LE. Removing career obstacles for young physician-scientists -- loan-repayment programs. The New England Journal of Medicine. 346: 368-72. PMID 11821517 DOI: 10.1056/NEJM200201313460515  1
1999 Rosenberg LE. The physician-scientist: An essential - And fragile - Link in the medical research chain Journal of Clinical Investigation. 103: 1621-1626. PMID 10377167  1
1998 Rosenberg IH, Rosenberg LE. The implications of genetic diversity for nutrient requirements: The case of folate Nutrition Reviews. 56: S47-S53. PMID 9564177  1
1997 Bander KW, Rosenberg LE. Building bridges between academia and industry: forms; foundations; functions. The Yale Journal of Biology and Medicine. 70: 213-7. PMID 9544491  0.01
1995 Rosenberg LE. America's medical research enterprise: a time for rededication. Proceedings of the Association of American Physicians. 107: 160-5. PMID 8630738  0.01
1994 Saavedra-Alanis VM, Rysavy P, Rosenberg LE, Kalousek F. Rat liver mitochondrial processing peptidase: Both α- and β-subunits are required for activity Journal of Biological Chemistry. 269: 9284-9288. PMID 8132665  1
1993 Paces V, Rosenberg LE, Fenton WA, Kalousek F. The β subunit of the mitochondrial processing peptidase from rat liver: Cloning and sequencing of a cDNA and comparison with a proposed family of metallopeptidases Proceedings of the National Academy of Sciences of the United States of America. 90: 5355-5358. PMID 8506385  1
1993 Tahara T, Kraus JP, Ohura T, Rosenberg LE, Fenton WA. Three independent mutations in the same exon of the PCCB gene: Differences between Caucasian and Japanese propionic acidaemia Journal of Inherited Metabolic Disease. 16: 353-360. PMID 8411997 DOI: 10.1007/BF00710282  1
1993 Zheng X, Rosenberg LE, Kalousek F, Fenton WA. GroEL, GroES, and ATP-dependent folding and spontaneous assembly of ornithine transcarbamylase Journal of Biological Chemistry. 268: 7489-7493. PMID 8096512  1
1993 Kraus JP, Le K, Swaroop M, Ohura T, Tahara T, Rosenberg LE, Roper MD, Kozich V. Human cystathionine beta-synthase cDNA: sequence, alternative splicing and expression in cultured cells. Human Molecular Genetics. 2: 1633-8. PMID 7903580  1
1992 Swaroop M, Bradley K, Ohura T, Tahara T, Roper MD, Rosenberg LE, Kraus JP. Rat cystathionine beta-synthase. Gene organization and alternative splicing. The Journal of Biological Chemistry. 267: 11455-61. PMID 1597473  1
1992 Isaya G, Kalousek F, Rosenberg LE. Amino-terminal octapeptides function as recognition signals for the mitochondrial intermediate peptidase Journal of Biological Chemistry. 267: 7904-7910. PMID 1560019  1
1992 Rosenberg LE. The human genome project Bulletin of the New York Academy of Medicine: Journal of Urban Health. 68: 113-114. PMID 1555017  1
1992 Isaya G, Kalousek F, Rosenberg LE. Sequence analysis of rat mitochondrial intermediate peptidase: Similarity to zinc metallopeptidases and to a putative yeast homologue Proceedings of the National Academy of Sciences of the United States of America. 89: 8317-8321. PMID 1518864  1
1992 Kalousek F, Isaya G, Rosenberg LE. Rat liver mitochondrial intermediate peptidase (MIP): Purification and initial characterization Embo Journal. 11: 2803-2809. PMID 1322290  1
1991 Taroni F, Rosenberg LE. The precursor of the biotin-binding subunit of mammalian propionyl-CoA carboxylase can be translocated into mitochondria as Apo- or Holoprotein Journal of Biological Chemistry. 266: 13267-13271. PMID 2071602  1
1991 Carstens RP, Fenton WA, Rosenberg LR. Identification of RNA splicing errors resulting in human ornithine transcarbamylase deficiency. American Journal of Human Genetics. 48: 1105-14. PMID 2035531  1
