| Year |
Citation |
Score |
| 2023 |
Rice JL, Austin ED, Mathai SC, Sahay S. Genetic testing in Pulmonary Arterial Hypertension evaluation: A patient and clinician survey. Chest. PMID 38008306 DOI: 10.1016/j.chest.2023.11.026 |
0.456 |
|
| 2023 |
Sullivan RT, Raj JU, Austin ED. Recent Advances in Pediatric Pulmonary Hypertension: Implications for Diagnosis and Treatment. Clinical Therapeutics. PMID 37517916 DOI: 10.1016/j.clinthera.2023.07.001 |
0.359 |
|
| 2023 |
Avitabile CM, Yung D, Handler S, Hopper RK, Fineman J, Freire G, Varghese N, Mullen MP, Krishnan US, Austin E, Silveira L, Ivy DD. Measurement of Physical Activity by Actigraphy in Infants and Young Children with Pulmonary Arterial Hypertension. The Journal of Pediatrics. 262: 113639. PMID 37517653 DOI: 10.1016/j.jpeds.2023.113639 |
0.383 |
|
| 2023 |
Torres G, Yang J, Griffiths M, Brandal S, Damico R, Vaidya D, Simpson CE, Pauciulo MW, Nichols WC, Ivy DD, Austin ED, Hassoun PM, Everett AD. Insulin-like growth factor binding Protein-4: A novel indicator of pulmonary arterial hypertension severity and survival. Pulmonary Circulation. 13: e12235. PMID 37152104 DOI: 10.1002/pul2.12235 |
0.337 |
|
| 2023 |
Meegan JE, Kerchberger VE, Fortune NL, McNeil JB, Bastarache JA, Austin ED, Ware LB, Hemnes AR, Brittain EL. Transpulmonary generation of cell-free hemoglobin contributes to vascular dysfunction in pulmonary arterial hypertension via dysregulated clearance mechanisms. Pulmonary Circulation. 13: e12185. PMID 36743426 DOI: 10.1002/pul2.12185 |
0.479 |
|
| 2022 |
Hopper RK, Abman SH, Elia EG, Avitabile CM, Yung D, Mullen MP, Austin ED, Bates A, Handler SS, Feinstein JA, Ivy DD, Kinsella JP, Mandl KD, Raj JU, Sleeper LA. Pulmonary Hypertension in Children with Down Syndrome: Results from the Pediatric Pulmonary Hypertension Network Registry. The Journal of Pediatrics. PMID 36027975 DOI: 10.1016/j.jpeds.2022.08.027 |
0.435 |
|
| 2022 |
Farrell R, Colglazier E, Parker C, Stevens L, Austin ED, Fineman JR. Caveolin-1 associated with severe (pediatric-onset) presentation of pulmonary arterial hypertension. Pulmonary Circulation. 12: e12100. PMID 35864912 DOI: 10.1002/pul2.12100 |
0.449 |
|
| 2022 |
Simpson CE, Griffiths M, Yang J, Nies MK, Vaidya D, Brandal S, Martin LJ, Pauciulo MW, Lutz KA, Coleman AW, Austin ED, Ivy DD, Nichols WC, Everett AD, Hassoun PM, et al. genotypic associations with endostatin levels and clinical features in pulmonary arterial hypertension: a quantitative trait association study. Erj Open Research. 8. PMID 35769420 DOI: 10.1183/23120541.00725-2021 |
0.419 |
|
| 2022 |
Nies MK, Yang J, Griffiths M, Damico R, Zhu J, Vaydia D, Fu Z, Brandal S, Austin ED, Ivy DD, Hassoun PM, Van Eyk JE, Everett AD. Proteomics discovery of pulmonary hypertension biomarkers: Insulin-like growth factor binding proteins are associated with disease severity. Pulmonary Circulation. 12: e12039. PMID 35514776 DOI: 10.1002/pul2.12039 |
0.408 |
|
| 2022 |
Yang J, Ambade AS, Nies M, Griffiths M, Damico R, Vaidya D, Brandal S, Pauciulo MW, Lutz KA, Coleman AW, Nichols WC, Austin ED, Ivy D, Hassoun PM, Everett AD. Hepatoma-derived growth factor is associated with pulmonary vascular remodeling and PAH disease severity and survival. Pulmonary Circulation. 12: e12007. PMID 35506100 DOI: 10.1002/pul2.12007 |
0.438 |
|
| 2022 |
Steffes LC, Austin ED. Upfront Combination Therapy: Growing the Case to Get Ahead of Pediatric Pulmonary Arterial Hypertension. Annals of the American Thoracic Society. 19: 163-165. PMID 35103566 DOI: 10.1513/AnnalsATS.202108-975ED |
0.442 |
|
| 2022 |
Rosenzweig EB, Bates A, Mullen MP, Abman SH, Austin ED, Everett A, Fineman J, Feinstein J, Hopper RK, Kinsella JP, Krishnan US, Lu M, Mandl KD, Raj JU, Varghese N, et al. Cardiac Catheterization and Hemodynamics in a Multicenter Cohort of Children with Pulmonary Hypertension. Annals of the American Thoracic Society. PMID 35049414 DOI: 10.1513/AnnalsATS.202108-998OC |
0.363 |
|
| 2021 |
Nickel NP, Galura GM, Zuckerman MJ, Hakim MN, Alkhateeb H, Mukherjee D, Austin ED, Heresi GA. Liver abnormalities in pulmonary arterial hypertension. Pulmonary Circulation. 11: 20458940211054304. PMID 34707859 DOI: 10.1177/20458940211054304 |
0.356 |
|
| 2021 |
Griffiths M, Yang J, Vaidya D, Nies M, Brandal S, Ivy DD, Hickey F, Wolter-Warmerdam K, Austin ED, Mullen M, Pauciulo MW, Lutz KA, Rosenzweig EB, Hirsch R, Yung D, et al. Biomarkers of Pulmonary Hypertension Are Altered in Children With Down Syndrome and Pulmonary Hypertension. The Journal of Pediatrics. PMID 34687693 DOI: 10.1016/j.jpeds.2021.10.017 |
0.388 |
|
| 2021 |
Simpson CE, Griffiths M, Yang J, Nies MK, Vaidya RD, Brandal S, Martin LJ, Pauciulo MW, Lutz KA, Coleman AW, Austin ED, Ivy DD, Nichols WC, Everett AD, Hassoun PM, et al. The angiostatic peptide endostatin enhances mortality risk prediction in pulmonary arterial hypertension. Erj Open Research. 7. PMID 34651041 DOI: 10.1183/23120541.00378-2021 |
0.338 |
|
| 2021 |
Daly CM, Griffiths M, Simpson CE, Yang J, Damico RL, Vaidya RD, Williams M, Brandal S, Jone PN, Polsen C, Ivy DD, Austin ED, Nichols WC, Pauciulo MW, Lutz K, et al. Angiostatic Peptide, Endostatin, Predicts Severity in Pediatric Congenital Heart Disease-Associated Pulmonary Hypertension. Journal of the American Heart Association. e021409. PMID 34622662 DOI: 10.1161/JAHA.120.021409 |
0.412 |
|
| 2021 |
Malloy KW, Austin ED. Pulmonary Hypertension in the child with Bronchopulmonary Dysplasia. Pediatric Pulmonology. PMID 34324276 DOI: 10.1002/ppul.25602 |
0.463 |
|
| 2021 |
