| Year |
Citation |
Score |
| 2018 |
LeGrys VA, Moon TC, Laux J, Accurso F, Martiniano SA. A multicenter evaluation of sweat chloride concentration and variation in infants with cystic fibrosis. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. PMID 30583934 DOI: 10.1016/J.Jcf.2018.12.006 |
0.386 |
|
| 2018 |
DeBoer EM, Wagner BD, Popler J, Harris JK, Zemanick ET, Accurso FJ, Sagel SD, Deterding RR. Novel Application of Aptamer Proteomic Analysis in Cystic Fibrosis Bronchoalveolar Lavage Fluid. Proteomics. Clinical Applications. e1800085. PMID 30431231 DOI: 10.1002/Prca.201800085 |
0.464 |
|
| 2018 |
Hoppe JE, Wagner BD, Accurso FJ, Zemanick ET, Sagel SD. Characteristics and outcomes of oral antibiotic treated pulmonary exacerbations in children with cystic fibrosis. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. PMID 29921503 DOI: 10.1016/J.Jcf.2018.05.015 |
0.434 |
|
| 2018 |
Mayer-Hamblett N, Retsch-Bogart G, Kloster M, Accurso F, Rosenfeld M, Albers G, Black P, Brown P, Cairns A, Davis SD, Graff GR, Kerby GS, Orenstein D, Buckingham R, Ramsey BW, et al. Azithromycin for Early Pseudomonas Infection in Cystic Fibrosis: The Optimize Randomized Trial. American Journal of Respiratory and Critical Care Medicine. PMID 29890086 DOI: 10.1164/Rccm.201802-0215Oc |
0.378 |
|
| 2018 |
Accurso FJ. Treatment of cystic fibrosis in infants. The Lancet. Respiratory Medicine. PMID 29886025 DOI: 10.1016/S2213-2600(18)30203-0 |
0.395 |
|
| 2017 |
Jain R, Beckett VV, Konstan MW, Accurso FJ, Burns JL, Mayer-Hamblett N, Milla C, VanDevanter DR, Chmiel JF. KB001-A, a novel anti-inflammatory, found to be safe and well-tolerated in cystic fibrosis patients infected with Pseudomonas aeruginosa. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. PMID 29292092 DOI: 10.1016/J.Jcf.2017.12.006 |
0.401 |
|
| 2017 |
Hoppe JE, Wagner BD, Sagel SD, Accurso FJ, Zemanick ET. Pulmonary exacerbations and clinical outcomes in a longitudinal cohort of infants and preschool children with cystic fibrosis. Bmc Pulmonary Medicine. 17: 188. PMID 29228933 DOI: 10.1186/S12890-017-0546-8 |
0.456 |
|
| 2017 |
Zemanick ET, Wagner BD, Robertson CE, Ahrens RC, Chmiel JF, Clancy JP, Gibson RL, Harris WT, Kurland G, Laguna TA, McColley SA, McCoy K, Retsch-Bogart G, Sobush KT, Zeitlin PL, ... ... Accurso FJ, et al. Airway microbiota across age and disease spectrum in cystic fibrosis. The European Respiratory Journal. 50. PMID 29146601 DOI: 10.1183/13993003.00832-2017 |
0.479 |
|
| 2017 |
Pittman JE, Noah H, Calloway HE, Davis SD, Leigh MW, Drumm M, Sagel SD, Accurso FJ, Knowles MR, Sontag MK. Early childhood lung function is a stronger predictor of adolescent lung function in cystic fibrosis than early Pseudomonas aeruginosa infection. Plos One. 12: e0177215. PMID 28505188 DOI: 10.1371/Journal.Pone.0177215 |
0.437 |
|
| 2017 |
DeBoer EM, Kroehl M, Wagner BD, Accurso F, Harris JK, Lynch DA, Sagel SD, Deterding RR. Proteomic profiling identifies novel circulating markers associated with bronchiectasis in cystic fibrosis. Proteomics. Clinical Applications. PMID 28452194 DOI: 10.1002/Prca.201600147 |
0.424 |
|
| 2017 |
Hisert KB, Heltshe SL, Pope C, Jorth P, Wu X, Edwards RM, Radey M, Accurso FJ, Wolter DJ, Cooke G, Adam RJ, Carter S, Grogan B, Launspach JL, Donnelly SC, et al. Restoring CFTR Function Reduces Airway Bacteria and Inflammation in People With Cystic Fibrosis and Chronic Lung Infections. American Journal of Respiratory and Critical Care Medicine. PMID 28222269 DOI: 10.1164/Rccm.201609-1954Oc |
0.478 |
|
| 2017 |
Farrell PM, White TB, Ren CL, Hempstead SE, Accurso F, Derichs N, Howenstine M, McColley SA, Rock M, Rosenfeld M, Sermet-Gaudelus I, Southern KW, Marshall BC, Sosnay PR. Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation. The Journal of Pediatrics. 181: S4-S15.e1. PMID 28129811 DOI: 10.1016/J.Jpeds.2016.09.064 |
0.396 |
|
| 2017 |
Farrell PM, White TB, Howenstine MS, Munck A, Parad RB, Rosenfeld M, Sommerburg O, Accurso FJ, Davies JC, Rock MJ, Sanders DB, Wilschanski M, Sermet-Gaudelus I, Blau H, Gartner S, et al. Diagnosis of Cystic Fibrosis in Screened Populations. The Journal of Pediatrics. 181: S33-S44.e2. PMID 28129810 DOI: 10.1016/J.Jpeds.2016.09.065 |
0.606 |
|
| 2016 |
Muhlebach MS, Clancy JP, Heltshe SL, Ziady A, Kelley T, Accurso F, Pilewski J, Mayer-Hamblett N, Joseloff E, Sagel SD. Biomarkers for cystic fibrosis drug development. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 15: 714-723. PMID 28215711 DOI: 10.1016/J.Jcf.2016.10.009 |
0.317 |
|
| 2016 |
Taylor-Cousar JL, Janssen JS, Wilson A, Clair CG, Pickard KM, Jones MC, Brayshaw SJ, Chacon CS, Barboa CM, Sontag MK, Accurso FJ, Nichols DP, Saavedra MT, Nick JA. Glucose >200 mg/dL during Continuous Glucose Monitoring Identifies Adult Patients at Risk for Development of Cystic Fibrosis Related Diabetes. Journal of Diabetes Research. 2016: 1527932. PMID 27999822 DOI: 10.1155/2016/1527932 |
0.395 |
|
| 2016 |
Woodruff SA, Sontag MK, Accurso FJ, Sokol RJ, Narkewicz MR. Prevalence of elevated liver enzymes in children with cystic fibrosis diagnosed by newborn screen. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. PMID 27555301 DOI: 10.1016/J.Jcf.2016.08.002 |
0.357 |
|
| 2016 |
Johnson EJ, Zemanick ET, Accurso FJ, Wagner BD, Robertson CE, Harris JK. Molecular Identification of Staphylococcus aureus in Airway Samples from Children with Cystic Fibrosis. Plos One. 11: e0147643. PMID 26808658 DOI: 10.1371/Journal.Pone.0147643 |
0.384 |
|
| 2016 |
Sullivan J, Accurso F, Marigowda G, Beusmans J, Geho D, Zhang E, Moss R, Waltz D. WS04.2 Improvement in inflammatory biomarkers in patients (pts) with cystic fibrosis (CF) homozygous for the F508del-CFTR mutation treated with lumacaftor (LUM) and ivacaftor (IVA) Journal of Cystic Fibrosis. 15: S6. DOI: 10.1016/S1569-1993(16)30079-0 |
0.426 |
|
| 2015 |
