| Year |
Citation |
Score |
| 2020 |
Jiang M, Volland S, Paniagua AE, Wang H, Balaji A, Li DG, Lopes VS, Burgess BL, Williams DS. Microtubule motor transport in the delivery of melanosomes to the actin-rich, apical domain of in the retinal pigment epithelium. Journal of Cell Science. PMID 32661088 DOI: 10.1242/Jcs.242214 |
0.307 |
|
| 2020 |
Lakkaraju A, Umapathy A, Tan LX, Daniele L, Philp NJ, Boesze-Battaglia K, Williams DS. The Cell Biology of the Retinal Pigment Epithelium. Progress in Retinal and Eye Research. 100846. PMID 32105772 DOI: 10.1016/J.Preteyeres.2020.100846 |
0.347 |
|
| 2020 |
Milstein ML, Cavanaugh BL, Roussey NM, Volland S, Williams DS, Goldberg AFX. Multistep peripherin-2/rds self-assembly drives membrane curvature for outer segment disk architecture and photoreceptor viability. Proceedings of the National Academy of Sciences of the United States of America. PMID 32041874 DOI: 10.1073/Pnas.1912513117 |
0.335 |
|
| 2019 |
Umapathy A, Williams DS. Live Imaging of Organelle Motility in RPE Flatmounts. Advances in Experimental Medicine and Biology. 1185: 389-393. PMID 31884643 DOI: 10.1007/978-3-030-27378-1_64 |
0.35 |
|
| 2019 |
Daniele LL, Caughey J, Volland S, Sharp RC, Dhingra A, Williams DS, Philp NJ, Boesze-Battaglia K. Peroxisome turnover and diurnal modulation of antioxidant activity in retinal pigment epithelia utilizes microtubule-associated protein 1 light chain 3B. American Journal of Physiology. Cell Physiology. PMID 31577510 DOI: 10.1152/Ajpcell.00185.2019 |
0.335 |
|
| 2019 |
Chadha A, Volland S, Baliaouri NV, Tran EM, Williams DS. The route of the visual receptor, rhodopsin, along the cilium. Journal of Cell Science. PMID 30975916 DOI: 10.1242/Jcs.229526 |
0.311 |
|
| 2018 |
Esteve-Rudd J, Hazim RA, Diemer T, Paniagua AE, Volland S, Umapathy A, Williams DS. Defective phagosome motility and degradation in cell nonautonomous RPE pathogenesis of a dominant macular degeneration. Proceedings of the National Academy of Sciences of the United States of America. PMID 29735674 DOI: 10.1073/Pnas.1709211115 |
0.389 |
|
| 2018 |
Hazim RA, Williams DS. Cell Culture Analysis of the Phagocytosis of Photoreceptor Outer Segments by Primary Mouse RPE Cells. Methods in Molecular Biology (Clifton, N.J.). 1753: 63-71. PMID 29564781 DOI: 10.1007/978-1-4939-7720-8_4 |
0.361 |
|
| 2017 |
Hazim RA, Karumbayaram S, Jiang M, Dimashkie A, Lopes VS, Li D, Burgess BL, Vijayaraj P, Alva-Ornelas JA, Zack JA, Kohn DB, Gomperts BN, Pyle AD, Lowry WE, Williams DS. Differentiation of RPE cells from integration-free iPS cells and their cell biological characterization. Stem Cell Research & Therapy. 8: 217. PMID 28969679 DOI: 10.1186/S13287-017-0652-9 |
0.321 |
|
| 2017 |
Galloway CA, Dalvi S, Hung SSC, MacDonald LA, Latchney LR, Wong RCB, Guymer RH, Mackey DA, Williams DS, Chung MM, Gamm DM, Pébay A, Hewitt AW, Singh R. Drusen in patient-derived hiPSC-RPE models of macular dystrophies. Proceedings of the National Academy of Sciences of the United States of America. PMID 28878022 DOI: 10.1073/Pnas.1710430114 |
0.334 |
|
| 2017 |
Williams DS, Chadha A, Hazim R, Gibbs D. Gene therapy approaches for prevention of retinal degeneration in Usher syndrome. Gene Therapy. PMID 28054582 DOI: 10.1038/Gt.2016.81 |
0.577 |
|
| 2016 |
Goldberg AF, Moritz OL, Williams DS. Molecular basis for photoreceptor outer segment architecture. Progress in Retinal and Eye Research. PMID 27260426 DOI: 10.1016/J.Preteyeres.2016.05.003 |