Abman SH, Mullen MP, Sleeper LA, Austin ED, Rosenzweig EB, Kinsella JP, Ivy D, Hopper RK, Usha Raj J, Fineman J, Keller RL, Bates A, Krishnan US, Avitabile CM, Davidson A, et al. Characterisation of Pediatric Pulmonary Hypertensive Vascular Disease from the PPHNet Registry. The European Respiratory Journal. PMID 34140292 DOI: 10.1183/13993003.03337-2020 |
0.349 |
|
| 2021 |
West JD, Austin ED, Rizzi EM, Yan L, Tanjore H, Crabtree AL, Moore CS, Muthian G, Carrier EJ, Jacobson DA, Hamid R, Kendall PL, Majka S, Rathinasabapathy A. KCNK3 Mutation Causes Altered Immune Function in Pulmonary Arterial Hypertension Patients and Mouse Models. International Journal of Molecular Sciences. 22. PMID 34065088 DOI: 10.3390/ijms22095014 |
0.344 |
|
| 2021 |
Gairhe S, Awad KS, Dougherty EJ, Ferreyra GA, Wang S, Yu ZX, Takeda K, Demirkale CY, Torabi-Parizi P, Austin ED, Elinoff JM, Danner RL. Type I interferon activation and endothelial dysfunction in caveolin-1 insufficiency-associated pulmonary arterial hypertension. Proceedings of the National Academy of Sciences of the United States of America. 118. PMID 33836561 DOI: 10.1073/pnas.2010206118 |
0.384 |
|
| 2021 |
Griffiths M, Yang J, Simpson CE, Vaidya D, Nies M, Brandal S, Damico R, Ivy D, Austin ED, Pauciulo MW, Lutz KA, Rosenzweig EB, Hirsch R, Yung D, Nichols WC, et al. ST2 is a biomarker of pediatric pulmonary arterial hypertension severity and clinical worsening. Chest. PMID 33609516 DOI: 10.1016/j.chest.2021.01.085 |
0.528 |
|
| 2021 |
Austin ED. Sex Hormones across the Menstrual Cycle in Pulmonary Arterial Hypertension: Adding a New Layer of Complexity. Annals of the American Thoracic Society. 18: 209-211. PMID 33522875 DOI: 10.1513/AnnalsATS.202011-1379ED |
0.36 |
|
| 2020 |
Yang J, Griffiths M, Nies MK, Brandal S, Damico R, Vaidya D, Tao X, Simpson CE, Kolb TM, Mathai SC, Pauciulo MW, Nichols WC, Ivy DD, Austin ED, Hassoun PM, et al. Insulin-like growth factor binding protein-2: a new circulating indicator of pulmonary arterial hypertension severity and survival. Bmc Medicine. 18: 268. PMID 33019943 DOI: 10.1186/s12916-020-01734-3 |
0.391 |
|
| 2020 |
Rathinasabapathy A, Copeland C, Crabtree A, Carrier EJ, Moore C, Shay S, Gladson S, Austin ED, Kenworthy AK, Loyd JE, Hemnes AR, West JD. Expression of a Human Caveolin-1 Mutation in Mice Drives Inflammatory and Metabolic Defect-Associated Pulmonary Arterial Hypertension. Frontiers in Medicine. 7: 540. PMID 33015095 DOI: 10.3389/Fmed.2020.00540 |
0.424 |
|
| 2020 |
Griffiths M, Yang J, Nies M, Vaidya D, Brandal S, Williams M, Matsui EC, Grant T, Damico R, Ivy D, Austin ED, Nichols WC, Pauciulo MW, Lutz K, Rosenzweig EB, et al. Pediatric pulmonary hypertension: insulin-like growth factor-binding protein 2 is a novel marker associated with disease severity and survival. Pediatric Research. PMID 32927467 DOI: 10.1038/S41390-020-01113-X |
0.352 |
|
| 2020 |
Badlam JB, Badesch DB, Austin ED, Benza RL, Chung WK, Farber HW, Feldkircher K, Frost AE, Poms AD, Lutz KA, Pauciulo MW, Yu C, Nichols WC, Elliott CG, Simms R, et al. United States Pulmonary Hypertension Scientific Registry (USPHSR): Baseline Characteristics. Chest. PMID 32858008 DOI: 10.1016/J.Chest.2020.07.088 |
0.573 |
|
| 2020 |
Chen JY, Griffiths M, Yang J, Nies MK, Damico RL, Simpson CE, Vaidya RD, Brandal S, Ivy DD, Austin ED, Nichols WC, Pauciulo MW, Lutz K, Rosenzweig EB, Hirsch R, et al. Elevated Interleukin-6 Levels Predict Clinical Worsening in Pediatric Pulmonary Arterial Hypertension. The Journal of Pediatrics. 223: 164-169.e1. PMID 32711743 DOI: 10.1016/J.Jpeds.2020.04.041 |
0.542 |
|
| 2020 |
Amin EK, Austin ED, Parker C, Colglazier E, Nawaytou H, Leary P, Hemnes AR, Teitel D, Fineman JR. BMPR2 Mutation Carriers: Novel Documentation of Onset and Rapid Advancement of Pulmonary Arterial Hypertension Without Symptoms: Cautionary Tales? American Journal of Respiratory and Critical Care Medicine. PMID 32692583 DOI: 10.1164/Rccm.202005-1611Le |
0.537 |
|
| 2020 |
Hansmann G, Sallmon H, Roehr CC, Kourembanas S, Austin ED, Koestenberger M. Pulmonary hypertension in bronchopulmonary dysplasia. Pediatric Research. PMID 32521539 DOI: 10.1038/S41390-020-0993-4 |
0.374 |
|
| 2020 |
Austin ED, Elliott CG. TBX4 syndrome: a systemic disease highlighted by pulmonary arterial hypertension in its most severe form. The European Respiratory Journal. 55. PMID 32409426 DOI: 10.1183/13993003.00585-2020 |
0.595 |
|
| 2020 |
Al-Naamani N, Krowka MJ, Forde KA, Krok KL, Feng R, Heresi GA, Dweik RA, Bartolome S, Bull TM, Roberts KE, Austin ED, Hemnes AR, Patel MJ, Oh JK, Lin G, et al. Estrogen Signaling and Portopulmonary Hypertension: The Pulmonary Vascular Complications of Liver Disease Study (PVCLD2). Hepatology (Baltimore, Md.). PMID 32407592 DOI: 10.1002/Hep.31314 |
0.416 |
|
| 2020 |
Dunmore BJ, Yang X, Crosby A, Moore S, Long L, Huang C, Southwood M, Austin ED, Rana A, Upton PD, Morrell NW. 4PBA Restores Signalling of a Cysteine-substituted Mutant BMPR2 Receptor Found in Patients with PAH. American Journal of Respiratory Cell and Molecular Biology. PMID 32255665 DOI: 10.1165/Rcmb.2019-0321Oc |
0.448 |
|
| 2020 |
Denver N, Homer NZM, Andrew R, Harvey KY, Morrell N, Austin ED, MacLean MR. Estrogen metabolites in a small cohort of patients with idiopathic pulmonary arterial hypertension. Pulmonary Circulation. 10: 2045894020908783. PMID 32206305 DOI: 10.1177/2045894020908783 |
0.539 |
|
| 2020 |
Badlam JB, Badesch D, Brittain E, Cordell S, Ding T, Fox K, Hemnes A, Loyd J, Pugh M, Robbins I, Yu C, Austin ED. Sex hormone exposure and reproductive factors in pulmonary arterial hypertension: a case-control study. Pulmonary Circulation. 10: 2045894020908786. PMID 32166018 DOI: 10.1177/2045894020908786 |
0.402 |
|
| 2020 |