Corvol H, Blackman SM, Boëlle PY, Gallins PJ, Pace RG, Stonebraker JR, Accurso FJ, Clement A, Collaco JM, Dang H, Dang AT, Franca A, Gong J, Guillot L, Keenan K, et al. Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis. Nature Communications. 6: 8382. PMID 26417704 DOI: 10.1038/Ncomms9382 |
0.427 |
|
| 2015 |
Accurso FJ. Cystic fibrosis, ivacaftor, and the Arg117His-CFTR mutation. The Lancet. Respiratory Medicine. 3: 498-9. PMID 26170070 DOI: 10.1016/S2213-2600(15)00246-5 |
0.382 |
|
| 2015 |
Torphy TJ, Allen J, Cantin AM, Konstan MW, Accurso FJ, Joseloff E, Ratjen FA, Chmiel JF. Considerations for the Conduct of Clinical Trials with Anti-inflammatory Agents in Cystic Fibrosis: A Cystic Fibrosis Foundation Workshop Report. Annals of the American Thoracic Society. PMID 26146892 DOI: 10.1513/Annalsats.201506-361Ot |
0.447 |
|
| 2015 |
Chmiel JF, Konstan MW, Accurso FJ, Lymp J, Mayer-Hamblett N, VanDevanter DR, Rose LM, Ramsey BW. Use of ibuprofen to assess inflammatory biomarkers in induced sputum: Implications for clinical trials in cystic fibrosis. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. PMID 25869324 DOI: 10.1016/J.Jcf.2015.03.007 |
0.33 |
|
| 2015 |
Miller MR, Soave D, Li W, Gong J, Pace RG, Boëlle PY, Cutting GR, Drumm ML, Knowles MR, Sun L, Rommens JM, Accurso F, Durie PR, Corvol H, Levy H, et al. Variants in Solute Carrier SLC26A9 Modify Prenatal Exocrine Pancreatic Damage in Cystic Fibrosis. The Journal of Pediatrics. 166: 1152-1157.e6. PMID 25771386 DOI: 10.1016/J.Jpeds.2015.01.044 |
0.434 |
|
| 2015 |
Flass T, Tong S, Frank DN, Wagner BD, Robertson CE, Kotter CV, Sokol RJ, Zemanick E, Accurso F, Hoffenberg EJ, Narkewicz MR. Intestinal lesions are associated with altered intestinal microbiome and are more frequent in children and young adults with cystic fibrosis and cirrhosis. Plos One. 10: e0116967. PMID 25658710 DOI: 10.1371/Journal.Pone.0116967 |
0.359 |
|
| 2015 |
Hoppe JE, Towler E, Wagner BD, Accurso FJ, Sagel SD, Zemanick ET. Sputum induction improves detection of pathogens in children with cystic fibrosis. Pediatric Pulmonology. 50: 638-46. PMID 25565628 DOI: 10.1002/Ppul.23150 |
0.443 |
|
| 2015 |
Zemanick ET, Wagner BD, Robertson CE, Stevens MJ, Szefler SJ, Accurso FJ, Sagel SD, Harris JK. Assessment of airway microbiota and inflammation in cystic fibrosis using multiple sampling methods. Annals of the American Thoracic Society. 12: 221-9. PMID 25474078 DOI: 10.1513/Annalsats.201407-310Oc |
0.395 |
|
| 2015 |
Taylor-Cousar JL, Wiley C, Felton LA, St Clair C, Jones M, Curran-Everett D, Poch K, Nichols DP, Solomon GM, Saavedra MT, Accurso FJ, Nick JA. Pharmacokinetics and tolerability of oral sildenafil in adults with cystic fibrosis lung disease. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 14: 228-36. PMID 25466700 DOI: 10.1016/J.Jcf.2014.10.006 |
0.474 |
|
| 2014 |
Kerem E, Konstan MW, De Boeck K, Accurso FJ, Sermet-Gaudelus I, Wilschanski M, Elborn JS, Melotti P, Bronsveld I, Fajac I, Malfroot A, Rosenbluth DB, Walker PA, McColley SA, Knoop C, et al. Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial. The Lancet. Respiratory Medicine. 2: 539-47. PMID 24836205 DOI: 10.1016/S2213-2600(14)70100-6 |
0.354 |
|
| 2014 |
Zemanick ET, Accurso FJ. Cystic fibrosis transmembrane conductance regulator and pseudomonas. American Journal of Respiratory and Critical Care Medicine. 189: 763-5. PMID 24684355 DOI: 10.1164/Rccm.201402-0209Ed |
0.392 |
|
| 2014 |
Accurso FJ, Van Goor F, Zha J, Stone AJ, Dong Q, Ordonez CL, Rowe SM, Clancy JP, Konstan MW, Hoch HE, Heltshe SL, Ramsey BW, Campbell PW, Ashlock MA. Sweat chloride as a biomarker of CFTR activity: proof of concept and ivacaftor clinical trial data. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 13: 139-47. PMID 24660233 DOI: 10.1016/J.Jcf.2013.09.007 |
0.393 |
|
| 2014 |
Courville CA, Tidwell S, Liu B, Accurso FJ, Dransfield MT, Rowe SM. Acquired defects in CFTR-dependent β-adrenergic sweat secretion in chronic obstructive pulmonary disease. Respiratory Research. 15: 25. PMID 24568560 DOI: 10.1186/1465-9921-15-25 |
0.407 |
|
| 2014 |
Soave D, Miller MR, Keenan K, Li W, Gong J, Ip W, Accurso F, Sun L, Rommens JM, Sontag M, Durie PR, Strug LJ. Evidence for a causal relationship between early exocrine pancreatic disease and cystic fibrosis-related diabetes: a Mendelian randomization study. Diabetes. 63: 2114-9. PMID 24550193 DOI: 10.2337/Db13-1464 |
0.411 |
|
| 2014 |
Milla CE, Chmiel JF, Accurso FJ, VanDevanter DR, Konstan MW, Yarranton G, Geller DE. Anti-PcrV antibody in cystic fibrosis: a novel approach targeting Pseudomonas aeruginosa airway infection. Pediatric Pulmonology. 49: 650-8. PMID 24019259 DOI: 10.1002/Ppul.22890 |
0.372 |
|
| 2014 |
Kerem E, Wilschanski M, Sermet-Gaudelus I, De Boeck K, Accurso F, Konstan M, Rowe S, Elfring G, Spiegel R, Peltz S, Barth J, Ajayi T. 94 The effect of Pseudomonas aeruginosa infection on pulmonary function outcome in a cohort of patients with nonsense mutation cystic fibrosis Journal of Cystic Fibrosis. 13: S70. DOI: 10.1016/S1569-1993(14)60230-7 |
0.4 |
|
| 2013 |
Konstan MW, Accurso FJ, Nasr SZ, Ahrens RC, Graff GR. Efficacy and safety of a unique enteric-coated bicarbonate-buffered pancreatic enzyme replacement therapy in children and adults with cystic fibrosis. Clinical Investigation. 3: 723-729. PMID 25210613 DOI: 10.4155/Cli.13.62 |
0.317 |
|
| 2013 |
Wagner BD, Takatsuki S, Accurso FJ, Ivy DD. Evaluation of circulating proteins and hemodynamics towards predicting mortality in children with pulmonary arterial hypertension. Plos One. 8: e80235. PMID 24278261 DOI: 10.1371/Journal.Pone.0080235 |
0.308 |
|
| 2013 |
Popler J, Wagner BD, Tarro HL, Accurso FJ, Deterding RR. Bronchoalveolar lavage fluid cytokine profiles in neuroendocrine cell hyperplasia of infancy and follicular bronchiolitis. Orphanet Journal of Rare Diseases. 8: 175. PMID 24216293 DOI: 10.1186/1750-1172-8-175 |
0.341 |
|
| 2013 |