0.325 |
|
| 2016 |
Hazim R, Jiang M, Esteve-Rudd J, Diemer T, Lopes VS, Williams DS. Live-Cell Imaging of Phagosome Motility in Primary Mouse RPE Cells. Advances in Experimental Medicine and Biology. 854: 751-5. PMID 26427485 DOI: 10.1007/978-3-319-17121-0_100 |
0.361 |
|
| 2015 |
Volland S, Hughes LC, Kong C, Burgess BL, Linberg KA, Luna G, Zhou ZH, Fisher SK, Williams DS. Three-dimensional organization of nascent rod outer segment disk membranes. Proceedings of the National Academy of Sciences of the United States of America. PMID 26578801 DOI: 10.1073/Pnas.1516309112 |
0.306 |
|
| 2015 |
Jiang M, Esteve-Rudd J, Lopes VS, Diemer T, Lillo C, Rump A, Williams DS. Microtubule motors transport phagosomes in the RPE, and lack of KLC1 leads to AMD-like pathogenesis. The Journal of Cell Biology. 210: 595-611. PMID 26261180 DOI: 10.1083/Jcb.201410112 |
0.349 |
|
| 2015 |
Volland S, Esteve-Rudd J, Hoo J, Yee C, Williams DS. A comparison of some organizational characteristics of the mouse central retina and the human macula. Plos One. 10: e0125631. PMID 25923208 DOI: 10.1371/Journal.Pone.0125631 |
0.421 |
|
| 2015 |
Lopes VS, Williams DS. Gene Therapy for the Retinal Degeneration of Usher Syndrome Caused by Mutations in MYO7A. Cold Spring Harbor Perspectives in Medicine. 5. PMID 25605753 DOI: 10.1101/Cshperspect.A017319 |
0.404 |
|
| 2015 |
Eblimit A, Nguyen TM, Chen Y, Esteve-Rudd J, Zhong H, Letteboer S, Van Reeuwijk J, Simons DL, Ding Q, Wu KM, Li Y, Van Beersum S, Moayedi Y, Xu H, Pickard P, ... ... Williams DS, et al. Spata7 is a retinal ciliopathy gene critical for correct RPGRIP1 localization and protein trafficking in the retina. Human Molecular Genetics. 24: 1584-601. PMID 25398945 DOI: 10.1093/Hmg/Ddu573 |
0.494 |
|
| 2014 |
Frost LS, Lopes VS, Bragin A, Reyes-Reveles J, Brancato J, Cohen A, Mitchell CH, Williams DS, Boesze-Battaglia K. The Contribution of Melanoregulin to Microtubule-Associated Protein 1 Light Chain 3 (LC3) Associated Phagocytosis in Retinal Pigment Epithelium. Molecular Neurobiology. PMID 25301234 DOI: 10.1007/S12035-014-8920-5 |
0.392 |
|
| 2014 |
Gee HY, Ashraf S, Wan X, Vega-Warner V, Esteve-Rudd J, Lovric S, Fang H, Hurd TW, Sadowski CE, Allen SJ, Otto EA, Korkmaz E, Washburn J, Levy S, Williams DS, et al. Mutations in EMP2 cause childhood-onset nephrotic syndrome. American Journal of Human Genetics. 94: 884-90. PMID 24814193 DOI: 10.1016/J.Ajhg.2014.04.010 |
0.362 |
|
| 2014 |
Lopes VS, Diemer T, Williams DS. Assessment of different virus-mediated approaches for retinal gene therapy of Usher 1B. Advances in Experimental Medicine and Biology. 801: 725-31. PMID 24664764 DOI: 10.1007/978-1-4614-3209-8_91 |
0.465 |
|
| 2014 |
Esteve-Rudd J, Lopes VS, Jiang M, Williams DS. In vivo and in vitro monitoring of phagosome maturation in retinal pigment epithelium cells. Advances in Experimental Medicine and Biology. 801: 85-90. PMID 24664684 DOI: 10.1007/978-1-4614-3209-8_11 |
0.377 |
|
| 2014 |
Crouse JA, Lopes VS, Sanagustin JT, Keady BT, Williams DS, Pazour GJ. Distinct functions for IFT140 and IFT20 in opsin transport. Cytoskeleton (Hoboken, N.J.). 71: 302-10. PMID 24619649 DOI: 10.1002/Cm.21173 |
0.383 |
|
| 2013 |