1991 Purdue PE, Allsop J, Isaya G, Rosenberg LE, Danpure CJ. Mistargeting of peroxisomal L-alanine:glyoxylate aminotransferase to mitochondria in primary hyperoxaluria patients depends upon activation of a cryptic mitochondrial targeting sequence by a point mutation Proceedings of the National Academy of Sciences of the United States of America. 88: 10900-10904. PMID 1961759  1
1991 Isaya G, Kalousek F, Fenton WA, Rosenberg LE. Cleavage of precursors by the mitochondrial processing peptidase requires a compatible mature protein or an intermediate octapeptide Journal of Cell Biology. 113: 65-76. PMID 1672532  1
1990 Tahara T, Kraus JP, Rosenberg LE. Direct DNA sequencing of PCR amplified genomic DNA by the Maxam-Gilbert method Biotechniques. 8: 366-368. PMID 2340169  1
1990 Kleiber J, Kalousek F, Swaroop M, Rosenberg LE. The general mitochondrial matrix processing protease from rat liver: structural characterization of the catalytic subunit. Proceedings of the National Academy of Sciences of the United States of America. 87: 7978-82. PMID 2236012  1
1990 Rosenberg LE. Treating genetic diseases: Lessons from three children Pediatric Research. 27: S10-S16. PMID 2192347  1
1990 Tahara T, Kraus JP, Rosenberg LE. An unusual insertion/deletion in the gene encoding the β-subunit of propionyl-CoA carboxylase is a frequent mutation in Caucasian propionic acidemia Proceedings of the National Academy of Sciences of the United States of America. 87: 1372-1376. PMID 2154743  1
1990 Tahara T, Eto Y, Kraus JP, Rosenberg LE. Molecular basis of organic acidemia--propionic acidemia Human Cell : Official Journal of Human Cell Research Society. 3: 311-317. PMID 2095843  1
1990 Ledley FD, Jansen R, Nham SU, Fenton WA, Rosenberg LE. Mutation eliminating mitochondrial leader sequence of methylmalonyl-CoA mutase causes muto methylmalonic acidemia Proceedings of the National Academy of Sciences of the United States of America. 87: 3147-3150. PMID 1970180  1
1989 Browner MF, Taroni F, Sztul E, Rosenberg LE. Sequence analysis, biogenesis, and mitochondrial import of the alpha-subunit of rat liver propionyl-CoA carboxylase. The Journal of Biological Chemistry. 264: 12680-5. PMID 2745462  1
1989 Ohura T, Kraus JP, Rosenberg LE. Unequal synthesis and differential degradation of propionyl CoA carboxylase subunits in cells from normal and propionic acidemia patients American Journal of Human Genetics. 45: 33-40. PMID 2741949  1
1989 Hendrick JP, Hodges PE, Rosenberg LE. Survey of amino-terminal proteolytic cleavage sites in mitochondrial precursor proteins: leader peptides cleaved by two matrix proteases share a three-amino acid motif Proceedings of the National Academy of Sciences of the United States of America. 86: 4056-4060. PMID 2657736  1
1989 Sztul ES, Chu TW, Strauss AW, Rosenberg LE. Translocation of precursor proteins into the mitochondrial matrix occurs through an environment accessible to aqueous perturbants. Journal of Cell Science. 94: 695-701. PMID 2630564  1
1989 Jansen R, Kalousek F, Fenton WA, Rosenberg LE, Ledley FD. Cloning of full-length methylmalonyl-CoA mutase from a cDNA library using the polymerase chain reaction Genomics. 4: 198-205. PMID 2567699 DOI: 10.1016/0888-7543(89)90300-5  1
1989 Hodges PE, Rosenberg LE. The spfash mouse: a missense mutation in the ornithine transcarbamylase gene also causes aberrant mRNA splicing. Proceedings of the National Academy of Sciences of the United States of America. 86: 4142-6. PMID 2471197  1
1989 Hodges PE, Rosenberg LE. The spf(ash) mouse: A missense mutation in the ornithine transcarbamylase gene also causes aberrant mRNA splicing Proceedings of the National Academy of Sciences of the United States of America. 86: 4142-4146.  1
1988 Isaya G, Fenton WA, Hendrick JP, Furtak K, Kalousek F, Rosenberg LE. Mitochondrial import and processing of mutant human ornithine transcarbamylase precursors in cultured cells Molecular and Cellular Biology. 8: 5150-5158. PMID 3244350  1