Raju SV, Jackson PL, Courville CA, McNicholas CM, Sloane PA, Sabbatini G, Tidwell S, Tang LP, Liu B, Fortenberry JA, Jones CW, Boydston JA, Clancy JP, Bowen LE, Accurso FJ, et al. Cigarette smoke induces systemic defects in cystic fibrosis transmembrane conductance regulator function. American Journal of Respiratory and Critical Care Medicine. 188: 1321-30. PMID 24040746 DOI: 10.1164/Rccm.201304-0733Oc |
0.326 |
|
| 2013 |
Rowe SM, Liu B, Hill A, Hathorne H, Cohen M, Beamer JR, Accurso FJ, Dong Q, Ordoñez CL, Stone AJ, Olson ER, Clancy JP. Optimizing nasal potential difference analysis for CFTR modulator development: assessment of ivacaftor in CF subjects with the G551D-CFTR mutation. Plos One. 8: e66955. PMID 23922647 DOI: 10.1371/Journal.Pone.0066955 |
0.332 |
|
| 2013 |
Zemanick ET, Harris JK, Wagner BD, Robertson CE, Sagel SD, Stevens MJ, Accurso FJ, Laguna TA. Inflammation and airway microbiota during cystic fibrosis pulmonary exacerbations. Plos One. 8: e62917. PMID 23646159 DOI: 10.1371/Journal.Pone.0062917 |
0.471 |
|
| 2013 |
Ajayi T, Konstan M, Accurso F, De Boeck K, Kerem E, Rowe S, Sermet-Gaudelus I, Wilschanski M, Brody A, Miller N, Elfring G, Spiegel R, Peltz S, Barth J. 63 The use of high resolution computerized tomography of the chest in evaluating the effect of ataluren in nonsense mutation cystic fibrosis (nmCF) lung disease Journal of Cystic Fibrosis. 12: S64. DOI: 10.1016/S1569-1993(13)60205-2 |
0.38 |
|
| 2013 |
Accurso FJ, Ratjen F, Altes T, Lubarsky B, Dong Q, Kang L, Davies J. 56 Effect of withdrawal of ivacaftor therapy on CFTR channel activity and lung function in patients with cystic fibrosis Journal of Cystic Fibrosis. 12. DOI: 10.1016/S1569-1993(13)60198-8 |
0.389 |
|
| 2013 |
Kerem E, Wilschanski M, Sermet-Gaudelus I, De Boeck K, Accurso F, Konstan M, Rowe S, Miller N, Elfring G, Spiegel R, Peltz S, Barth J, Ajayi T. WS7.5 Interim results of the phase 3 open-label study of ataluren in nonsense mutation cystic fibrosis (nmCF) Journal of Cystic Fibrosis. 12: S15. DOI: 10.1016/S1569-1993(13)60044-2 |
0.326 |
|
| 2012 |
Ratjen F, Durham T, Navratil T, Schaberg A, Accurso FJ, Wainwright C, Barnes M, Moss RB. Long term effects of denufosol tetrasodium in patients with cystic fibrosis. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 11: 539-49. PMID 22682898 DOI: 10.1016/J.Jcf.2012.05.003 |
0.326 |
|
| 2012 |
Laguna TA, Wagner BD, Starcher B, Luckey Tarro HK, Mann SA, Sagel SD, Accurso FJ. Urinary desmosine: a biomarker of structural lung injury during CF pulmonary exacerbation. Pediatric Pulmonology. 47: 856-63. PMID 22431382 DOI: 10.1002/ppul.22525 |
0.363 |
|
| 2012 |
Ramsey BW, Banks-Schlegel S, Accurso FJ, Boucher RC, Cutting GR, Engelhardt JF, Guggino WB, Karp CL, Knowles MR, Kolls JK, LiPuma JJ, Lynch S, McCray PB, Rubenstein RC, Singh PK, et al. Future directions in early cystic fibrosis lung disease research: an NHLBI workshop report. American Journal of Respiratory and Critical Care Medicine. 185: 887-92. PMID 22312017 DOI: 10.1164/Rccm.201111-2068Ws |
0.4 |
|
| 2011 |
Accurso FJ, Moss RB, Wilmott RW, Anbar RD, Schaberg AE, Durham TA, Ramsey BW. Denufosol tetrasodium in patients with cystic fibrosis and normal to mildly impaired lung function. American Journal of Respiratory and Critical Care Medicine. 183: 627-34. PMID 21169471 DOI: 10.1164/Rccm.201008-1267Oc |
0.438 |
|
| 2011 |
Cooley J, Sontag MK, Accurso FJ, Remold-O'Donnell E. SerpinB1 in cystic fibrosis airway fluids: quantity, molecular form and mechanism of elastase inhibition. The European Respiratory Journal. 37: 1083-90. PMID 20817705 DOI: 10.1183/09031936.00073710 |
0.486 |
|
| 2010 |
Zemanick ET, Wagner BD, Sagel SD, Stevens MJ, Accurso FJ, Harris JK. Reliability of quantitative real-time PCR for bacterial detection in cystic fibrosis airway specimens. Plos One. 5: e15101. PMID 21152087 DOI: 10.1371/Journal.Pone.0015101 |
0.446 |
|
| 2010 |
Accurso FJ, Rowe SM, Clancy JP, Boyle MP, Dunitz JM, Durie PR, Sagel SD, Hornick DB, Konstan MW, Donaldson SH, Moss RB, Pilewski JM, Rubenstein RC, Uluer AZ, Aitken ML, et al. Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation. The New England Journal of Medicine. 363: 1991-2003. PMID 21083385 DOI: 10.1056/Nejmoa0909825 |
0.425 |
|
| 2010 |
Zemanick ET, Wagner BD, Harris JK, Wagener JS, Accurso FJ, Sagel SD. Pulmonary exacerbations in cystic fibrosis with negative bacterial cultures. Pediatric Pulmonology. 45: 569-77. PMID 20503282 DOI: 10.1002/Ppul.21221 |
0.485 |
|
| 2010 |
Solomon GM, Konstan MW, Wilschanski M, Billings J, Sermet-Gaudelus I, Accurso F, Vermeulen F, Levin E, Hathorne H, Reeves G, Sabbatini G, Hill A, Mayer-Hamblett N, Ashlock M, Clancy JP, et al. An international randomized multicenter comparison of nasal potential difference techniques. Chest. 138: 919-28. PMID 20472865 DOI: 10.1378/Chest.10-0179 |
0.326 |
|
| 2010 |
Nick JA, Chacon CS, Brayshaw SJ, Jones MC, Barboa CM, St Clair CG, Young RL, Nichols DP, Janssen JS, Huitt GA, Iseman MD, Daley CL, Taylor-Cousar JL, Accurso FJ, Saavedra MT, et al. Effects of gender and age at diagnosis on disease progression in long-term survivors of cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 182: 614-26. PMID 20448091 DOI: 10.1164/Rccm.201001-0092Oc |
0.384 |
|
| 2010 |
Modi AC, Cassedy AE, Quittner AL, Accurso F, Sontag M, Koenig JM, Ittenbach RF. Trajectories of adherence to airway clearance therapy for patients with cystic fibrosis. Journal of Pediatric Psychology. 35: 1028-37. PMID 20304772 DOI: 10.1093/Jpepsy/Jsq015 |
0.432 |
|
| 2010 |
Wagner BD, Accurso FJ, Laguna TA. The applicability of urinary creatinine as a method of specimen normalization in the cystic fibrosis population. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 9: 212-6. PMID 20227353 DOI: 10.1016/J.Jcf.2010.02.004 |
0.414 |
|
| 2010 |