Halliday SJ, Matthews DT, Talati MH, Austin ED, Su YR, Absi TS, Fortune NL, Gailani D, Matafonov A, West JD, Hemnes AR. A multifaceted investigation into molecular associations of chronic thromboembolic pulmonary hypertension pathogenesis. Jrsm Cardiovascular Disease. 9: 2048004020906994. PMID 32110389 DOI: 10.1177/2048004020906994 |
0.458 |
|
| 2020 |
Austin ED, Hamid R. Deconstructing the Melting Pot in PAH. American Journal of Respiratory and Critical Care Medicine. PMID 32053755 DOI: 10.1164/Rccm.202001-0156Ed |
0.322 |
|
| 2020 |
Simpson CE, Chen JY, Damico RL, Hassoun PM, Martin LJ, Yang J, Nies M, Griffiths M, Vaidya RD, Brandal S, Pauciulo MW, Lutz KA, Coleman AW, Austin ED, Ivy DD, et al. Cellular sources of IL-6 and associations with clinical phenotypes and outcomes in PAH. The European Respiratory Journal. PMID 32029443 DOI: 10.1183/13993003.01761-2019 |
0.338 |
|
| 2020 |
Simpson CE, Damico RL, Hassoun PM, Martin LJ, Yang J, Nies MK, Vaidya RD, Brandal S, Pauciulo MW, Austin ED, Ivy DD, Nichols WC, Everett AD. Noninvasive prognostic biomarkers for left heart failure as predictors of survival in pulmonary arterial hypertension. Chest. PMID 31987881 DOI: 10.1016/J.Chest.2019.12.037 |
0.502 |
|
| 2020 |
Welch CL, Austin ED, Chung WK. Genes that drive the pathobiology of pediatric pulmonary arterial hypertension. Pediatric Pulmonology. PMID 31917901 DOI: 10.1002/Ppul.24637 |
0.432 |
|
| 2019 |
Nickel NP, Yuan K, Dorfmuller P, Provencher S, Lai YC, Bonnet S, Austin ED, Koch CD, Morris A, Perros F, Montani D, Zamanian RT, de Jesus Perez VA. BEYOND THE LUNGS: SYSTEMIC MANIFESTATIONS OF PULMONARY ARTERIAL HYPERTENSION. American Journal of Respiratory and Critical Care Medicine. PMID 31513751 DOI: 10.1164/Rccm.201903-0656Ci |
0.546 |
|
| 2019 |
Hansmann G, Koestenberger M, Alastalo TP, Apitz C, Austin ED, Bonnet D, Budts W, D'Alto M, Gatzoulis MA, Hasan BS, Kozlik-Feldmann R, Kumar RK, Lammers AE, Latus H, Michel-Behnke I, et al. 2019 updated consensus statement on the diagnosis and treatment of pediatric pulmonary hypertension: The European Pediatric Pulmonary Vascular Disease Network (EPPVDN), endorsed by AEPC, ESPR and ISHLT. The Journal of Heart and Lung Transplantation : the Official Publication of the International Society For Heart Transplantation. 38: 879-901. PMID 31495407 DOI: 10.1016/J.Healun.2019.06.022 |
0.478 |
|
| 2019 |
Ivy DD, Feinstein J, Yung D, Mullen M, Kirkpatrick EC, Hirsch R, Austin E, Fineman J, Truong U, Solum D, Deng CQ, Hopper RK. EXPRESS: Oral Treprostinil in Transition or as Add-on Therapy in Pediatric Pulmonary Arterial Hypertension. Pulmonary Circulation. 2045894019856471. PMID 31215336 DOI: 10.1177/2045894019856471 |
0.535 |
|
| 2019 |
Ong MS, Abman S, Austin ED, Feinstein JA, Hopper RK, Krishnan US, Mullen MP, Natter MD, Raj JU, Rosenzweig EB, Mandl KD. Racial and Ethnic Differences in Pediatric Pulmonary Hypertension: An Analysis of the Pediatric Pulmonary Hypertension Network Registry. The Journal of Pediatrics. PMID 31176455 DOI: 10.1016/J.Jpeds.2019.04.046 |
0.516 |
|
| 2019 |
Galambos C, Mullen MP, Shieh JT, Schwerk N, Kielt MJ, Ullmann N, Boldrini R, Stucin-Gantar I, Haass C, Bansal M, Agrawal PB, Johnson J, Peca D, Surace C, Cutrera R, ... ... Austin ED, et al. Phenotype characterisation of mutation and deletion carriers with neonatal and pediatric pulmonary hypertension. The European Respiratory Journal. PMID 31151956 DOI: 10.1183/13993003.01965-2018 |
0.514 |
|
| 2019 |
Elliott CG, Austin E, Badesch D, Badlam J, Benza R, Chung WK, Farber HW, Feldkircher K, Frost AE, Poms AD, Lutz K, Pauciulo MW, Yu C, Nichols WC. EXPRESS: United States Pulmonary Hypertension Scientific Registry (USPHSR): Rationale, design, and clinical implications. Pulmonary Circulation. 2045894019851696. PMID 31099303 DOI: 10.1177/2045894019851696 |
0.564 |
|
| 2019 |
Goss KN, Austin E, Battiola TJ, Tepper RS, Lahm T. EXPRESS: Novel Early Life Risk Factors for Adult Pulmonary Hypertension. Pulmonary Circulation. 2045894019842002. PMID 30880574 DOI: 10.1177/2045894019842002 |
0.437 |
|
| 2019 |
Nickel N, Perez VAJ, Fessel JP, Cogan J, Hamid R, West JD, de Caestecker M, Yang H, Zamanian RT, Austin E. EXPRESS: Low-Grade Albuminuria in Pulmonary Arterial Hypertension. Pulmonary Circulation. 2045894018824564. PMID 30632900 DOI: 10.1177/2045894018824564 |
0.55 |
|
| 2018 |
Bryant A, Fu C, Lu Y, Brantly M, Moldawer L, Brusko T, Brittain E, West JD, Austin E, Hamid R. EXPRESS: A Checkpoint on Innate Myeloid Cells in Pulmonary Arterial Hypertension. Pulmonary Circulation. 2045894018823528. PMID 30562157 DOI: 10.1177/2045894018823528 |
0.554 |
|
| 2018 |
Rhodes CJ, Batai K, Bleda M, Haimel M, Southgate L, Germain M, Pauciulo MW, Hadinnapola C, Aman J, Girerd B, Arora A, Knight J, Hanscombe KB, Karnes JH, Kaakinen M, ... ... Austin ED, et al. Genetic determinants of risk in pulmonary arterial hypertension: international genome-wide association studies and meta-analysis. The Lancet. Respiratory Medicine. PMID 30527956 DOI: 10.1016/S2213-2600(18)30409-0 |
0.536 |
|
| 2018 |
Dannewitz Prosseda S, Tian X, Kuramoto K, Boehm M, Sudheendra D, Miyagawa K, Zhang F, Solow-Cordero D, Saldivar JC, Austin ED, Loyd JE, Wheeler L, Andruska A, Donato M, Wang L, et al. Fragile Histidine Triad (FHIT), a Novel Modifier Gene in Pulmonary Arterial Hypertension. American Journal of Respiratory and Critical Care Medicine. PMID 30107138 DOI: 10.1164/Rccm.201712-2553Oc |
0.586 |
|
| 2018 |
Zhu N, Welch CL, Wang J, Allen PM, Gonzaga-Jauregui C, Ma L, King AK, Krishnan U, Rosenzweig EB, Ivy DD, Austin ED, Hamid R, Pauciulo MW, Lutz KA, Nichols WC, et al. Rare variants in SOX17 are associated with pulmonary arterial hypertension with congenital heart disease. Genome Medicine. 10: 56. PMID 30029678 DOI: 10.1186/S13073-018-0566-X |