Ashraf S, Gee HY, Woerner S, Xie LX, Vega-Warner V, Lovric S, Fang H, Song X, Cattran DC, Avila-Casado C, Paterson AD, Nitschké P, Bole-Feysot C, Cochat P, Esteve-Rudd J, ... ... Williams DS, et al. ADCK4 mutations promote steroid-resistant nephrotic syndrome through CoQ10 biosynthesis disruption. The Journal of Clinical Investigation. 123: 5179-89. PMID 24270420 DOI: 10.1172/Jci69000 |
0.36 |
|
| 2013 |
Zariwala MA, Gee HY, Kurkowiak M, Al-Mutairi DA, Leigh MW, Hurd TW, Hjeij R, Dell SD, Chaki M, Dougherty GW, Adan M, Spear PC, Esteve-Rudd J, Loges NT, Rosenfeld M, ... ... Williams DS, et al. ZMYND10 is mutated in primary ciliary dyskinesia and interacts with LRRC6. American Journal of Human Genetics. 93: 336-45. PMID 23891469 DOI: 10.1016/J.Ajhg.2013.06.007 |
0.324 |
|
| 2013 |
Frost LS, Lopes VS, Stefano FP, Bragin A, Williams DS, Mitchell CH, Boesze-Battaglia K. Loss of melanoregulin (MREG) enhances cathepsin-D secretion by the retinal pigment epithelium. Visual Neuroscience. 30: 55-64. PMID 23611523 DOI: 10.1017/S0952523813000096 |
0.374 |
|
| 2013 |
Lopes VS, Boye SE, Louie CM, Boye S, Dyka F, Chiodo V, Fofo H, Hauswirth WW, Williams DS. Retinal gene therapy with a large MYO7A cDNA using adeno-associated virus. Gene Therapy. 20: 824-33. PMID 23344065 DOI: 10.1038/Gt.2013.3 |
0.451 |
|
| 2012 |
Trivedi D, Colin E, Louie CM, Williams DS. Live-cell imaging evidence for the ciliary transport of rod photoreceptor opsin by heterotrimeric kinesin-2. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 32: 10587-93. PMID 22855808 DOI: 10.1523/Jneurosci.0015-12.2012 |
0.403 |
|
| 2012 |
Engelhardt M, Tosha C, Lopes VS, Chen B, Nguyen L, Nusinowitz S, Williams DS. Functional and morphological analysis of the subretinal injection of retinal pigment epithelium cells. Visual Neuroscience. 29: 83-93. PMID 22391151 DOI: 10.1017/S0952523812000041 |
0.422 |
|
| 2012 |
Harkewicz R, Du H, Tong Z, Alkuraya H, Bedell M, Sun W, Wang X, Hsu YH, Esteve-Rudd J, Hughes G, Su Z, Zhang M, Lopes VS, Molday RS, Williams DS, et al. Essential role of ELOVL4 protein in very long chain fatty acid synthesis and retinal function. The Journal of Biological Chemistry. 287: 11469-80. PMID 22199362 DOI: 10.1074/Jbc.M111.256073 |
0.406 |
|
| 2012 |
Williams DS, Lopes VS. Gene therapy strategies for Usher syndrome type 1B. Advances in Experimental Medicine and Biology. 723: 235-42. PMID 22183338 DOI: 10.1007/978-1-4614-0631-0_31 |
0.462 |
|
| 2011 |
Williams DS, Lopes VS. The many different cellular functions of MYO7A in the retina. Biochemical Society Transactions. 39: 1207-10. PMID 21936790 DOI: 10.1042/Bst0391207 |
0.506 |
|
| 2011 |
Jacobson SG, Cideciyan AV, Gibbs D, Sumaroka A, Roman AJ, Aleman TS, Schwartz SB, Olivares MB, Russell RC, Steinberg JD, Kenna MA, Kimberling WJ, Rehm HL, Williams DS. Retinal disease course in Usher syndrome 1B due to MYO7A mutations. Investigative Ophthalmology & Visual Science. 52: 7924-36. PMID 21873662 DOI: 10.1167/Iovs.11-8313 |
0.581 |
|
| 2011 |
Phillips JB, Blanco-Sanchez B, Lentz JJ, Tallafuss A, Khanobdee K, Sampath S, Jacobs ZG, Han PF, Mishra M, Titus TA, Williams DS, Keats BJ, Washbourne P, Westerfield M. Harmonin (Ush1c) is required in zebrafish Müller glial cells for photoreceptor synaptic development and function. Disease Models & Mechanisms. 4: 786-800. PMID 21757509 DOI: 10.1242/Dmm.006429 |
0.405 |
|
| 2011 |