1988 Kraus JP, Novotný J, Kalousek F, Swaroop M, Rosenberg LE. Different structures in the amino-terminal domain of the ornithine transcarbamylase leader peptide are involved in mitochondrial import and carboxyl-terminal cleavage. Proceedings of the National Academy of Sciences of the United States of America. 85: 8905-9. PMID 3194398  1
1988 Kalousek F, Hendrick JP, Rosenberg LE. Two mitochondrial matrix proteases act sequentially in the processing of mammalian matrix enzymes Proceedings of the National Academy of Sciences of the United States of America. 85: 7536-7540. PMID 3050998  1
1988 Sztul ES, Chu TW, Strauss AW, Rosenberg LE. Import of the malate dehydrogenase precursor by mitochondria. Cleavage within leader peptide by matrix protease leads to formation of intermediate-sized form. The Journal of Biological Chemistry. 263: 12085-91. PMID 3042789  1
1988 Fox JE, Rosenberg LE. Toward a molecular understanding of ornithine transcarbamylase deficiency Advances in Neurology. 48: 71-81. PMID 2891259  1
1988 Kelley KA, Chamberlain JW, Nolan JA, Horwich AL, Kalousek F, Eisenstadt J, Herrup K, Rosenberg LE. Meiotic expression of human ornithine transcarbamylase in the testes of transgenic mice. Molecular and Cellular Biology. 8: 1821-5. PMID 2837657  1
1987 Sztul ES, Hendrick JP, Kraus JP, Wall D, Kalousek F, Rosenberg LE. Import of rat ornithine transcarbamylase precursor into mitochondria: two-step processing of the leader peptide. The Journal of Cell Biology. 105: 2631-9. PMID 3693395  1
1987 Horwich AL, Kalousek F, Fenton WA, Furtak K, Pollock RA, Rosenberg LE. The ornithine transcarbamylase leader peptide directs mitochondrial import through both its midportion structure and net positive charge. The Journal of Cell Biology. 105: 669-77. PMID 3624306  1
1987 Matsubara Y, Kraus JP, Ozasa H, Glassberg R, Finocchiaro G, Ikeda Y, Mole J, Rosenberg LE, Tanaka K. Molecular cloning and nucleotide sequence of cDNA encoding the entire precursor of rat liver medium chain acyl coenzyme A dehydrogenase Journal of Biological Chemistry. 262: 10104-10108. PMID 3611054  1
1987 Fenton WA, Hack AM, Kraus JP, Rosenberg LE. Immunochemical studies of fibroblasts from patients with methylmalonyl-CoA mutase apoenzyme deficiency: detection of a mutation interfering with mitochondrial import. Proceedings of the National Academy of Sciences of the United States of America. 84: 1421-4. PMID 2881300  1
1986 Horwich AL, Kalousek F, Fenton WA, Pollock RA, Rosenberg LE. Targeting of pre-ornithine transcarbamylase to mitochondria: definition of critical regions and residues in the leader peptide. Cell. 44: 451-9. PMID 3943133 DOI: 10.1016/0092-8674(86)90466-6  1
1986 Fox J, Hack AM, Fenton WA, Golbus MS, Winter S, Kalousek F, Rozen R, Brusilow SW, Rosenberg LE. Prenatal diagnosis of ornithine transcarbamylase deficiency with use of DNA polymorphisms. The New England Journal of Medicine. 315: 1205-8. PMID 3762643 DOI: 10.1056/NEJM198611063151907  1
1986 Rosenberg LE, Fenton WA, Horwich AL, Kalousek F, Kraus JP. Targeting of nuclear-encoded proteins to the mitochondrial matrix: implications for human genetic defects. Annals of the New York Academy of Sciences. 488: 99-108. PMID 3472484  1
1986 Kraus JP, Firgaira F, Novotny J, Kalousek F, Williams KR, Williamson C, Ohura T, Rosenberg LE. Coding sequence of the precursor of the β subunit of rat propionyl-CoA carboxylase Proceedings of the National Academy of Sciences of the United States of America. 83: 8049-8053. PMID 3464942 DOI: 10.1073/pnas.83.21.8049  1