Sontag MK, Quittner AL, Modi AC, Koenig JM, Giles D, Oermann CM, Konstan MW, Castile R, Accurso FJ. Lessons learned from a randomized trial of airway secretion clearance techniques in cystic fibrosis. Pediatric Pulmonology. 45: 291-300. PMID 20146387 DOI: 10.1002/Ppul.21179 |
0.401 |
|
| 2010 |
Zemanick ET, Harris JK, Conway S, Konstan MW, Marshall B, Quittner AL, Retsch-Bogart G, Saiman L, Accurso FJ. Measuring and improving respiratory outcomes in cystic fibrosis lung disease: opportunities and challenges to therapy. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 9: 1-16. PMID 19833563 DOI: 10.1016/J.Jcf.2009.09.003 |
0.48 |
|
| 2010 |
Accurso FJ, Durham T, Navratil T, Deans C, Herje N, Smiley L, Schaberg A. Analysis of polypharmacy in patients with mild CF lung disease assigned to placebo in phase 3 clinical trial of denufosol Journal of Cystic Fibrosis. 9. DOI: 10.1016/S1569-1993(10)60216-0 |
0.394 |
|
| 2010 |
Treggiari M, Retsch-Bogart G, Mayer-Hamblett N, Khan U, Kronmal R, Ramsey B, Accurso F. Comparative efficacy and safety of four randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis Journal of Cystic Fibrosis. 9: S54. DOI: 10.1016/S1569-1993(10)60210-X |
0.343 |
|
| 2010 |
Navratil T, Evans C, Schaberg A, Johnson F, Durham T, Ren C, Ratjen F, Moss R, Accurso F. Aerosol and pharmacokinetic properties of denufosol support its use for early intervention in CF lung disease Journal of Cystic Fibrosis. 9: S21. DOI: 10.1016/S1569-1993(10)60079-3 |
0.39 |
|
| 2010 |
Accurso F, Tian W, Schaberg A, Navratil T, Howenstine M, Liou T. Potential of denufosol as an early intervention in CF lung disease: efficacy in patients with minimal pharmacotherapy in a US phase 3 clinical trial Journal of Cystic Fibrosis. 9: S21. DOI: 10.1016/S1569-1993(10)60078-1 |
0.346 |
|
| 2010 |
Moss RB, Schaberg A, Deans C, Tian W, Smiley L, Herje N, Durham T, Accurso FJ. Denufosol improves lung function in adolescent CF patients Journal of Cystic Fibrosis. 9. DOI: 10.1016/S1569-1993(10)60077-X |
0.378 |
|
| 2009 |
Borowitz D, Robinson KA, Rosenfeld M, Davis SD, Sabadosa KA, Spear SL, Michel SH, Parad RB, White TB, Farrell PM, Marshall BC, Accurso FJ. Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis. The Journal of Pediatrics. 155: S73-93. PMID 19914445 DOI: 10.1016/J.Jpeds.2009.09.001 |
0.669 |
|
| 2009 |
Borowitz D, Parad RB, Sharp JK, Sabadosa KA, Robinson KA, Rock MJ, Farrell PM, Sontag MK, Rosenfeld M, Davis SD, Marshall BC, Accurso FJ. Cystic Fibrosis Foundation practice guidelines for the management of infants with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome during the first two years of life and beyond. The Journal of Pediatrics. 155: S106-16. PMID 19914443 DOI: 10.1016/J.Jpeds.2009.09.003 |
0.675 |
|
| 2009 |
Dorfman R, Li W, Sun L, Lin F, Wang Y, Sandford A, Paré PD, McKay K, Kayserova H, Piskackova T, Macek M, Czerska K, Sands D, Tiddens H, Margarit S, ... ... Accurso FJ, et al. Modifier gene study of meconium ileus in cystic fibrosis: statistical considerations and gene mapping results. Human Genetics. 126: 763-78. PMID 19662435 DOI: 10.1007/S00439-009-0724-8 |
0.363 |
|
| 2009 |
Kalka-Moll WM, LiPuma JJ, Accurso FJ, Plum G, van Koningsbruggen S, Vandamme P. Airway infection with a novel Cupriavidus species in persons with cystic fibrosis. Journal of Clinical Microbiology. 47: 3026-8. PMID 19605576 DOI: 10.1128/Jcm.00846-09 |
0.431 |
|
| 2009 |
Laguna TA, Wagner BD, Luckey HK, Mann SA, Sagel SD, Regelmann W, Accurso FJ. Sputum desmosine during hospital admission for pulmonary exacerbation in cystic fibrosis. Chest. 136: 1561-8. PMID 19567495 DOI: 10.1378/Chest.09-0217 |
0.443 |
|
| 2009 |
Sontag MK, Wright D, Beebe J, Accurso FJ, Sagel SD. A new cystic fibrosis newborn screening algorithm: IRT/IRT1 upward arrow/DNA. The Journal of Pediatrics. 155: 618-22. PMID 19540513 DOI: 10.1016/J.Jpeds.2009.03.057 |
0.37 |
|
| 2009 |
Sagel SD, Sontag MK, Accurso FJ. Relationship between antimicrobial proteins and airway inflammation and infection in cystic fibrosis. Pediatric Pulmonology. 44: 402-9. PMID 19283840 DOI: 10.1002/Ppul.21028 |
0.43 |
|
| 2009 |
Abman S, Jobe A, Chernick V, Blaisdell C, Castro M, Ramirez MI, Gern JE, Cutting G, Redding G, Hagood JS, Whitsett J, Abman S, Raj JU, Barst R, Kato GJ, ... ... Accurso F, et al. Strategic plan for pediatric respiratory diseases research: an NHLBI working group report. Pediatric Pulmonology. 44: 2-13. PMID 19086051 DOI: 10.1002/Ppul.20973 |
0.375 |
|
| 2009 |
Bernus A, Wagner BD, Accurso F, Doran A, Kaess H, Ivy DD. Brain natriuretic peptide levels in managing pediatric patients with pulmonary arterial hypertension. Chest. 135: 745-51. PMID 18849405 DOI: 10.1378/Chest.08-0187 |
0.307 |
|
| 2009 |
Accurso FJ, Durham TA, Schaberg AE. Relationship between pulmonary exacerbations and lung function decline in a six month trial of denufosol Journal of Cystic Fibrosis. 8. DOI: 10.1016/S1569-1993(09)60105-3 |
0.378 |
|
| 2009 |
Mospan A, Durham T, Schaberg A, Accurso F. Effects of denufosol on sinusitis-related complaints in a phase 3 trial in cystic fibrosis patients Journal of Cystic Fibrosis. 8: S26. DOI: 10.1016/S1569-1993(09)60104-1 |
0.346 |
|
| 2009 |
Accurso F, Rowe S, Durie P, Konstan M, Dunitz J, Hornick D, Sagel S, Boyle M, Uluer A, Moss R, Ramsey B, Freedman S, Dong Q, Zha J, Stone A, et al. Final results of a 14- and 28-day study of VX-770 in subjects with CF Journal of Cystic Fibrosis. 8: S25. DOI: 10.1016/S1569-1993(09)60101-6 |
0.338 |
|
| 2008 |
Saavedra MT, Hughes GJ, Sanders LA, Carr M, Rodman DM, Coldren CD, Geraci MW, Sagel SD, Accurso FJ, West J, Nick JA. Circulating RNA transcripts identify therapeutic response in cystic fibrosis lung disease. American Journal of Respiratory and Critical Care Medicine. 178: 929-38. PMID 18723435 DOI: 10.1164/Rccm.200803-387Oc |
0.428 |
|
| 2008 |
Farrell PM, Rosenstein BJ, White TB, Accurso FJ, Castellani C, Cutting GR, Durie PR, Legrys VA, Massie J, Parad RB, Rock MJ, Campbell PW. Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report. The Journal of Pediatrics. 153: S4-S14. PMID 18639722 DOI: 10.1016/J.Jpeds.2008.05.005 |