Lopes VS, Gibbs D, Libby RT, Aleman TS, Welch DL, Lillo C, Jacobson SG, Radu RA, Steel KP, Williams DS. The Usher 1B protein, MYO7A, is required for normal localization and function of the visual retinoid cycle enzyme, RPE65. Human Molecular Genetics. 20: 2560-70. PMID 21493626 DOI: 10.1093/Hmg/Ddr155 |
0.624 |
|
| 2010 |
Lopes VS, Jimeno D, Khanobdee K, Song X, Chen B, Nusinowitz S, Williams DS. Dysfunction of heterotrimeric kinesin-2 in rod photoreceptor cells and the role of opsin mislocalization in rapid cell death. Molecular Biology of the Cell. 21: 4076-88. PMID 20926680 DOI: 10.1091/Mbc.E10-08-0715 |
0.374 |
|
| 2010 |
Otto EA, Hurd TW, Airik R, Chaki M, Zhou W, Stoetzel C, Patil SB, Levy S, Ghosh AK, Murga-Zamalloa CA, van Reeuwijk J, Letteboer SJ, Sang L, Giles RH, Liu Q, ... ... Williams DS, et al. Candidate exome capture identifies mutation of SDCCAG8 as the cause of a retinal-renal ciliopathy. Nature Genetics. 42: 840-50. PMID 20835237 DOI: 10.1038/Ng.662 |
0.397 |
|
| 2010 |
Liao JL, Yu J, Huang K, Hu J, Diemer T, Ma Z, Dvash T, Yang XJ, Travis GH, Williams DS, Bok D, Fan G. Molecular signature of primary retinal pigment epithelium and stem-cell-derived RPE cells. Human Molecular Genetics. 19: 4229-38. PMID 20709808 DOI: 10.1093/Hmg/Ddq341 |
0.356 |
|
| 2010 |
Trivedi D, Williams DS. Ciliary transport of opsin. Advances in Experimental Medicine and Biology. 664: 185-91. PMID 20238016 DOI: 10.1007/978-1-4419-1399-9_21 |
0.383 |
|
| 2010 |
Louie CM, Caridi G, Lopes VS, Brancati F, Kispert A, Lancaster MA, Schlossman AM, Otto EA, Leitges M, Gröne HJ, Lopez I, Gudiseva HV, O'Toole JF, Vallespin E, Ayyagari R, ... ... Williams DS, et al. AHI1 is required for photoreceptor outer segment development and is a modifier for retinal degeneration in nephronophthisis. Nature Genetics. 42: 175-80. PMID 20081859 DOI: 10.1038/Ng.519 |
0.501 |
|
| 2010 |
Gibbs D, Diemer T, Khanobdee K, Hu J, Bok D, Williams DS. Function of MYO7A in the human RPE and the validity of shaker1 mice as a model for Usher syndrome 1B. Investigative Ophthalmology & Visual Science. 51: 1130-5. PMID 19643958 DOI: 10.1167/Iovs.09-4032 |
0.593 |
|
| 2009 |
Schwander M, Lopes V, Sczaniecka A, Gibbs D, Lillo C, Delano D, Tarantino LM, Wiltshire T, Williams DS, Müller U. A novel allele of myosin VIIa reveals a critical function for the C-terminal FERM domain for melanosome transport in retinal pigment epithelial cells. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 29: 15810-8. PMID 20016096 DOI: 10.1523/Jneurosci.4876-09.2009 |
0.59 |
|
| 2009 |
Avasthi P, Watt CB, Williams DS, Le YZ, Li S, Chen CK, Marc RE, Frederick JM, Baehr W. Trafficking of membrane proteins to cone but not rod outer segments is dependent on heterotrimeric kinesin-II. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 29: 14287-98. PMID 19906976 DOI: 10.1523/Jneurosci.3976-09.2009 |
0.394 |
|
| 2009 |
Grillet N, Xiong W, Reynolds A, Kazmierczak P, Sato T, Lillo C, Dumont RA, Hintermann E, Sczaniecka A, Schwander M, Williams D, Kachar B, Gillespie PG, Müller U. Harmonin mutations cause mechanotransduction defects in cochlear hair cells. Neuron. 62: 375-87. PMID 19447093 DOI: 10.1016/J.Neuron.2009.04.006 |
0.317 |
|
| 2009 |
Falzone TL, Stokin GB, Lillo C, Rodrigues EM, Westerman EL, Williams DS, Goldstein LS. Axonal stress kinase activation and tau misbehavior induced by kinesin-1 transport defects. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 29: 5758-67. PMID 19420244 DOI: 10.1523/Jneurosci.0780-09.2009 |