1986 Matsubara Y, Kraus JP, Yang-Feng TL, Francke U, Rosenberg LE, Tanaka K. Molecular cloning of cDNAs encoding rat and human medium-chain acyl-CoA dehydrogenase and assignment of the gene to human chromosome 1 Proceedings of the National Academy of Sciences of the United States of America. 83: 6543-6547. PMID 3462713 DOI: 10.1073/pnas.83.17.6543  1
1986 Kraus JP, Williamson CL, Firgaira FA, Yang-Feng TL, Münke M, Francke U, Rosenberg LE. Cloning and screening with nanogram amounts of immunopurified mRNAs: cDNA cloning and chromosomal mapping of cystathionine β-synthase and the β subunit of propionyl-CoA carboxylase Proceedings of the National Academy of Sciences of the United States of America. 83: 2047-2051. PMID 3457373  1
1986 Jaeger P, Portmann L, Saunders A, Rosenberg LE, Thier SO. Anticystinuric effects of glutamine and of dietary sodium restriction New England Journal of Medicine. 315: 1120-1123. PMID 3093863  1
1986 Fox JE, Hack AM, Fenton WA, Rosenberg LE. Identification and application of additional restriction fragment length polymorphisms at the human ornithine transcarbamylase locus. American Journal of Human Genetics. 38: 841-7. PMID 3014867  1
1986 McClead RE, Rozen R, Fox J, Rosenberg L, Menke J, Bickers R, Morrow G. Clinical application of DNA analysis in a family with OTC deficiency American Journal of Medical Genetics. 25: 513-518. PMID 2878615  1
1986 Rozen R, Fox JE, Hack AM, Fenton WA, Horwich AL, Rosenberg LE. DNA analysis for ornithine transcarbamylase deficiency. Journal of Inherited Metabolic Disease. 9: 49-57. PMID 2878115 DOI: 10.1007/BF01800858  1
1985 Rosenberg LE. Using patient materials for product development: A dean's perspective Clinical Research. 33: 452-454. PMID 4053503  1
1985 Horwich AL, Fenton WA, Firgaira FA, Fox JE, Kolansky D, Mellman IS, Rosenberg LE. Expression of amplified DNA sequences for ornithine transcarbamylase in HeLa cells: arginine residues may be required for mitochondrial import of enzyme precursor. The Journal of Cell Biology. 100: 1515-21. PMID 3988798 DOI: 10.1083/jcb.100.5.1515  1
1985 Horwich AL, Kalousek F, Rosenberg LE. Arginine in the leader peptide is required for both import and proteolytic cleavage of a mitochondrial precursor. Proceedings of the National Academy of Sciences of the United States of America. 82: 4930-3. PMID 3895227  1
1985 Horwich AL, Kalousek F, Mellman I, Rosenberg LE. A leader peptide is sufficient to direct mitochondrial import of a chimeric protein. The Embo Journal. 4: 1129-35. PMID 3891325  1
1985 Kraus JP, Hodges PE, Williamson CL, Horwich AL, Kalousek F, Williams KR, Rosenberg LE. A cDNA clone for the precursor of rat mitochondrial ornithine transcarbamylase: comparison of rat and human leader sequences and conservation of catalytic sites. Nucleic Acids Research. 13: 943-52. PMID 3839075 DOI: 10.1093/nar/13.3.943  1
1985 Rozen R, Fox J, Fenton WA, Horwich AL, Rosenberg LE. Gene deletion and restriction fragment length polymorphisms at the human ornithine transcarbamylase locus. Nature. 313: 815-7. PMID 2983225 DOI: 10.1038/313815a0  1
1984 Kalousek F, Orsulak MD, Rosenberg LE. Newly processed ornithine transcarbamylase subunits are assembled to trimers in rat liver mitochondria Journal of Biological Chemistry. 259: 5392-5395. PMID 6715349  1
1984 Skovby F, Kraus JP, Rosenberg LE. Homocystinuria: Biogenesis of cystathionine β-synthase subunits in cultured fibroblasts and in an in vitro translation system programmed with fibroblast messenger RNA American Journal of Human Genetics. 36: 452-459. PMID 6711564  1
1984 Skovby F, Kraus JP, Rosenberg LE. Biosynthesis and proteolytic activation of cystathionine β-synthase in rat liver Journal of Biological Chemistry. 259: 588-593. PMID 6706953  1
1984 Skovby F, Kraus JP, Rosenberg LE. Biosynthesis of human cystathionine β-synthase in cultured fibroblasts Journal of Biological Chemistry. 259: 583-587. PMID 6706952  1