0.693 |
|
| 2008 |
Laguna TA, Sontag MK, Osberg I, Wagener JS, Accurso FJ, Sokol RJ. Decreased total serum coenzyme-Q10 concentrations: a longitudinal study in children with cystic fibrosis. The Journal of Pediatrics. 153: 402-7. PMID 18534204 DOI: 10.1016/J.Jpeds.2008.03.028 |
0.31 |
|
| 2008 |
Laguna TA, Sagel SD, Sontag MK, Accurso FJ. The clinical course of a Mexican female with cystic fibrosis and the novel genotype S531P/S531P. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 7: 454-6. PMID 18463004 DOI: 10.1016/J.Jcf.2008.03.008 |
0.371 |
|
| 2008 |
Accurso FJ. Update in cystic fibrosis 2007. American Journal of Respiratory and Critical Care Medicine. 177: 1058-61. PMID 18460460 DOI: 10.1164/Rccm.200801-069Up |
0.455 |
|
| 2008 |
Accurso FJ, Sontag MK. Gene modifiers in cystic fibrosis. The Journal of Clinical Investigation. 118: 839-41. PMID 18292812 DOI: 10.1172/Jci35138 |
0.463 |
|
| 2008 |
Cooley J, McDonald B, Accurso FJ, Crouch EC, Remold-O'Donnell E. Patterns of neutrophil serine protease-dependent cleavage of surfactant protein D in inflammatory lung disease. Journal of Leukocyte Biology. 83: 946-55. PMID 18211966 DOI: 10.1189/Jlb.1007684 |
0.307 |
|
| 2008 |
Papas KA, Sontag MK, Pardee C, Sokol RJ, Sagel SD, Accurso FJ, Wagener JS. A pilot study on the safety and efficacy of a novel antioxidant rich formulation in patients with cystic fibrosis. Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 7: 60-7. PMID 17569601 DOI: 10.1016/J.Jcf.2007.05.001 |
0.386 |
|
| 2007 |
Harris JK, De Groote MA, Sagel SD, Zemanick ET, Kapsner R, Penvari C, Kaess H, Deterding RR, Accurso FJ, Pace NR. Molecular identification of bacteria in bronchoalveolar lavage fluid from children with cystic fibrosis. Proceedings of the National Academy of Sciences of the United States of America. 104: 20529-33. PMID 18077362 DOI: 10.1073/Pnas.0709804104 |
0.449 |
|
| 2007 |
Moss RB, Milla C, Colombo J, Accurso F, Zeitlin PL, Clancy JP, Spencer LT, Pilewski J, Waltz DA, Dorkin HL, Ferkol T, Pian M, Ramsey B, Carter BJ, Martin DB, et al. Repeated aerosolized AAV-CFTR for treatment of cystic fibrosis: a randomized placebo-controlled phase 2B trial. Human Gene Therapy. 18: 726-32. PMID 17685853 DOI: 10.1089/Hum.2007.022 |
0.447 |
|
| 2007 |
Gibson RL, Emerson J, Mayer-Hamblett N, Burns JL, McNamara S, Accurso FJ, Konstan MW, Chatfield BA, Retsch-Bogart G, Waltz DA, Acton J, Zeitlin P, Hiatt P, Moss R, Williams J, et al. Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis. Pediatric Pulmonology. 42: 610-23. PMID 17534969 DOI: 10.1002/Ppul.20625 |
0.382 |
|
| 2007 |
Accurso FJ. Update in cystic fibrosis 2006. American Journal of Respiratory and Critical Care Medicine. 175: 754-7. PMID 17405941 DOI: 10.1164/Rccm.200701-160Up |
0.49 |
|
| 2007 |
Rancourt RC, Lee RL, O'Neill H, Accurso FJ, White CW. Reduced thioredoxin increases proinflammatory cytokines and neutrophil influx in rat airways: modulation by airway mucus. Free Radical Biology & Medicine. 42: 1441-53. PMID 17395017 DOI: 10.1016/J.Freeradbiomed.2007.02.007 |
0.426 |
|
| 2007 |
Comeau AM, Accurso FJ, White TB, Campbell PW, Hoffman G, Parad RB, Wilfond BS, Rosenfeld M, Sontag MK, Massie J, Farrell PM, O'Sullivan BP. Guidelines for implementation of cystic fibrosis newborn screening programs: Cystic Fibrosis Foundation workshop report. Pediatrics. 119: e495-518. PMID 17272609 DOI: 10.1542/Peds.2006-1993 |
0.633 |
|
| 2007 |
Mayer-Hamblett N, Aitken ML, Accurso FJ, Kronmal RA, Konstan MW, Burns JL, Sagel SD, Ramsey BW. Association between pulmonary function and sputum biomarkers in cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 175: 822-8. PMID 17234902 DOI: 10.1164/Rccm.200609-1354Oc |
0.468 |
|
| 2006 |
Sontag MK, Corey M, Hokanson JE, Marshall JA, Sommer SS, Zerbe GO, Accurso FJ. Genetic and physiologic correlates of longitudinal immunoreactive trypsinogen decline in infants with cystic fibrosis identified through newborn screening. The Journal of Pediatrics. 149: 650-657. PMID 17095337 DOI: 10.1016/J.Jpeds.2006.07.026 |
0.442 |
|
| 2006 |
Accurso FJ. Update in cystic fibrosis 2005. American Journal of Respiratory and Critical Care Medicine. 173: 944-7. PMID 16632633 DOI: 10.1164/Rccm.2601006 |
0.464 |
|
| 2005 |
Lee RL, Rancourt RC, del Val G, Pack K, Pardee C, Accurso FJ, White CW. Thioredoxin and dihydrolipoic acid inhibit elastase activity in cystic fibrosis sputum. American Journal of Physiology. Lung Cellular and Molecular Physiology. 289: L875-82. PMID 16214824 DOI: 10.1152/Ajplung.00103.2005 |
0.387 |
|
| 2005 |
Sontag MK, Hammond KB, Zielenski J, Wagener JS, Accurso FJ. Two-tiered immunoreactive trypsinogen-based newborn screening for cystic fibrosis in Colorado: screening efficacy and diagnostic outcomes. The Journal of Pediatrics. 147: S83-8. PMID 16202790 DOI: 10.1016/J.Jpeds.2005.08.005 |
0.413 |
|
| 2005 |
Accurso FJ, Sontag MK, Wagener JS. Complications associated with symptomatic diagnosis in infants with cystic fibrosis. The Journal of Pediatrics. 147: S37-41. PMID 16202780 DOI: 10.1016/J.Jpeds.2005.08.034 |
0.445 |
|
| 2005 |
Condino AA, Hoffenberg EJ, Accurso F, Penvari C, Anthony M, Gralla J, O'Connor JA. Frequency of ASCA seropositivity in children with cystic fibrosis. Journal of Pediatric Gastroenterology and Nutrition. 41: 23-6. PMID 15990625 DOI: 10.1097/01.Mpg.0000166801.61708.60 |
0.436 |
|
| 2005 |
Bush A, Accurso F, Macnee W, Lazarus SC, Abraham E. Cystic fibrosis, pediatrics, control of breathing, pulmonary physiology and anatomy, and surfactant biology in AJRCCM in 2004. American Journal of Respiratory and Critical Care Medicine. 171: 545-53. PMID 15753484 DOI: 10.1164/Rccm.2412007 |
0.351 |
|
| 2005 |