0.302 |
|
| 2009 |
Gibbs D, Cideciyan AV, Jacobson SG, Williams DS. Retinal pigment epithelium defects in humans and mice with mutations in MYO7A: imaging melanosome-specific autofluorescence. Investigative Ophthalmology & Visual Science. 50: 4386-93. PMID 19324852 DOI: 10.1167/Iovs.09-3471 |
0.618 |
|
| 2009 |
Williams DS, Aleman TS, Lillo C, Lopes VS, Hughes LC, Stone EM, Jacobson SG. Harmonin in the murine retina and the retinal phenotypes of Ush1c-mutant mice and human USH1C. Investigative Ophthalmology & Visual Science. 50: 3881-9. PMID 19324851 DOI: 10.1167/Iovs.08-3358 |
0.339 |
|
| 2009 |
Damek-Poprawa M, Diemer T, Lopes VS, Lillo C, Harper DC, Marks MS, Wu Y, Sparrow JR, Rachel RA, Williams DS, Boesze-Battaglia K. Melanoregulin (MREG) modulates lysosome function in pigment epithelial cells. The Journal of Biological Chemistry. 284: 10877-89. PMID 19240024 DOI: 10.1074/Jbc.M808857200 |
0.374 |
|
| 2008 |
Yang Z, Chen Y, Lillo C, Chien J, Yu Z, Michaelides M, Klein M, Howes KA, Li Y, Kaminoh Y, Chen H, Zhao C, Chen Y, Al-Sheikh YT, Karan G, ... ... Williams DS, et al. Mutant prominin 1 found in patients with macular degeneration disrupts photoreceptor disk morphogenesis in mice. The Journal of Clinical Investigation. 118: 2908-16. PMID 18654668 DOI: 10.1172/Jci35891 |
0.371 |
|
| 2008 |
Jacobson SG, Cideciyan AV, Aleman TS, Sumaroka A, Roman AJ, Gardner LM, Prosser HM, Mishra M, Bech-Hansen NT, Herrera W, Schwartz SB, Liu XZ, Kimberling WJ, Steel KP, Williams DS. Usher syndromes due to MYO7A, PCDH15, USH2A or GPR98 mutations share retinal disease mechanism. Human Molecular Genetics. 17: 2405-15. PMID 18463160 DOI: 10.1093/Hmg/Ddn140 |
0.375 |
|
| 2008 |
Allocca M, Doria M, Petrillo M, Colella P, Garcia-Hoyos M, Gibbs D, Kim SR, Maguire A, Rex TS, Di Vicino U, Cutillo L, Sparrow JR, Williams DS, Bennett J, Auricchio A. Serotype-dependent packaging of large genes in adeno-associated viral vectors results in effective gene delivery in mice. The Journal of Clinical Investigation. 118: 1955-64. PMID 18414684 DOI: 10.1172/Jci34316 |
0.578 |
|
| 2008 |
Feathers KL, Lyubarsky AL, Khan NW, Teofilo K, Swaroop A, Williams DS, Pugh EN, Thompson DA. Nrl-knockout mice deficient in Rpe65 fail to synthesize 11-cis retinal and cone outer segments. Investigative Ophthalmology & Visual Science. 49: 1126-35. PMID 18326740 DOI: 10.1167/Iovs.07-1234 |
0.33 |
|
| 2008 |
Diemer T, Gibbs D, Williams DS. Analysis of the rate of disk membrane digestion by cultured RPE cells. Advances in Experimental Medicine and Biology. 613: 321-6. PMID 18188960 DOI: 10.1007/978-0-387-74904-4_37 |
0.522 |
|
| 2008 |
Williams DS. Usher syndrome: animal models, retinal function of Usher proteins, and prospects for gene therapy. Vision Research. 48: 433-41. PMID 17936325 DOI: 10.1016/J.Visres.2007.08.015 |
0.364 |
|
| 2007 |
Klomp AE, Teofilo K, Legacki E, Williams DS. Analysis of the linkage of MYRIP and MYO7A to melanosomes by RAB27A in retinal pigment epithelial cells. Cell Motility and the Cytoskeleton. 64: 474-87. PMID 17352418 DOI: 10.1002/Cm.20198 |
0.381 |
|
| 2007 |
Hashimoto T, Gibbs D, Lillo C, Azarian SM, Legacki E, Zhang XM, Yang XJ, Williams DS. Lentiviral gene replacement therapy of retinas in a mouse model for Usher syndrome type 1B. Gene Therapy. 14: 584-94. PMID 17268537 DOI: 10.1038/sj.gt.3302897 |