0.561 |
|
| 2018 |
Badlam JB, Austin ED. Beyond oestrogens: towards a broader evaluation of the hormone profile in pulmonary arterial hypertension. The European Respiratory Journal. 51. PMID 29954927 DOI: 10.1183/13993003.01058-2018 |
0.557 |
|
| 2018 |
Zhu N, Gonzaga-Jauregui C, Welch CL, Ma L, Qi H, King AK, Krishnan U, Rosenzweig EB, Ivy DD, Austin ED, Hamid R, Nichols WC, Pauciulo MW, Lutz KA, Sawle A, et al. Exome Sequencing in Children With Pulmonary Arterial Hypertension Demonstrates Differences Compared With Adults. Circulation. Genomic and Precision Medicine. 11: e001887. PMID 29631995 DOI: 10.1161/CIRCGEN.117.001887 |
0.481 |
|
| 2018 |
Kinsella JP, Steinhorn RH, Mullen MP, Hopper RK, Keller RL, Ivy DD, Austin ED, Krishnan US, Rosenzweig EB, Fineman JR, Everett AD, Hanna BD, Humpl T, Raj JU, Abman SH, et al. The Left Ventricle in Congenital Diaphragmatic Hernia: Implications for the Management of Pulmonary Hypertension. The Journal of Pediatrics. PMID 29628412 DOI: 10.1016/J.Jpeds.2018.02.040 |
0.501 |
|
| 2018 |
Brittain EL, Thenappan T, Maron BA, Chan SY, Austin ED, Spiekerkoetter E, Bogaard HJ, Guignabert C, Paulin R, Machado RF, Yu PB. Update in Pulmonary Vascular Disease 2016 and 2017. American Journal of Respiratory and Critical Care Medicine. PMID 29533671 DOI: 10.1164/Rccm.201801-0062Up |
0.491 |
|
| 2018 |
Whitaker ME, Nair V, Sinari S, Dherange P, Natarajan B, Trutter L, Brittain EL, Hemnes AR, Austin E, Patel K, Black SM, Garcia JGN, Yuan JX, Vanderpool R, Rischard F, et al. Diabetes Mellitus Associates with Increased Right Ventricular Afterload and Remodeling in Pulmonary Arterial Hypertension. The American Journal of Medicine. PMID 29421689 DOI: 10.1016/J.Amjmed.2017.12.046 |
0.456 |
|
| 2018 |
Benza R, Frost A, Elliott G, Austin E, Badesch D, Farber H, Chung W, Poms A, Feldkircher K, Yu C, Badlam J, Pauciulo M, Nichols W. INITIAL DATA FROM THE US PULMONARY HYPERTENSION REGISTRY: GENETICS AND DEMOGRAPHICS IN NEWLY DIAGNOSED PULMONARY ARTERIAL HYPERTENSION (PAH) Journal of the American College of Cardiology. 71: A1926. DOI: 10.1016/S0735-1097(18)32467-7 |
0.521 |
|
| 2018 |
Chew J, Weiner J, Saurers D, Austin E, Christensen J. DECREASED PULMONARY PULSE TRANSIT IS ASSOCIATED WITH PEDIATRIC PULMONARY ARTERIAL HYPERTENSION Journal of the American College of Cardiology. 71: A580. DOI: 10.1016/S0735-1097(18)31121-5 |
0.553 |
|
| 2018 |
Farber H, Badlam J, Frost A, Benza R, Austin E, Badesch D, Chung W, Poms A, Feldkircher K, Yu C, Pauciulo M, Nichols W, Elliott C. The United States Pulmonary Hypertension Scientific Registry (USPHSR): Objectives and Preliminary Data The Journal of Heart and Lung Transplantation. 37: S205. DOI: 10.1016/J.Healun.2018.01.500 |
0.449 |
|
| 2017 |
O'Connor MG, Suthar D, Vera K, Slaughter JC, Maitre NL, Steele S, Beller A, Fike CD, Aschner JL, Moore PE, Austin ED. Pulmonary hypertension in the premature infant population: Analysis of echocardiographic findings and biomarkers. Pediatric Pulmonology. PMID 29168320 DOI: 10.1002/Ppul.23913 |
0.42 |
|
| 2017 |
Ventetuolo CE, Hess E, Austin ED, Barón AE, Klinger JR, Lahm T, Maddox TM, Plomondon ME, Thompson L, Zamanian RT, Choudhary G, Maron BA. Sex-based differences in veterans with pulmonary hypertension: Results from the veterans affairs-clinical assessment reporting and tracking database. Plos One. 12: e0187734. PMID 29121097 DOI: 10.1371/Journal.Pone.0187734 |
0.401 |
|
| 2017 |
Chew JD, Loyd JE, Austin ED. Genetics of Pulmonary Arterial Hypertension. Seminars in Respiratory and Critical Care Medicine. 38: 585-595. PMID 29032562 DOI: 10.1055/s-0037-1606201 |
0.494 |
|
| 2017 |
Austin ED, Hamid R. Y Not? Sex Chromosomes May Modify Sexual Dimorphism in Pulmonary Hypertension. American Journal of Respiratory and Critical Care Medicine. PMID 28968140 DOI: 10.1164/Rccm.201709-1865Ed |
0.398 |
|
| 2017 |
Copeland CA, Han B, Tiwari A, Austin ED, Loyd JE, West JD, Kenworthy AK. A disease-associated frameshift mutation in caveolin-1 disrupts caveolae formation and function through introduction of a de novo ER retention signal. Molecular Biology of the Cell. PMID 28904206 DOI: 10.1091/Mbc.E17-06-0421 |
0.409 |
|
| 2017 |
Moore PE, Poston JT, Boyer D, Barsky E, Gaffin J, Boyne KB, Ross KR, Mann Dosier LB, Vece TJ, Casey AM, Welsh SK, Logan JW, Shepherd EG, Phinzy PA, Panitch HB, ... ... Austin ED, et al. ATS Core Curriculum 2017: Part II. Pediatric Pulmonary Medicine. Annals of the American Thoracic Society. 14: S165-S181. PMID 28857623 DOI: 10.1513/Annalsats.201702-143Cme |
0.43 |
|
| 2017 |
Chen X, Austin ED, Talati M, Fessel JP, Farber-Eger EH, Brittain EL, Hemnes AR, Loyd JE, West J. Oestrogen inhibition reverses pulmonary arterial hypertension and associated metabolic defects. The European Respiratory Journal. 50. PMID 28775043 DOI: 10.1183/13993003.02337-2016 |
0.453 |
|
| 2017 |
Austin ED, Feinstein JA. Accelerometry: Improving Objective Assessments of Therapeutic Impact in Pediatric Pulmonary Arterial Hypertension. American Journal of Respiratory and Critical Care Medicine. 196: 127-129. PMID 28707968 DOI: 10.1164/Rccm.201702-0409Ed |
0.532 |
|
| 2017 |
Egnatchik RA, Brittain EL, Shah AT, Fares WH, Ford HJ, Monahan K, Kang CJ, Kocurek EG, Zhu S, Luong T, Nguyen TT, Hysinger E, Austin ED, Skala MC, Young JD, et al. Dysfunctional BMPR2 signaling drives an abnormal endothelial requirement for glutamine in pulmonary arterial hypertension. Pulmonary Circulation. 7: 186-199. PMID 28680578 DOI: 10.1086/690236 |
0.526 |
|
| 2017 |
Kulik TJ, Austin ED. Pulmonary hypertension's variegated landscape: a snapshot. Pulmonary Circulation. 7: 67-81. PMID 28680566 DOI: 10.1177/2045893216686930 |