Rodman DM, Polis JM, Heltshe SL, Sontag MK, Chacon C, Rodman RV, Brayshaw SJ, Huitt GA, Iseman MD, Saavedra MT, Taussig LM, Wagener JS, Accurso FJ, Nick JA. Late diagnosis defines a unique population of long-term survivors of cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 171: 621-6. PMID 15591474 DOI: 10.1164/Rccm.200403-404Oc |
0.391 |
|
| 2004 |
Wagener JS, Sontag MK, Sagel SD, Accurso FJ. Update on newborn screening for cystic fibrosis. Current Opinion in Pulmonary Medicine. 10: 500-4. PMID 15510057 DOI: 10.1097/01.Mcp.0000138993.69390.Ef |
0.456 |
|
| 2004 |
Accurso F. Curcumin and cystic fibrosis. Journal of Pediatric Gastroenterology and Nutrition. 39: 235. PMID 15319620 DOI: 10.1097/00005176-200409000-00001 |
0.485 |
|
| 2004 |
Rubio F, Cooley J, Accurso FJ, Remold-O'Donnell E. Linkage of neutrophil serine proteases and decreased surfactant protein-A (SP-A) levels in inflammatory lung disease. Thorax. 59: 318-23. PMID 15047952 DOI: 10.1136/Thx.2003.014902 |
0.439 |
|
| 2004 |
Karp CL, Flick LM, Park KW, Softic S, Greer TM, Keledjian R, Yang R, Uddin J, Guggino WB, Atabani SF, Belkaid Y, Xu Y, Whitsett JA, Accurso FJ, Wills-Karp M, et al. Defective lipoxin-mediated anti-inflammatory activity in the cystic fibrosis airway. Nature Immunology. 5: 388-92. PMID 15034576 DOI: 10.1038/Ni1056 |
0.421 |
|
| 2004 |
Wooldridge JL, Deutsch GH, Sontag MK, Osberg I, Chase DR, Silkoff PE, Wagener JS, Abman SH, Accurso FJ. NO pathway in CF and non-CF children. Pediatric Pulmonology. 37: 338-50. PMID 15022131 DOI: 10.1002/Ppul.10455 |
0.439 |
|
| 2004 |
Rancourt RC, Tai S, King M, Heltshe SL, Penvari C, Accurso FJ, White CW. Thioredoxin liquefies and decreases the viscoelasticity of cystic fibrosis sputum. American Journal of Physiology. Lung Cellular and Molecular Physiology. 286: L931-8. PMID 14695120 DOI: 10.1152/Ajplung.00352.2003 |
0.346 |
|
| 2003 |
Saiman L, Marshall BC, Mayer-Hamblett N, Burns JL, Quittner AL, Cibene DA, Coquillette S, Fieberg AY, Accurso FJ, Campbell PW. Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial. Jama. 290: 1749-56. PMID 14519709 DOI: 10.1001/Jama.290.13.1749 |
0.477 |
|
| 2003 |
Ordoñez CL, Henig NR, Mayer-Hamblett N, Accurso FJ, Burns JL, Chmiel JF, Daines CL, Gibson RL, McNamara S, Retsch-Bogart GZ, Zeitlin PL, Aitken ML. Inflammatory and microbiologic markers in induced sputum after intravenous antibiotics in cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 168: 1471-5. PMID 12969869 DOI: 10.1164/Rccm.200306-731Oc |
0.351 |
|
| 2003 |
Wagener JS, Sontag MK, Accurso FJ. Newborn screening for cystic fibrosis. Current Opinion in Pediatrics. 15: 309-15. PMID 12806263 DOI: 10.1097/00008480-200306000-00015 |
0.33 |
|
| 2003 |
Maselli JH, Sontag MK, Norris JM, MacKenzie T, Wagener JS, Accurso FJ. Risk factors for initial acquisition of Pseudomonas aeruginosa in children with cystic fibrosis identified by newborn screening. Pediatric Pulmonology. 35: 257-62. PMID 12629621 DOI: 10.1002/Ppul.10230 |
0.381 |
|
| 2003 |
Accurso FJ, Sontag MK. Seeking modifier genes in cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 167: 289-90. PMID 12554616 DOI: 10.1164/Rccm.2210006 |
0.378 |
|
| 2003 |
Gibson RL, Emerson J, McNamara S, Burns JL, Rosenfeld M, Yunker A, Hamblett N, Accurso F, Dovey M, Hiatt P, Konstan MW, Moss R, Retsch-Bogart G, Wagener J, Waltz D, et al. Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 167: 841-9. PMID 12480612 DOI: 10.1164/Rccm.200208-855Oc |
0.356 |
|
| 2002 |
Sagel SD, Sontag MK, Wagener JS, Kapsner RK, Osberg I, Accurso FJ. Induced sputum inflammatory measures correlate with lung function in children with cystic fibrosis. The Journal of Pediatrics. 141: 811-7. PMID 12461498 DOI: 10.1067/Mpd.2002.129847 |
0.459 |
|
| 2002 |
Davies PS, Erskine JM, Hambidge KM, Accurso FJ. Longitudinal investigation of energy expenditure in infants with cystic fibrosis. European Journal of Clinical Nutrition. 56: 940-6. PMID 12373612 DOI: 10.1038/Sj.Ejcn.1601441 |
0.414 |
|
| 2002 |
Sagel SD, Accurso FJ. Monitoring inflammation in CF. Cytokines. Clinical Reviews in Allergy & Immunology. 23: 41-57. PMID 12162105 DOI: 10.1385/Criai:23:1:041 |
0.456 |
|
| 2002 |
Kerby GS, Cottin V, Accurso FJ, Hoffmann F, Chan ED, Fadok VA, Riches DW. Impairment of macrophage survival by NaCl: implications for early pulmonary inflammation in cystic fibrosis. American Journal of Physiology. Lung Cellular and Molecular Physiology. 283: L188-97. PMID 12060576 DOI: 10.1152/Ajplung.00263.2001 |
0.323 |
|
| 2002 |
Sagel SD, Dowell EB, Accurso FJ. Bacterial colonization and infection in the CF lung. Methods in Molecular Medicine. 70: 433-46. PMID 11917541 DOI: 10.1385/1-59259-187-6:433 |
0.4 |
|
| 2002 |
Vandivier RW, Fadok VA, Ogden CA, Hoffmann PR, Brain JD, Accurso FJ, Fisher JH, Greene KE, Henson PM. Impaired clearance of apoptotic cells from cystic fibrosis airways. Chest. 121: 89S. PMID 11893715 DOI: 10.1378/Chest.121.3_Suppl.89S |
0.399 |
|
| 2002 |
Chan ED, Choi HS, Cool C, Accurso FJ, Fantuzzi G. Interleukin-18 expression in cystic fibrosis lungs. Chest. 121: 84S-85S. PMID 11893709 DOI: 10.1378/Chest.121.3_Suppl.84S |
0.405 |
|
| 2002 |
Vandivier RW, Fadok VA, Hoffmann PR, Bratton DL, Penvari C, Brown KK, Brain JD, Accurso FJ, Henson PM. Elastase-mediated phosphatidylserine receptor cleavage impairs apoptotic cell clearance in cystic fibrosis and bronchiectasis. The Journal of Clinical Investigation. 109: 661-70. PMID 11877474 DOI: 10.1172/Jci13572 |
0.349 |
|
| 2001 |
Sagel SD, Kapsner R, Osberg I, Sontag MK, Accurso FJ. Airway inflammation in children with cystic fibrosis and healthy children assessed by sputum induction. American Journal of Respiratory and Critical Care Medicine. 164: 1425-31. PMID 11704590 DOI: 10.1164/Ajrccm.164.8.2104075 |
0.448 |
|
| 2001 |
Oermann CM, Sockrider MM, Giles D, Sontag MK, Accurso FJ, Castile RG. Comparison of high-frequency chest wall oscillation and oscillating positive expiratory pressure in the home management of cystic fibrosis: a pilot study. Pediatric Pulmonology. 32: 372-7. PMID 11596162 DOI: 10.1002/Ppul.1146 |