0.605 |
|
| 2007 |
Boesze-Battaglia K, Song H, Sokolov M, Lillo C, Pankoski-Walker L, Gretzula C, Gallagher B, Rachel RA, Jenkins NA, Copeland NG, Morris F, Jacob J, Yeagle P, Williams DS, Damek-Poprawa M. The tetraspanin protein peripherin-2 forms a complex with melanoregulin, a putative membrane fusion regulator. Biochemistry. 46: 1256-72. PMID 17260955 DOI: 10.1021/Bi061466I |
0.334 |
|
| 2006 |
Jimeno D, Feiner L, Lillo C, Teofilo K, Goldstein LS, Pierce EA, Williams DS. Analysis of kinesin-2 function in photoreceptor cells using synchronous Cre-loxP knockout of Kif3a with RHO-Cre. Investigative Ophthalmology & Visual Science. 47: 5039-46. PMID 17065525 DOI: 10.1167/Iovs.06-0032 |
0.343 |
|
| 2006 |
Sayer JA, Otto EA, O'Toole JF, Nurnberg G, Kennedy MA, Becker C, Hennies HC, Helou J, Attanasio M, Fausett BV, Utsch B, Khanna H, Liu Y, Drummond I, Kawakami I, ... ... Williams DS, et al. The centrosomal protein nephrocystin-6 is mutated in Joubert syndrome and activates transcription factor ATF4. Nature Genetics. 38: 674-81. PMID 16682973 DOI: 10.1038/Ng1786 |
0.319 |
|
| 2006 |
Chang B, Khanna H, Hawes N, Jimeno D, He S, Lillo C, Parapuram SK, Cheng H, Scott A, Hurd RE, Sayer JA, Otto EA, Attanasio M, O'Toole JF, Jin G, ... ... Williams DS, et al. In-frame deletion in a novel centrosomal/ciliary protein CEP290/NPHP6 perturbs its interaction with RPGR and results in early-onset retinal degeneration in the rd16 mouse. Human Molecular Genetics. 15: 1847-57. PMID 16632484 DOI: 10.1093/Hmg/Ddl107 |
0.368 |
|
| 2006 |
Azarian SM, McLeod I, Lillo C, Gibbs D, Yates JR, Williams DS. Proteomic analysis of mature melanosomes from the retinal pigmented epithelium. Journal of Proteome Research. 5: 521-9. PMID 16512666 DOI: 10.1021/Pr0502323 |
0.584 |
|
| 2006 |
Jimeno D, Lillo C, Roberts EA, Goldstein LS, Williams DS. Kinesin-2 and photoreceptor cell death: requirement of motor subunits. Experimental Eye Research. 82: 351-3. PMID 16337628 DOI: 10.1016/J.Exer.2005.10.026 |
0.345 |
|
| 2005 |
Zhu X, Wu K, Rife L, Cawley NX, Brown B, Adams T, Teofilo K, Lillo C, Williams DS, Loh YP, Craft CM. Carboxypeptidase E is required for normal synaptic transmission from photoreceptors to the inner retina. Journal of Neurochemistry. 95: 1351-62. PMID 16219026 DOI: 10.1111/J.1471-4159.2005.03460.X |
0.308 |
|
| 2005 |
Khanna H, Hurd TW, Lillo C, Shu X, Parapuram SK, He S, Akimoto M, Wright AF, Margolis B, Williams DS, Swaroop A. RPGR-ORF15, which is mutated in retinitis pigmentosa, associates with SMC1, SMC3, and microtubule transport proteins. The Journal of Biological Chemistry. 280: 33580-7. PMID 16043481 DOI: 10.1074/Jbc.M505827200 |
0.361 |
|
| 2005 |
Kitamoto J, Libby RT, Gibbs D, Steel KP, Williams DS. Myosin VI is required for normal retinal function. Experimental Eye Research. 81: 116-20. PMID 15978262 DOI: 10.1016/J.Exer.2005.02.014 |
0.635 |
|
| 2005 |
Daniele LL, Lillo C, Lyubarsky AL, Nikonov SS, Philp N, Mears AJ, Swaroop A, Williams DS, Pugh EN. Cone-like morphological, molecular, and electrophysiological features of the photoreceptors of the Nrl knockout mouse. Investigative Ophthalmology & Visual Science. 46: 2156-67. PMID 15914637 DOI: 10.1167/Iovs.04-1427 |
0.303 |
|
| 2005 |