0.548 |
|
| 2017 |
Nickel NP, O'Leary JM, Brittain EL, Fessel JP, Zamanian RT, West JD, Austin ED. Kidney dysfunction in patients with pulmonary arterial hypertension. Pulmonary Circulation. 7: 38-54. PMID 28680564 DOI: 10.1086/690018 |
0.453 |
|
| 2017 |
Krishnan U, Feinstein JA, Adatia I, Austin ED, Mullen MP, Hopper RK, Hanna B, Romer L, Keller RL, Fineman J, Steinhorn R, Kinsella JP, Ivy DD, Rosenzweig EB, Raj U, et al. Evaluation and Management of Pulmonary Hypertension in Children with Bronchopulmonary Dysplasia. The Journal of Pediatrics. PMID 28645441 DOI: 10.1016/J.Jpeds.2017.05.029 |
0.449 |
|
| 2017 |
Ong MS, Mullen MP, Austin ED, Szolovits P, Natter M, Geva A, Cai T, Kong SW, Mandl KD. Learning a Comorbidity-Driven Taxonomy of Pediatric Pulmonary Hypertension. Circulation Research. PMID 28611076 DOI: 10.1161/Circresaha.117.310804 |
0.344 |
|
| 2017 |
Gaskill CF, Carrier EJ, Kropski JA, Bloodworth NC, Menon S, Foronjy RF, Taketo MM, Hong CC, Austin ED, West JD, Means AL, Loyd JE, Merryman WD, Hemnes AR, De Langhe S, et al. Disruption of lineage specification in adult pulmonary mesenchymal progenitor cells promotes microvascular dysfunction. The Journal of Clinical Investigation. PMID 28463231 DOI: 10.1172/Jci88629 |
0.423 |
|
| 2017 |
Marsboom G, Chen Z, Yuan Y, Zhang Y, Tiruppathi C, Loyd JE, Austin ED, Machado RF, Minshall RD, Rehman J, Malik AB. Aberrant Caveolin-1-Mediated Smad Signaling and Proliferation Identified by Analysis of Adenine 474 Deletion Mutation (c.474delA) in Patient Fibroblasts: A New Perspective in the Mechanism of Pulmonary Hypertension. Molecular Biology of the Cell. PMID 28298490 DOI: 10.1091/Mbc.E16-06-0380 |
0.399 |
|
| 2016 |
Gaskill C, Marriott S, Pratap S, Menon S, Hedges LK, Fessel JP, Kropski JA, Ames D, Wheeler L, Loyd JE, Hemnes AR, Roop DR, Klemm DJ, Austin ED, Majka SM. Shared gene expression patterns in mesenchymal progenitors derived from lung and epidermis in pulmonary arterial hypertension: identifying key pathways in pulmonary vascular disease. Pulmonary Circulation. 6: 483-497. PMID 28090290 DOI: 10.1086/688314 |
0.494 |
|
| 2016 |
Gu M, Shao NY, Sa S, Li D, Termglinchan V, Ameen M, Karakikes I, Sosa G, Grubert F, Lee J, Cao A, Taylor S, Ma Y, Zhao Z, Chappell J, ... ... Austin ED, et al. Patient-Specific iPSC-Derived Endothelial Cells Uncover Pathways that Protect against Pulmonary Hypertension in BMPR2 Mutation Carriers. Cell Stem Cell. PMID 28017794 DOI: 10.1016/J.Stem.2016.08.019 |
0.464 |
|
| 2016 |
Humpl T, Berger RM, Austin ED, Fasnacht Boillat MS, Bonnet D, Ivy DD, Zuk M, Beghetti M, Schulze-Neick I. Treatment initiation in paediatric pulmonary hypertension: insights from a multinational registry. Cardiology in the Young. 1-10. PMID 27995825 DOI: 10.1017/S1047951116002493 |
0.517 |
|
| 2016 |
Han B, Copeland CA, Kawano Y, Rosenzweig EB, Austin ED, Shahmirzadi L, Tang S, Raghunathan K, Chung WK, Kenworthy AK. Characterization of a caveolin-1 mutation associated with both PAH and congenital generalized lipodystrophy. Traffic (Copenhagen, Denmark). PMID 27717241 DOI: 10.1111/Tra.12452 |
0.434 |
|
| 2016 |
Austin ED, West J, Loyd JE, Hemnes AR. Molecular Medicine of Pulmonary Arterial Hypertension: From Population Genetics to Precision Medicine and Gene Editing. American Journal of Respiratory and Critical Care Medicine. PMID 27398627 DOI: 10.1164/Rccm.201605-0905Pp |
0.492 |
|
| 2016 |
Yang J, Nies MK, Fu Z, Damico R, Korley FK, Hassoun PM, Ivy DD, Austin ED, Everett AD. Hepatoma Derived Growth Factor Predicts Disease Severity and Survival in Pulmonary Artery Hypertension. American Journal of Respiratory and Critical Care Medicine. PMID 27254543 DOI: 10.1164/Rccm.201512-2498Oc |
0.564 |
|
| 2016 |
O'Connor MG, Cornfield DN, Austin ED. Pulmonary hypertension in the premature infant: a challenging comorbidity in a vulnerable population. Current Opinion in Pediatrics. PMID 27043088 DOI: 10.1097/Mop.0000000000000355 |
0.441 |
|
| 2016 |
Brittain EL, Talati M, Fessel JP, Zhu H, Penner N, Calcutt MW, West J, Funke M, Lewis GD, Gerszten RE, Hamid R, Pugh ME, Austin ED, Newman JH, Hemnes AR. Fatty Acid Metabolic Defects and Right Ventricular Lipotoxicity in Human Pulmonary Arterial Hypertension. Circulation. PMID 27006481 DOI: 10.1161/Circulationaha.115.019351 |
0.483 |
|
| 2016 |
Hemnes AR, Zhao M, West J, Newman JH, Rich S, Archer SL, Robbins IM, Blackwell TS, Cogan J, Loyd JE, Zhao Z, Gaskill C, Jetter C, Kropski JA, Majka SM, ... Austin ED, et al. Critical Genomic Networks and Vasoreactive Variants in Idiopathic Pulmonary Arterial Hypertension. American Journal of Respiratory and Critical Care Medicine. PMID 26926454 DOI: 10.1164/Rccm.201508-1678Oc |
0.555 |
|
| 2016 |
Mar PL, Nwazue V, Black BK, Biaggioni I, Diedrich A, Paranjape SY, Loyd JE, Hemnes AR, Robbins IM, Robertson D, Raj SR, Austin ED. Valsalva Maneuver in Pulmonary Arterial Hypertension: Susceptibility to Syncope and Autonomic Dysfunction. Chest. PMID 26836906 DOI: 10.1016/J.Chest.2015.11.015 |
0.486 |
|
| 2016 |
Evans JD, Girerd B, Montani D, Wang XJ, Galiè N, Austin ED, Elliott G, Asano K, Grünig E, Yan Y, Jing ZC, Manes A, Palazzini M, Wheeler LA, Nakayama I, et al. BMPR2 mutations and survival in pulmonary arterial hypertension: an individual participant data meta-analysis. The Lancet. Respiratory Medicine. PMID 26795434 DOI: 10.1016/S2213-2600(15)00544-5 |
0.55 |
|
| 2016 |
Krishnan U, Ivy D, Austin E, Fineman J, Adatia I, Berman-Rosenzweig E, Abman S. PH Roundtable: Pediatric Pulmonary Hypertension Guidelines Highlights and Challenges Advances in Pulmonary Hypertension. 15: 100-104. DOI: 10.21693/1933-088X-15.2.100 |
0.402 |
|
| 2015 |