0.402 |
|
| 2001 |
Wojtczak HA, Kerby GS, Wagener JS, Copenhaver SC, Gotlin RW, Riches DW, Accurso FJ. Beclomethasone diproprionate reduced airway inflammation without adrenal suppression in young children with cystic fibrosis: a pilot study. Pediatric Pulmonology. 32: 293-302. PMID 11568990 DOI: 10.1002/Ppul.1122 |
0.416 |
|
| 2001 |
Noone PG, Hamblett N, Accurso F, Aitken ML, Boyle M, Dovey M, Gibson R, Johnson C, Kellerman D, Konstan MW, Milgram L, Mundahl J, Retsch-Bogort G, Rodman D, Williams-Warren J, et al. Safety of aerosolized INS 365 in patients with mild to moderate cystic fibrosis: results of a phase I multi-center study. Pediatric Pulmonology. 32: 122-8. PMID 11477729 DOI: 10.1002/Ppul.1098 |
0.349 |
|
| 2001 |
Bals R, Weiner DJ, Meegalla RL, Accurso F, Wilson JM. Salt-independent abnormality of antimicrobial activity in cystic fibrosis airway surface fluid. American Journal of Respiratory Cell and Molecular Biology. 25: 21-5. PMID 11472971 DOI: 10.1165/Ajrcmb.25.1.4436 |
0.441 |
|
| 2000 |
Krebs NF, Westcott JE, Arnold TD, Kluger BM, Accurso FJ, Miller LV, Hambidge KM. Abnormalities in zinc homeostasis in young infants with cystic fibrosis. Pediatric Research. 48: 256-61. PMID 10926304 DOI: 10.1203/00006450-200008000-00022 |
0.349 |
|
| 1999 |
Feranchak AP, Sontag MK, Wagener JS, Hammond KB, Accurso FJ, Sokol RJ. Prospective, long-term study of fat-soluble vitamin status in children with cystic fibrosis identified by newborn screen. The Journal of Pediatrics. 135: 601-10. PMID 10547249 DOI: 10.1016/S0022-3476(99)70059-4 |
0.38 |
|
| 1999 |
Rosenfeld M, Emerson J, Accurso F, Armstrong D, Castile R, Grimwood K, Hiatt P, McCoy K, McNamara S, Ramsey B, Wagener J. Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis. Pediatric Pulmonology. 28: 321-8. PMID 10536062 DOI: 10.1002/(Sici)1099-0496(199911)28:5<321::Aid-Ppul3>3.0.Co;2-V |
0.359 |
|
| 1999 |
Dobyns EL, Griebel J, Kinsella JP, Abman SH, Accurso FJ. Infant lung function after inhaled nitric oxide therapy for persistent pulmonary hypertension of the newborn. Pediatric Pulmonology. 28: 24-30. PMID 10406047 DOI: 10.1002/(Sici)1099-0496(199907)28:1<24::Aid-Ppul5>3.0.Co;2-M |
0.412 |
|
| 1998 |
Krebs NF, Sontag M, Accurso FJ, Hambidge KM. Low plasma zinc concentrations in young infants with cystic fibrosis. The Journal of Pediatrics. 133: 761-4. PMID 9842040 DOI: 10.1016/S0022-3476(98)70147-7 |
0.392 |
|
| 1997 |
Eid NS, Accurso FJ, Stenzler A. Early asymptomatic pulmonary changes in infants with cystic fibrosis. Pediatric Pulmonology. Supplement. 16: 276-7. PMID 9443311 |
0.342 |
|
| 1997 |
Wagener JS, Kahn TZ, Copenhaver SC, Accurso FJ. Early inflammation and the development of pulmonary disease in cystic fibrosis. Pediatric Pulmonology. Supplement. 16: 267-8. PMID 9443306 DOI: 10.1002/Ppul.19502308138 |
0.456 |
|
| 1997 |
Accurso FJ. Early pulmonary disease in cystic fibrosis. Current Opinion in Pulmonary Medicine. 3: 400-3. PMID 9391757 DOI: 10.1097/00063198-199711000-00002 |
0.456 |
|
| 1996 |
Kirchner KK, Wagener JS, Khan TZ, Copenhaver SC, Accurso FJ. Increased DNA levels in bronchoalveolar lavage fluid obtained from infants with cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 154: 1426-9. PMID 8912759 DOI: 10.1164/Ajrccm.154.5.8912759 |
0.436 |
|
| 1996 |
Dobyns EL, Griebel J, Fashaw L, Moreland SG, Kinsella JP, Abman SH, Accurso FJ. FOLLOW-UP PULMONARY FUNCTION IN INFANTS AFTER INHALED NITRIC OXIDE TREATMENT OF PERSISTENT PULMONARY HYPERTENSION. 2294 Pediatric Research. 39: 385-385. DOI: 10.1203/00006450-199604001-02319 |
0.389 |
|
| 1995 |
Bronstein MN, Davies PS, Hambidge KM, Accurso FJ. Normal energy expenditure in the infant with presymptomatic cystic fibrosis. The Journal of Pediatrics. 126: 28-33. PMID 7815219 DOI: 10.1016/S0022-3476(95)70495-7 |
0.376 |
|
| 1995 |
Khan TZ, Wagener JS, Bost T, Martinez J, Accurso FJ, Riches DW. Early pulmonary inflammation in infants with cystic fibrosis. American Journal of Respiratory and Critical Care Medicine. 151: 1075-82. PMID 7697234 DOI: 10.1164/Ajrccm.151.4.7697234 |
0.462 |
|
| 1995 |
Giles DR, Wagener JS, Accurso FJ, Butler-Simon N. Short-term effects of postural drainage with clapping vs autogenic drainage on oxygen saturation and sputum recovery in patients with cystic fibrosis. Chest. 108: 952-4. PMID 7555167 DOI: 10.1378/Chest.108.4.952 |
0.325 |
|
| 1993 |
Mohon RT, Wagener JS, Abman SH, Seltzer WK, Accurso FJ. Relationship of genotype to early pulmonary function in infants with cystic fibrosis identified through neonatal screening. The Journal of Pediatrics. 122: 550-5. PMID 8463899 DOI: 10.1016/S0022-3476(05)83534-6 |
0.423 |
|
| 1993 |
Rusakow LS, Abman SH, Sokol RJ, Seltzer W, Hammond KB, Accurso FJ. Immunoreactive trypsinogen levels in infants with cystic fibrosis complicated by meconium ileus Screening. 2: 13-17. DOI: 10.1016/0925-6164(93)90013-9 |
0.399 |
|
| 1992 |
Dove AM, Szefler SJ, Hill MR, Jusko WJ, Larsen GL, Accurso FJ. Altered prednisolone pharmacokinetics in patients with cystic fibrosis. The Journal of Pediatrics. 120: 789-94. PMID 1578318 DOI: 10.1016/S0022-3476(05)80250-1 |
0.38 |
|
| 1992 |
Bronstein MN, Sokol RJ, Abman SH, Chatfield BA, Hammond KB, Hambidge KM, Stall CD, Accurso FJ. Pancreatic insufficiency, growth, and nutrition in infants identified by newborn screening as having cystic fibrosis. The Journal of Pediatrics. 120: 533-40. PMID 1552390 DOI: 10.1016/S0022-3476(05)82478-3 |
0.363 |
|
| 1991 |
Accurso FJ, Abman SH, Wilkening RB, Worthen GS, Henson P. Fetal pulmonary vasodilation after exogenous platelet-activating factor. Journal of Applied Physiology (Bethesda, Md. : 1985). 70: 778-87. PMID 2022570 DOI: 10.1152/Jappl.1991.70.2.778 |
0.308 |
|
| 1991 |
Seltzer WK, Accurso F, Fall MZ, VanRiper AJ, Descartes M, Huang Y, McCabe ERB. Screening for cystic fibrosis: Feasibility of molecular genetic analysis of dried blood specimens Biochemical Medicine and Metabolic Biology. 46: 105-109. PMID 1931151 DOI: 10.1016/0885-4505(91)90055-P |