1984 Lindgren V, de Martinville B, Horwich AL, Rosenberg LE, Francke U. Human ornithine transcarbamylase locus mapped to band Xp21.1 near the Duchenne muscular dystrophy locus. Science (New York, N.Y.). 226: 698-700. PMID 6494904  1
1984 Horwich AL, Fenton WA, Williams KR, Kalousek F, Kraus JP, Doolittle RF, Konigsberg W, Rosenberg LE. Structure and expression of a complementary DNA for the nuclear coded precursor of human mitochondrial ornithine transcarbamylase. Science (New York, N.Y.). 224: 1068-74. PMID 6372096  1
1984 Firgaira FA, Hendrick JP, Kalousek F, Kraus JP, Rosenberg LE. RNA required for import of precursor proteins into mitochondria Science. 226: 1319-1322. PMID 6209799  1
1984 Fenton WA, Hack AM, Helfgott D, Rosenberg LE. Biogenesis of the mitochondrial enzyme methylmalonyl-CoA mutase. Synthesis and processing of a precursor in a cell-free system and in cultured cells. The Journal of Biological Chemistry. 259: 6616-21. PMID 6144679  1
1983 Kraus JP, Kalousek F, Rosenberg LE. Biosynthesis and mitochondrial processing of the beta subunit of propionyl coenzyme A carboxylase from rat liver Journal of Biological Chemistry. 258: 7245-7248. PMID 6863243  1
1983 Kraus JP, Rosenberg LE. Cystathionine β-synthase from human liver: Improved purification scheme and additional characterization of the enzyme in crude and pure form Archives of Biochemistry and Biophysics. 222: 44-52. PMID 6838228 DOI: 10.1016/0003-9861(83)90500-3  1
1983 Rosenberg LE, Kalousek F, Orsulak MD. Biogenesis of ornithine transcarbamylase in spf(ash) mutant mice: Two cytoplasmic precursors, one mitochondrial enzyme Science. 222: 426-428. PMID 6623083  1
1983 Horwich AL, Kraus JP, Williams K, Kalousek F, Konigsberg W, Rosenberg LE. Molecular cloning of the cDNA coding for rat ornithine transcarbamoylase. Proceedings of the National Academy of Sciences of the United States of America. 80: 4258-62. PMID 6576335  1
1983 Matsui SM, Mahoney MJ, Rosenberg LE. The natural history of the inherited methylmalonic acidemias New England Journal of Medicine. 308: 857-861. PMID 6132336  1
1982 Rosenberg LE. Clinical implications. Society. 19: 60-1. PMID 11650600 DOI: 10.1007/BF02699958  1
1982 Rosenberg LE, Desnick RJ, Bach G, van Diggelen OP, d'Azzo A, Mueller OT, Wolf B, Kraus JP, Velazquez A, Berman M, Chemke J. Workshop on inborn errors of metabolism Progress in Clinical and Biological Research. 103: 223-229. PMID 7163221  1
1982 Kolansky DM, Conboy JG, Fenton WA, Rosenberg LE. Energy-dependent translocation of the precursor of ornithine transcarbamylase by isolated rat liver mitochondria Journal of Biological Chemistry. 257: 8467-8471. PMID 7085676  1
1982 Skovby F, Kraus J, Redlich C, Rosenberg LE. Immunochemical studies on cultured fibroblasts from patients with homocystinuria due to cystathionine β-synthase deficiency American Journal of Human Genetics. 34: 73-83. PMID 7081217  1
1982 Conboy JG, Fenton WA, Rosenberg LE. Processing of pre-ornithine transcarbamylase requires a zinc-dependent protease localized to the mitochondrial matrix Biochemical and Biophysical Research Communications. 105: 1-7. PMID 7046739 DOI: 10.1016/S0006-291X(82)80002-8  1
1982 Kraus JP, Rosenberg LE. Purification of low-abundance messenger RNAs from rat liver by polysome immunoadsorption Proceedings of the National Academy of Sciences of the United States of America. 79: 4015-4019. PMID 6180433  1
1982 Rosenberg LE. The inherited methylmalonic acidemias Progress in Clinical and Biological Research. 103: 187-209. PMID 6131428  1
1982 Fenton WA, Hack AM, Willard HF, Gertler A, Rosenberg LE. Purification and properties of methylmalonyl coenzyme A mutase from human liver. Archives of Biochemistry and Biophysics. 214: 815-23. PMID 6124211 DOI: 10.1016/0003-9861(82)90088-1  1