Kinsella JP, Steinhorn RH, Krishnan US, Feinstein JA, Adatia I, Austin ED, Rosenzweig EB, Everett AD, Fineman JR, Hanna BD, Hopper RK, Humpl T, Ivy DD, Keller RL, Mullen MP, et al. Recommendations for the Use of Inhaled Nitric Oxide Therapy in Premature Newborns with Severe Pulmonary Hypertension. The Journal of Pediatrics. PMID 26703869 DOI: 10.1016/J.Jpeds.2015.11.050 |
0.457 |
|
| 2015 |
Yan L, Chen X, Talati M, Nunley BW, Gladson S, Blackwell T, Cogan J, Austin E, Wheeler F, Loyd J, West J, Hamid R. Bone Marrow-derived Cells Contribute to Pathogenesis of Pulmonary Arterial Hypertension. American Journal of Respiratory and Critical Care Medicine. PMID 26651104 DOI: 10.1164/Rccm.201502-0407Oc |
0.541 |
|
| 2015 |
Austin ED, Loyd JE. Toward Precision Medicine in Pulmonary Arterial Hypertension. American Journal of Respiratory and Critical Care Medicine. 192: 1272-4. PMID 26623685 DOI: 10.1164/Rccm.201508-1607Ed |
0.564 |
|
| 2015 |
Huang J, Wolk JH, Gewitz MH, Loyd JE, West J, Austin ED, Mathew R. Enhanced caveolin-1 expression in smooth muscle cells: Possible prelude to neointima formation. World Journal of Cardiology. 7: 671-84. PMID 26516422 DOI: 10.4330/Wjc.V7.I10.671 |
0.332 |
|
| 2015 |
Chen X, Talati M, Fessel JP, Hemnes AR, Gladson S, French J, Shay S, Trammell A, Phillips JA, Hamid R, Cogan JD, Dawson EP, Womble KE, Hedges LK, Martinez EG, ... ... Austin ED, et al. The Estrogen Metabolite 16αOHE Exacerbates BMPR2-Associated PAH Through miR-29-Mediated Modulation of Cellular Metabolism. Circulation. PMID 26487756 DOI: 10.1161/Circulationaha.115.016133 |
0.457 |
|
| 2015 |
Machado RD, Southgate L, Eichstaedt CA, Aldred MA, Austin ED, Best DH, Chung WK, Benjamin N, Elliott CG, Eyries M, Fischer C, Gräf S, Hinderhofer K, Humbert M, Keiles SB, et al. Pulmonary Arterial Hypertension: A Current Perspective on Established and Emerging Molecular Genetic Defects. Human Mutation. PMID 26387786 DOI: 10.1002/Humu.22904 |
0.512 |
|
| 2015 |
Mosley JD, Brittain EL, Loyd JE, Denny JC, Austin ED, Larkin EK. Letter by Mosley Regarding Article, "Iron Homeostasis and Pulmonary Hypertension: Iron Deficiency Leads to Pulmonary Vascular Remodeling in the Rat". Circulation Research. 117: e56-7. PMID 26316607 DOI: 10.1161/Circresaha.115.306867 |
0.443 |
|
| 2015 |
Chung WK, Austin ED, Best DH, Brown LM, Elliott CG. When to offer genetic testing for pulmonary arterial hypertension. The Canadian Journal of Cardiology. 31: 544-7. PMID 25840103 DOI: 10.1016/J.Cjca.2014.11.005 |
0.519 |
|
| 2015 |
Damico R, Kolb TM, Valera L, Wang L, Housten T, Tedford RJ, Kass DA, Rafaels N, Gao L, Barnes KC, Benza RL, Rand JL, Hamid R, Loyd JE, Robbins IM, ... ... Austin ED, et al. Serum endostatin is a genetically determined predictor of survival in pulmonary arterial hypertension. American Journal of Respiratory and Critical Care Medicine. 191: 208-18. PMID 25489667 DOI: 10.1164/Rccm.201409-1742Oc |
0.586 |
|
| 2015 |
Prewitt AR, Ghose S, Frump AL, Datta A, Austin ED, Kenworthy AK, de Caestecker MP. Heterozygous null bone morphogenetic protein receptor type 2 mutations promote SRC kinase-dependent caveolar trafficking defects and endothelial dysfunction in pulmonary arterial hypertension. The Journal of Biological Chemistry. 290: 960-71. PMID 25411245 DOI: 10.1074/Jbc.M114.591057 |
0.491 |
|
| 2015 |
Hemnes AR, Trammell AW, Archer SL, Rich S, Yu C, Nian H, Penner N, Funke M, Wheeler L, Robbins IM, Austin ED, Newman JH, West J. Peripheral blood signature of vasodilator-responsive pulmonary arterial hypertension. Circulation. 131: 401-9; discussion 40. PMID 25361553 DOI: 10.1161/Circulationaha.114.013317 |
0.528 |
|
| 2015 |
Mar PL, Nwazue V, Black BK, Biaggioni I, Diedrich A, Paranjape SY, Loyd JE, Hemnes AR, Robbins IM, Robertson D, Raj SR, Austin ED. Valsalva Maneuver in Pulmonary Arterial Hypertension: Hemodynamic Changes and Excessive Systemic Vasodilation Autonomic Neuroscience. 192: 105-106. DOI: 10.1016/J.Autneu.2015.07.165 |
0.541 |
|
| 2014 |
Best DH, Austin ED, Chung WK, Elliott CG. Genetics of pulmonary hypertension. Current Opinion in Cardiology. 29: 520-7. PMID 25159282 DOI: 10.1097/Hco.0000000000000105 |
0.514 |
|
| 2014 |
Marriott S, Baskir RS, Gaskill C, Menon S, Carrier EJ, Williams J, Talati M, Helm K, Alford CE, Kropski JA, Loyd J, Wheeler L, Johnson J, Austin E, Nozik-Grayck E, et al. ABCG2pos lung mesenchymal stem cells are a novel pericyte subpopulation that contributes to fibrotic remodeling. American Journal of Physiology. Cell Physiology. 307: C684-98. PMID 25122876 DOI: 10.1152/Ajpcell.00114.2014 |
0.338 |
|
| 2014 |
Benson L, Brittain EL, Pugh ME, Austin ED, Fox K, Wheeler L, Robbins IM, Hemnes AR. Impact of diabetes on survival and right ventricular compensation in pulmonary arterial hypertension. Pulmonary Circulation. 4: 311-8. PMID 25006450 DOI: 10.1086/675994 |
0.449 |
|
| 2014 |
Austin ED, Loyd JE. The genetics of pulmonary arterial hypertension. Circulation Research. 115: 189-202. PMID 24951767 DOI: 10.1161/Circresaha.115.303404 |
0.491 |
|
| 2014 |
Brittain EL, Janz DR, Austin ED, Bastarache JA, Wheeler LA, Ware LB, Hemnes AR. Elevation of plasma cell-free hemoglobin in pulmonary arterial hypertension. Chest. 146: 1478-85. PMID 24945582 DOI: 10.1378/Chest.14-0809 |
0.523 |
|
| 2014 |
West JD, Austin ED, Gaskill C, Marriott S, Baskir R, Bilousova G, Jean JC, Hemnes AR, Menon S, Bloodworth NC, Fessel JP, Kropski JA, Irwin D, Ware LB, Wheeler L, et al. Identification of a common Wnt-associated genetic signature across multiple cell types in pulmonary arterial hypertension. American Journal of Physiology. Cell Physiology. 307: C415-30. PMID 24871858 DOI: 10.1152/Ajpcell.00057.2014 |
0.468 |
|
| 2014 |