Karan G, Lillo C, Yang Z, Cameron DJ, Locke KG, Zhao Y, Thirumalaichary S, Li C, Birch DG, Vollmer-Snarr HR, Williams DS, Zhang K. Lipofuscin accumulation, abnormal electrophysiology, and photoreceptor degeneration in mutant ELOVL4 transgenic mice: a model for macular degeneration. Proceedings of the National Academy of Sciences of the United States of America. 102: 4164-9. PMID 15749821 DOI: 10.1073/Pnas.0407698102 |
0.316 |
|
| 2005 |
Otto EA, Loeys B, Khanna H, Hellemans J, Sudbrak R, Fan S, Muerb U, O'Toole JF, Helou J, Attanasio M, Utsch B, Sayer JA, Lillo C, Jimeno D, Coucke P, ... ... Williams DS, et al. Nephrocystin-5, a ciliary IQ domain protein, is mutated in Senior-Loken syndrome and interacts with RPGR and calmodulin. Nature Genetics. 37: 282-8. PMID 15723066 DOI: 10.1038/Ng1520 |
0.342 |
|
| 2004 |
Gibbs D, Azarian SM, Lillo C, Kitamoto J, Klomp AE, Steel KP, Libby RT, Williams DS. Role of myosin VIIa and Rab27a in the motility and localization of RPE melanosomes. Journal of Cell Science. 117: 6473-83. PMID 15572405 DOI: 10.1242/Jcs.01580 |
0.607 |
|
| 2004 |
Libby RT, Lillo C, Kitamoto J, Williams DS, Steel KP. Myosin Va is required for normal photoreceptor synaptic activity. Journal of Cell Science. 117: 4509-15. PMID 15316067 DOI: 10.1242/Jcs.01316 |
0.312 |
|
| 2003 |
Gibbs D, Williams DS. Isolation and culture of primary mouse retinal pigmented epithelial cells. Advances in Experimental Medicine and Biology. 533: 347-52. PMID 15180284 DOI: 10.1007/978-1-4615-0067-4_44 |
0.514 |
|
| 2003 |
Lillo C, Kitamoto J, Liu X, Quint E, Steel KP, Williams DS. Mouse models for Usher syndrome 1B. Advances in Experimental Medicine and Biology. 533: 143-50. PMID 15180258 DOI: 10.1007/978-1-4615-0067-4_18 |
0.341 |
|
| 2003 |
Libby RT, Kitamoto J, Holme RH, Williams DS, Steel KP. Cdh23 mutations in the mouse are associated with retinal dysfunction but not retinal degeneration. Experimental Eye Research. 77: 731-9. PMID 14609561 DOI: 10.1016/J.Exer.2003.07.007 |
0.355 |
|
| 2003 |
Gibbs D, Kitamoto J, Williams DS. Abnormal phagocytosis by retinal pigmented epithelium that lacks myosin VIIa, the Usher syndrome 1B protein. Proceedings of the National Academy of Sciences of the United States of America. 100: 6481-6. PMID 12743369 DOI: 10.1073/Pnas.1130432100 |
0.643 |
|
| 2002 |
Udovichenko IP, Gibbs D, Williams DS. Actin-based motor properties of native myosin VIIa. Journal of Cell Science. 115: 445-50. PMID 11839794 |
0.482 |
|
| 2001 |
Liu X, Williams DS. Coincident onset of expression of myosin VIIa and opsin in the cilium of the developing photoreceptor cell Experimental Eye Research. 72: 351-355. PMID 11180984 DOI: 10.1006/Exer.2000.0963 |
0.304 |
|
| 2000 |
Marszalek JR, Liu X, Roberts EA, Chui D, Marth JD, Williams DS, Goldstein LS. Genetic evidence for selective transport of opsin and arrestin by kinesin-II in mammalian photoreceptors. Cell. 102: 175-87. PMID 10943838 DOI: 10.1016/S0092-8674(00)00023-4 |
0.321 |
|
| 1999 |
Liu X, Udovichenko IP, Brown SDM, Steel KP, Williams DS. Myosin VIIa Participates in Opsin Transport through The Photoreceptor Cilium The Journal of Neuroscience. 19: 6267-6274. DOI: 10.1523/Jneurosci.19-15-06267.1999 |
0.336 |
|
| 1998 |
Wolfrum U, Liu X, Schmitt A, Udovichenko IP, Williams DS. Myosin VIIa as a Common Component of Cilia and Microvilli Cytoskeleton. 40: 261-271. PMID 9678669 DOI: 10.1002/(Sici)1097-0169(1998)40:3<261::Aid-Cm5>3.0.Co;2-G |
0.323 |
|
| 1997 |