1981 Rosenberg L. Leon Rosenberg on the "human life" bill. Science (New York, N.Y.). 212: 907. PMID 11643642  1
1981 Halperin EC, Thier SO, Rosenberg LE. The use of D-penicillamine in cystinuria: Efficacy and untoward reactions Yale Journal of Biology and Medicine. 54: 439-446. PMID 7342491  1
1981 Mc Reynolds JW, Crowley B, Mahoney MJ, Rosenberg LE. Autosomal recessive inheritance of human mitochondrial carbamyl phosphate synthetase deficiency American Journal of Human Genetics. 33: 345-353. PMID 7246541  1
1981 Rosenberg LE. Presidential address. On the state of our Society American Journal of Human Genetics. 33: 329-336. PMID 7246540  1
1981 Fenton WA, Rosenberg LE. The defect in the cbl B class of human methylmalonic acidemia: Deficiency of cob(I)alamin adenosyltransferase activity in extracts of cultured fibroblasts Biochemical and Biophysical Research Communications. 98: 283-289. PMID 7213387 DOI: 10.1016/0006-291X(81)91900-8  1
1981 Berliner N, Rosenberg LE. Uptake and metabolism of free cyanocobalamin by cultured human fibroblasts from controls and a patient with transcobalamin II deficiency Metabolism. 30: 230-236. PMID 7207198 DOI: 10.1016/0026-0495(81)90146-3  1
1981 Conboy JG, Rosenberg LE. Posttranslational uptake and processing of in vitro synthesized ornithine transcarbamoylase precursor by isolated rat liver mitochondria Proceedings of the National Academy of Sciences of the United States of America. 78: 3073-3077. PMID 6942417  1
1981 Sennett C, Rosenberg LE, Mellman IS. Transmembrane transport of cobalamin in prokaryotic and eukaryotic cells. Annual Review of Biochemistry. 50: 1053-86. PMID 6267986 DOI: 10.1146/annurev.bi.50.070181.005201  1
1981 Kraus JP, Conboy JG, Rosenberg LE. Pre-ornithine transcarbamylase. Properties of the cytoplasmic precursor of a mitochondrial matrix enzyme Journal of Biological Chemistry. 256: 10739-10742. PMID 6169723  1
1981 Kolhouse JF, Utley C, Fenton WA, Rosenberg LE. Immunochemical studies on cultured fibroblasts from patients with inherited methylmalonic acidemia Proceedings of the National Academy of Sciences of the United States of America. 78: 7737-7741. PMID 6121323  1
1980 Lipson MH, Kraus JP, Solomon LR, Rosenberg LE. Depletion of cultured human fibroblasts of pyridoxal 5'-phosphate: Effect on activities of aspartate aminotransferase, alanine aminotransferase, and cystathionine β-synthase Archives of Biochemistry and Biophysics. 204: 486-493. PMID 7447458  1
1980 Lipson MH, Kraus J, Rosenberg LE. Affinity of cystathionine β-synthase for pyridoxal 5'-phosphate in cultured cells: A mechanism for pyridoxine-responsive homocystinuria Journal of Clinical Investigation. 66: 188-193. PMID 7400312  1
1980 Wolf B, Willard HF, Rosenberg LE. Kinetic analysis of genetic complementation in heterokaryons of propionyl CoA carboxylase-deficient human fibroblasts American Journal of Human Genetics. 32: 16-25. PMID 7361761  1
1980 Skovby F, Rosenberg LE, Thier SO. No effect of L-glutamine on cystinuria New England Journal of Medicine. 302: 236-237. PMID 7350472  1
1980 Kalousek F, Darigo MD, Rosenberg LE. Isolation and characterization of propionyl-CoA carboxylase from normal human liver. Evidence for a protomeric tetramer of nonidentical subunits Journal of Biological Chemistry. 255: 60-65. PMID 6765947  1
1980 Willard HF, Rosenberg LE. Interactions of methylmalonyl CoA mutase from normal human fibroblasts with adenosylcobalamin and methylmalonyl CoA: Evidence for non-equivalent active sites Archives of Biochemistry and Biophysics. 200: 130-139. PMID 6102452 DOI: 10.1016/0003-9861(80)90339-2  1