West J, Austin E, Fessel JP, Loyd J, Hamid R. Rescuing the BMPR2 signaling axis in pulmonary arterial hypertension. Drug Discovery Today. 19: 1241-5. PMID 24794464 DOI: 10.1016/J.Drudis.2014.04.015 |
0.556 |
|
| 2014 |
Austin ED, Kawut SM, Gladwin MT, Abman SH. Pulmonary hypertension: NHLBI Workshop on the Primary Prevention of Chronic Lung Diseases. Annals of the American Thoracic Society. 11: S178-85. PMID 24754827 DOI: 10.1513/Annalsats.201312-443Ld |
0.553 |
|
| 2014 |
Zhao M, Austin ED, Hemnes AR, Loyd JE, Zhao Z. An evidence-based knowledgebase of pulmonary arterial hypertension to identify genes and pathways relevant to pathogenesis. Molecular Biosystems. 10: 732-40. PMID 24448676 DOI: 10.1039/C3Mb70496C |
0.465 |
|
| 2014 |
Hemnes AR, Brittain EL, Trammell AW, Fessel JP, Austin ED, Penner N, Maynard KB, Gleaves L, Talati M, Absi T, Disalvo T, West J. Evidence for right ventricular lipotoxicity in heritable pulmonary arterial hypertension. American Journal of Respiratory and Critical Care Medicine. 189: 325-34. PMID 24274756 DOI: 10.1164/Rccm.201306-1086Oc |
0.541 |
|
| 2014 |
Best DH, Sumner KL, Austin ED, Chung WK, Brown LM, Borczuk AC, Rosenzweig EB, Bayrak-Toydemir P, Mao R, Cahill BC, Tazelaar HD, Leslie KO, Hemnes AR, Robbins IM, Elliott CG. EIF2AK4 mutations in pulmonary capillary hemangiomatosis. Chest. 145: 231-6. PMID 24135949 DOI: 10.1378/Chest.13-2366 |
0.49 |
|
| 2014 |
Marsboom G, Theriault K, Debroy A, Mao M, Baig S, Tiruppathi C, Bonini M, Rehman J, Austin E, Malik A. Newly identified caveolin-1 mutation associated with heritable human pulmonary arterial hypertension mediates hyperproliferation via augmented calcium signaling (1089.10) The Faseb Journal. 28. DOI: 10.1096/Fasebj.28.1_Supplement.1089.10 |
0.559 |
|
| 2014 |
Austin ED, Newman JH, Loyd JE, Phillips JA. Heritable and Idiopathic Forms of Pulmonary Arterial Hypertension Reference Module in Biomedical Research. DOI: 10.1016/B978-0-12-801238-3.05521-5 |
0.509 |
|
| 2013 |
Brittain EL, Pugh ME, Wheeler LA, Robbins IM, Loyd JE, Newman JH, Larkin EK, Austin ED, Hemnes AR. Shorter survival in familial versus idiopathic pulmonary arterial hypertension is associated with hemodynamic markers of impaired right ventricular function. Pulmonary Circulation. 3: 589-98. PMID 24618543 DOI: 10.1086/674326 |
0.514 |
|
| 2013 |
Fessel JP, Chen X, Frump A, Gladson S, Blackwell T, Kang C, Johnson J, Loyd JE, Hemnes A, Austin E, West J. Interaction between bone morphogenetic protein receptor type 2 and estrogenic compounds in pulmonary arterial hypertension. Pulmonary Circulation. 3: 564-77. PMID 24618541 DOI: 10.1086/674312 |
0.48 |
|
| 2013 |
Frump AL, Lowery JW, Hamid R, Austin ED, de Caestecker M. Abnormal trafficking of endogenously expressed BMPR2 mutant allelic products in patients with heritable pulmonary arterial hypertension. Plos One. 8: e80319. PMID 24224048 DOI: 10.1371/Journal.Pone.0080319 |
0.421 |
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| 2013 |
Soares JJ, Deutsch GH, Moore PE, Fazili MF, Austin ED, Brown RF, Sokolow AG, Hilmes MA, Young LR. Childhood interstitial lung diseases: an 18-year retrospective analysis. Pediatrics. 132: 684-91. PMID 24081995 DOI: 10.1542/Peds.2013-1780 |
0.346 |
|
| 2013 |
Austin ED, Loyd JE. Heritable forms of pulmonary arterial hypertension. Seminars in Respiratory and Critical Care Medicine. 34: 568-80. PMID 24037626 DOI: 10.1055/S-0033-1355443 |
0.525 |
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| 2013 |
Brittain EL, Pugh ME, Wheeler LA, Robbins IM, Loyd JE, Newman JH, Austin ED, Hemnes AR. Prostanoids but not oral therapies improve right ventricular function in pulmonary arterial hypertension. Jacc. Heart Failure. 1: 300-7. PMID 24015376 DOI: 10.1016/J.Jchf.2013.05.004 |
0.539 |
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| 2013 |
Austin ED, Lahm T, West J, Tofovic SP, Johansen AK, Maclean MR, Alzoubi A, Oka M. Gender, sex hormones and pulmonary hypertension. Pulmonary Circulation. 3: 294-314. PMID 24015330 DOI: 10.4103/2045-8932.114756 |
0.493 |
|
| 2013 |
Ma L, Roman-Campos D, Austin ED, Eyries M, Sampson KS, Soubrier F, Germain M, Trégouët DA, Borczuk A, Rosenzweig EB, Girerd B, Montani D, Humbert M, Loyd JE, Kass RS, et al. A novel channelopathy in pulmonary arterial hypertension. The New England Journal of Medicine. 369: 351-61. PMID 23883380 DOI: 10.1056/Nejmoa1211097 |
0.551 |
|
| 2013 |
Germain M, Eyries M, Montani D, Poirier O, Girerd B, Dorfmüller P, Coulet F, Nadaud S, Maugenre S, Guignabert C, Carpentier W, Vonk-Noordegraaf A, Lévy M, Chaouat A, Lambert JC, ... ... Austin ED, et al. Genome-wide association analysis identifies a susceptibility locus for pulmonary arterial hypertension. Nature Genetics. 45: 518-21. PMID 23502781 DOI: 10.1038/Ng.2581 |
0.554 |
|
| 2013 |
Wynn J, Krishnan U, Aspelund G, Zhang Y, Duong J, Stolar CJ, Hahn E, Pietsch J, Chung D, Moore D, Austin E, Mychaliska G, Gajarski R, Foong YL, Michelfelder E, et al. Outcomes of congenital diaphragmatic hernia in the modern era of management. The Journal of Pediatrics. 163: 114-9.e1. PMID 23375362 DOI: 10.1016/J.Jpeds.2012.12.036 |
0.451 |
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| 2012 |
Larkin EK, Newman JH, Austin ED, Hemnes AR, Wheeler L, Robbins IM, West JD, Phillips JA, Hamid R, Loyd JE. Longitudinal analysis casts doubt on the presence of genetic anticipation in heritable pulmonary arterial hypertension. American Journal of Respiratory and Critical Care Medicine. 186: 892-6. PMID 22923661 DOI: 10.1164/Rccm.201205-0886Oc |
0.529 |
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| 2012 |