Liu X, Vansant G, Udovichenko IP, Wolfrum U, Williams DS. Myosin VIIa, the product of the Usher 1B syndrome gene, is concentrated in the connecting cilia of photoreceptor cells. Cytoskeleton. 37: 240-252. PMID 9227854 DOI: 10.1002/(Sici)1097-0169(1997)37:3<240::Aid-Cm6>3.0.Co;2-A |
0.383 |
|
| 1997 |
Boesze-Battaglia K, Kong F, Lamba OP, Stefano FP, Williams DS. Purification and light-dependent phosphorylation of a candidate fusion protein, the photoreceptor cell peripherin/rds. Biochemistry. 36: 6835-46. PMID 9184167 DOI: 10.1021/Bi9627370 |
0.34 |
|
| 1996 |
Schlamp CL, Williams DS. Myosin V in the retina: Localization in the rod photoreceptor synapse Experimental Eye Research. 63: 613-619. PMID 9068368 DOI: 10.1006/Exer.1996.0155 |
0.309 |
|
| 1996 |
Hicks JL, Liu X, Williams DS. Role of the ninaC proteins in photoreceptor cell structure: Ultrastructure of ninaC deletion mutants and binding to actin filaments Cell Motility and the Cytoskeleton. 35: 367-379. PMID 8956007 DOI: 10.1002/(Sici)1097-0169(1996)35:4<367::Aid-Cm8>3.0.Co;2-3 |
0.309 |
|
| 1995 |
Azarian SM, King AJ, Hallett MA, Williams DS. Selective Proteolysis of Arrestin by Calpain MOLECULAR CHARACTERISTICS AND ITS EFFECT ON RHODOPSIN DEPHOSPHORYLATION Journal of Biological Chemistry. 270: 24375-24384. PMID 7592650 DOI: 10.1074/Jbc.270.41.24375 |
0.3 |
|
| 1992 |
Arikawa K, Molday LL, Molday RS, Williams DS. Localization of peripherin/rds in the disk membranes of cone and rod photoreceptors: Relationship to disk membrane morphogenesis and retinal degeneration Journal of Cell Biology. 116: 659-667. PMID 1730772 DOI: 10.1083/Jcb.116.3.659 |
0.343 |
|
| 1991 |
Arikawa K, Williams DS. Alpha-actinin and actin in the outer retina: A double immunoelectron microscopic study Cell Motility and the Cytoskeleton. 18: 15-25. PMID 2004431 DOI: 10.1002/Cm.970180103 |
0.302 |
|
| 1990 |
Williams DS, Arikawa K, Paallysaho T. Cytoskeletal components of the adherens junctions between the photoreceptors and the supportive Muller cells Journal of Comparative Neurology. 295: 155-164. PMID 2341633 DOI: 10.1002/Cne.902950113 |
0.334 |
|
| 1990 |
Williams DS, Linberg KA, Fisher SK. Shedding of cone photoreceptor disk membranes in lizard eyecups maintained in vitro. Experimental Eye Research. 50: 231-3. PMID 2311685 DOI: 10.1016/0014-4835(90)90236-N |
0.302 |
|
| 1989 |
Williams DS, Shuster TA, Moldrawski MR, Blest AD, Farber DB. Isolation of rod outer segments on Percoll gradients: Effect of specific protease inhibition Experimental Eye Research. 49: 439-444. PMID 2551708 DOI: 10.1016/0014-4835(89)90052-3 |
0.302 |
|
| 1988 |
Williams DS, Linberg KA, Vaughan DK, Fariss RN, Fisher SK. Disruption of microfilament organization and deregulation of disk membrane morphogenesis by cytochalasin D in rod and cone photoreceptors. The Journal of Comparative Neurology. 272: 161-76. PMID 3397406 DOI: 10.1002/Cne.902720202 |
0.306 |
|
| 1988 |
Anderson DH, Williams DS, Neitz J, Fariss RN, Fliesler SJ. Tunicamycin-induced degeneration in cone photoreceptors. Visual Neuroscience. 1: 153-8. PMID 3154792 DOI: 10.1017/S0952523800001425 |
0.339 |
|
| 1980 |
Williams DS, Blest AD. Extracellular shedding of photoreceptor membrane in the open rhabdom of a tipulid fly Cell and Tissue Research. 205: 423-438. PMID 7357581 DOI: 10.1007/Bf00232283 |
0.308 |
|
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