1980 Willard HF, Rosenberg LE. Inherited methylmalonyl CoA mutase apoenzyme deficiency in human fibroblasts. Evidence for allelic heterogeneity, genetic compounds, and codominant expression Journal of Clinical Investigation. 65: 690-698. PMID 6101601  1
1980 Bondy PK, Rosenberg LE. Error in dosage of mithramycin for hypercalcemia New England Journal of Medicine. 303: 341.  1
1979 Youngdahl-Turner P, Mellman IS, Allen RH, Rosenberg LE. Protein mediated vitamin uptake. Adsorptive endocytosis of the transcobalamin II-cobalamin complex by cultured human fibroblasts. Experimental Cell Research. 118: 127-34. PMID 759210 DOI: 10.1016/0014-4827(79)90590-1  1
1979 Wolf B, Rosenberg LE. Stimulation of propionyl CoA and β- methylcrotonyl CoA carboxylase activities in human leukocytes and cultured fibroblasts by biotin Pediatric Research. 13: 1275-1279. PMID 514693  1
1979 Wolf B, Kalousek F, Rosenberg LE. Essential arginine residues in the active sites of propionyl CoA carboxylase and beta-methylcrotonyl CoA carboxylase Enzyme. 24: 302-306. PMID 510274  1
1979 Mellman I, Willard HF, Youngdahl-Turner P, Rosenberg LE. Cobalamin coenzyme synthesis in normal and mutant human fibroblasts. Evidence for a processing enzyme activity deficient in cblC cells. The Journal of Biological Chemistry. 254: 11847-53. PMID 500677  1
1979 Conboy JG, Kalousek F, Rosenberg LE. In vitro synthesis of a putative precursor of mitochondrial ornithine transcarbamoylase Proceedings of the National Academy of Sciences of the United States of America. 76: 5724-5727. PMID 293676  1
1979 Mellman IS, Lin PF, Ruddle FH, Rosenberg LE. Genetic control of cobalamin binding in normal and mutant cells: assignment of the gene for 5-methyltetrahydrofolate:L-homocysteine S-methyltransferase to human chromosome 1. Proceedings of the National Academy of Sciences of the United States of America. 76: 405-9. PMID 284356  1
1979 Willard HF, Rosenberg LE. Inborn errors of cobalamin metabolism: Effect of cobalamin supplementation in culture on methylmalonyl CoA mutase activity in normal and mutant human fibroblasts Biochemical Genetics. 17: 57-75. PMID 36882 DOI: 10.1007/BF00484474  1
1979 Lipson MH, Kraus JP, Solomon LR, Rosenberg LE. Vitamin B6 metabolism in cultured human fibroblasts Pediatric Research. 13: No. 914.  1
1978 Mellman I, Willard HF, Rosenberg LE. Cobalamin binding and cobalamin-dependent enzyme activity in normal and mutant human fibroblasts. The Journal of Clinical Investigation. 62: 952-60. PMID 30783 DOI: 10.1172/JCI109224  0.72
1978 Willard HF, Mellman IS, Rosenberg LE. Genetic complementation among inherited deficiencies of methylmalonyl-CoA mutase activity: evidence for a new class of human cobalamin mutant. American Journal of Human Genetics. 30: 1-13. PMID 23678  0.72
1977 Mellman IS, Youngdahl-Turner P, Willard HF, Rosenberg LE. Intracellular binding of radioactive hydroxocobalamin to cobalamin-dependent apoenzymes in rat liver. Proceedings of the National Academy of Sciences of the United States of America. 74: 916-20. PMID 15258  0.72
1976 Halloran KH, Hsia E, Rosenberg LE. Genetic counseling for congenital heart disease. The Journal of Pediatrics. 88: 1054-6. PMID 1271176  0.01
1975 Rosenberg LE, Patel L, Lilljeqvist AC. Absence of an intracellular cobalamin-binding protein in cultured fibroblasts from patients with defective synthesis of 5'-deoxyadenosylcobalamin and methylcobalamin. Proceedings of the National Academy of Sciences of the United States of America. 72: 4617-21. PMID 16592285  0.01
1967 Elsas LJ, Rosenberg LE. Inhibition of amino Acid transport in rat kidney cortex by puromycin. Proceedings of the National Academy of Sciences of the United States of America. 57: 371-8. PMID 16591480  0.01
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