0.372 |
|
| 1991 |
Abman SH, Ogle JW, Harbeck RJ, Butler-Simon N, Hammond KB, Accurso FJ. Early bacteriologic, immunologic, and clinical courses of young infants with cystic fibrosis identified by neonatal screening. The Journal of Pediatrics. 119: 211-7. PMID 1907318 DOI: 10.1016/S0022-3476(05)80729-2 |
0.425 |
|
| 1991 |
Hammond KB, Abman SH, Sokol RJ, Accurso FJ. Efficacy of statewide neonatal screening for cystic fibrosis by assay of trypsinogen concentrations. The New England Journal of Medicine. 325: 769-74. PMID 1870650 DOI: 10.1056/Nejm199109123251104 |
0.405 |
|
| 1991 |
Abman SH, Accurso FJ. Sustained fetal pulmonary vasodilation with prolonged atrial natriuretic factor and GMP infusions. The American Journal of Physiology. 260: H183-92. PMID 1847014 DOI: 10.1152/Ajpheart.1991.260.1.H183 |
0.302 |
|
| 1991 |
Sokol RJ, Reardon MC, Accurso FJ, Stall C, Narkewicz MR, Abman SH, Hammond KB. Fat-soluble vitamins in infants identified by cystic fibrosis newborn screening. Pediatric Pulmonology. Supplement. 7: 52-5. PMID 1782131 DOI: 10.1002/Ppul.1950110711 |
0.326 |
|
| 1991 |
Accurso FJ, Sokol RJ, Hammond KB, Abman SH. Early respiratory course in infants with cystic fibrosis: relevance to newborn screening. Pediatric Pulmonology. Supplement. 7: 42-5. PMID 1782128 |
0.356 |
|
| 1991 |
Helton JL, Harmon RJ, Robinson N, Accurso FJ. Parental attitudes toward newborn screening for cystic fibrosis. Pediatric Pulmonology. Supplement. 7: 23-8. PMID 1782125 DOI: 10.1002/Ppul.1950110706 |
0.353 |
|
| 1990 |
Abman SH, Accurso FJ, Sokol RJ. Hypoalbuminemia in young infants with cystic fibrosis. The Journal of Pediatrics. 116: 840-1. PMID 2329440 DOI: 10.1016/S0022-3476(05)82695-2 |
0.405 |
|
| 1989 |
Sokol RJ, Reardon MC, Accurso FJ, Stall C, Narkewicz M, Abman SH, Hammond KB. Fat-soluble-vitamin status during the first year of life in infants with cystic fibrosis identified by screening of newborns. The American Journal of Clinical Nutrition. 50: 1064-71. PMID 2816791 DOI: 10.1093/Ajcn/50.5.1064 |
0.324 |
|
| 1989 |
Abman SH, Accurso FJ. Acute effects of partial compression of ductus arteriosus on fetal pulmonary circulation. The American Journal of Physiology. 257: H626-34. PMID 2764143 DOI: 10.1152/Ajpheart.1989.257.2.H626 |
0.326 |
|
| 1989 |
Abman SH, Shanley PF, Accurso FJ. Failure of postnatal adaptation of the pulmonary circulation after chronic intrauterine pulmonary hypertension in fetal lambs. The Journal of Clinical Investigation. 83: 1849-58. PMID 2723062 DOI: 10.1172/Jci114091 |
0.35 |
|
| 1989 |
Sokol RJ, Butler-Simon N, Heubi JE, Iannaccone ST, McCLUNG HJ, Accurso F, Hammond K, Heyman M, Sinatra F, Riely C, Perrault J, Levy J, Silverman A. Vitamin E deficiency neuropathy in children with fat malabsorption. Studies in cystic fibrosis and chronic cholestasis. Annals of the New York Academy of Sciences. 570: 156-169. PMID 2629595 DOI: 10.1111/J.1749-6632.1989.Tb14916.X |
0.325 |
|
| 1988 |
Abman SH, Accurso FJ. Acute and chronic fetal pulmonary hypertension alter pulmonary vasoreactivity. Chest. 93: 117S-119S. PMID 3342690 DOI: 10.1378/Chest.93.3_Supplement.117S-A |
0.361 |
|
| 1988 |
Accurso FJ, Wilkening RB. Temporal response of the fetal pulmonary circulation to pharmacologic vasodilators. Proceedings of the Society For Experimental Biology and Medicine. Society For Experimental Biology and Medicine (New York, N.Y.). 187: 89-98. PMID 3340622 DOI: 10.3181/00379727-187-42642 |
0.33 |
|
| 1988 |
Abman SH, Ogle JW, Butler-Simon N, Rumack CM, Accurso FJ. Role of respiratory syncytial virus in early hospitalizations for respiratory distress of young infants with cystic fibrosis. The Journal of Pediatrics. 113: 826-30. PMID 3183835 DOI: 10.1016/S0022-3476(88)80008-8 |
0.4 |
|
| 1987 |
Abman SH, Accurso FJ, Wilkening RB, Meschia G. Persistent fetal pulmonary hypoperfusion after acute hypoxia. The American Journal of Physiology. 253: H941-8. PMID 2889374 DOI: 10.1152/Ajpheart.1987.253.4.H941 |
0.341 |
|
| 1986 |
Abman SH, Wilkening RB, Ward RM, Accurso FJ. Adaptation of fetal pulmonary blood flow to local infusion of tolazoline Pediatric Research. 20: 1131-1135. PMID 3797106 DOI: 10.1203/00006450-198611000-00013 |
0.362 |
|
| 1986 |
Abman SH, Accurso FJ, Michael Bowman C. Persistent morbidity and mortality of protein calorie malnutrition in young infants with CF Journal of Pediatric Gastroenterology and Nutrition. 5: 393-396. PMID 3088250 DOI: 10.1097/00005176-198605000-00010 |
0.444 |
|
| 1985 |
Abman SH, Reardon MC, Accurso FJ, Hammond KB, Sokol RJ. Hypoalbuminemia at diagnosis as a marker for severe respiratory course in infants with cystic fibrosis identified by newborn screening The Journal of Pediatrics. 107: 933-935. PMID 3851839 DOI: 10.1016/S0022-3476(85)80194-3 |
0.366 |
|
| 1984 |
Abman SH, Accurso FJ, Bowman CM. Unsuspected cardiopulmonary abnormalities complicating bronchopulmonary dysplasia Archives of Disease in Childhood. 59: 966-970. PMID 6238574 DOI: 10.1136/Adc.59.10.966 |
0.37 |
|
| 1984 |
Reardon MC, Hammond K, Accurso FJ, Mccabe ERB, Cotton EK, Bowman CM. Nutritional And Pulmonary Abnormalities At The Time Of Diagnosis Of Cystic Fibrosis In Infants Identified By Neonatal Screening Pediatric Research. 18: 402-402. DOI: 10.1203/00006450-198404001-01853 |
0.447 |
|
| 1984 |
Accurso FJ, Truog R, Wilkening RB, Meschia G. Adaptation Of Fetal Pulmonary Blood Flow To Pharmacologic Vasodilators Pediatric Research. 18: 385-385. DOI: 10.1203/00006450-198404001-01752 |
0.355 |
|
| 1981 |
Ratner IM, Hernandez JA, Accurso FJ, Cotton EK. 1400 Low Peak Inspiratory Pressures (Pip) For Ventilation Of Infants With Hyaline Membrane Disease (Hmd) Pediatric Research. 15: 676-676. DOI: 10.1203/00006450-198104001-01429 |
0.315 |
|
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