Cogan J, Austin E, Hedges L, Womack B, West J, Loyd J, Hamid R. Role of BMPR2 alternative splicing in heritable pulmonary arterial hypertension penetrance. Circulation. 126: 1907-16. PMID 22923426 DOI: 10.1161/Circulationaha.112.106245 |
0.58 |
|
| 2012 |
Austin ED, Ma L, LeDuc C, Berman Rosenzweig E, Borczuk A, Phillips JA, Palomero T, Sumazin P, Kim HR, Talati MH, West J, Loyd JE, Chung WK. Whole exome sequencing to identify a novel gene (caveolin-1) associated with human pulmonary arterial hypertension. Circulation. Cardiovascular Genetics. 5: 336-43. PMID 22474227 DOI: 10.1161/Circgenetics.111.961888 |
0.513 |
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| 2012 |
Austin ED, Hamid R, Hemnes AR, Loyd JE, Blackwell T, Yu C, Phillips Iii JA, Gaddipati R, Gladson S, Gu E, West J, Lane KB. BMPR2 expression is suppressed by signaling through the estrogen receptor. Biology of Sex Differences. 3: 6. PMID 22348410 DOI: 10.1186/2042-6410-3-6 |
0.411 |
|
| 2012 |
Flynn C, Zheng S, Yan L, Hedges L, Womack B, Fessel J, Cogan J, Austin E, Loyd J, West J, Zhao Z, Hamid R. Connectivity map analysis of nonsense-mediated decay-positive BMPR2-related hereditary pulmonary arterial hypertension provides insights into disease penetrance. American Journal of Respiratory Cell and Molecular Biology. 47: 20-7. PMID 22312021 DOI: 10.1165/Rcmb.2011-0251Oc |
0.473 |
|
| 2012 |
Newman JH, Loyd JE, Hemnes AR, West JD, Austin E, Fessel J, Hamid R, Phillips JA. Chasing Pulmonary Hypertension: 1980–2012 Advances in Pulmonary Hypertension. 11: 121-123. DOI: 10.21693/1933-088X-11.3.121 |
0.466 |
|
| 2012 |
Benson L, Pugh M, Austin E, Fox K, Wheeler L, Brittain E, Robbins I, Hemnes A. Long-Term Impact of Diabetes Mellitus on Survival in Idiopathic and Heritable Pulmonary Arterial Hypertension Chest. 142: 847A. DOI: 10.1378/Chest.1390335 |
0.458 |
|
| 2012 |
Brittain EL, Pugh ME, Wheeler LA, Wells QS, Robbins IM, Loyd JE, Austin ED, Hemnes AR. HERITABLE PULMONARY ARTERIAL HYPERTENSION IS ASSOCIATED WITH WORSE PULMONARY CAPACITANCE AND RIGHT VENTRICULAR STROKE WORK INDEX COMPARED TO IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION Journal of the American College of Cardiology. 59: E1600. DOI: 10.1016/S0735-1097(12)61601-5 |
0.57 |
|
| 2011 |
Austin ED, Menon S, Hemnes AR, Robinson LR, Talati M, Fox KL, Cogan JD, Hamid R, Hedges LK, Robbins I, Lane K, Newman JH, Loyd JE, West J. Idiopathic and heritable PAH perturb common molecular pathways, correlated with increased MSX1 expression. Pulmonary Circulation. 1: 389-98. PMID 22140629 DOI: 10.4103/2045-8932.87308 |
0.426 |
|
| 2011 |
Fessel JP, Loyd JE, Austin ED. The genetics of pulmonary arterial hypertension in the post-BMPR2 era. Pulmonary Circulation. 1: 305-19. PMID 22140620 DOI: 10.4103/2045-8932.87293 |
0.46 |
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| 2011 |
Ikonomou L, Hemnes AR, Bilousova G, Hamid R, Loyd JE, Hatzopoulos AK, Kotton DN, Majka SM, Austin ED. Programmatic change: lung disease research in the era of induced pluripotency. American Journal of Physiology. Lung Cellular and Molecular Physiology. 301: L830-5. PMID 21984571 DOI: 10.1152/Ajplung.00255.2011 |
0.38 |
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| 2011 |
Lane KL, Talati M, Austin E, Hemnes AR, Johnson JA, Fessel JP, Blackwell T, Mernaugh RL, Robinson L, Fike C, Roberts LJ, West J. Oxidative injury is a common consequence of BMPR2 mutations. Pulmonary Circulation. 1: 72-83. PMID 21904662 DOI: 10.4103/2045-8932.78107 |
0.387 |
|
| 2011 |
Hemnes AR, Pugh ME, Newman AL, Robbins IM, Tolle J, Austin ED, Newman JH. End tidal CO(2) tension: pulmonary arterial hypertension vs pulmonary venous hypertension and response to treatment. Chest. 140: 1267-73. PMID 21622547 DOI: 10.1378/Chest.11-0155 |
0.59 |
|
| 2011 |
Austin ED. Gender, Sex Hormones, and Pulmonary Arterial Hypertension Advances in Pulmonary Hypertension. 10: 160-166. DOI: 10.21693/1933-088X-10.3.160 |
0.512 |
|
| 2010 |
Austin ED, Hamid R, Ahmad F. Somatic mutations in pulmonary arterial hypertension: primary or secondary events? American Journal of Respiratory and Critical Care Medicine. 182: 1094-6. PMID 21041561 DOI: 10.1164/Rccm.201007-1147Ed |
0.559 |
|
| 2010 |
Hamid R, Hedges LK, Austin E, Phillips JA, Loyd JE, Cogan JD. Transcripts from a novel BMPR2 termination mutation escape nonsense mediated decay by downstream translation re-initiation: implications for treating pulmonary hypertension. Clinical Genetics. 77: 280-6. PMID 20095988 DOI: 10.1111/J.1399-0004.2009.01311.X |
0.494 |
|
| 2010 |
Austin ED, Rock MT, Mosse CA, Vnencak-Jones CL, Yoder SM, Robbins IM, Loyd JE, Meyrick BO. T lymphocyte subset abnormalities in the blood and lung in pulmonary arterial hypertension. Respiratory Medicine. 104: 454-62. PMID 19880300 DOI: 10.1016/J.Rmed.2009.10.004 |
0.55 |
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| 2009 |
Austin ED, Phillips JA, Cogan JD, Hamid R, Yu C, Stanton KC, Phillips CA, Wheeler LA, Robbins IM, Newman JH, Loyd JE. Truncating and missense BMPR2 mutations differentially affect the severity of heritable pulmonary arterial hypertension. Respiratory Research. 10: 87. PMID 19785764 DOI: 10.1186/1465-9921-10-87 |
0.492 |
|
| 2009 |
Austin ED, Loyd JE, Phillips JA. Genetics of pulmonary arterial hypertension. Seminars in Respiratory and Critical Care Medicine. 30: 386-98. PMID 19634078 DOI: 10.1055/S-0029-1233308 |
0.56 |
|
| 2009 |
Austin ED, Cogan JD, West JD, Hedges LK, Hamid R, Dawson EP, Wheeler LA, Parl FF, Loyd JE, Phillips JA. Alterations in oestrogen metabolism: implications for higher penetrance of familial pulmonary arterial hypertension in females. The European Respiratory Journal. 34: 1093-9. PMID 19357154 DOI: 10.1183/09031936.00010409 |
0.411 |
|
| 2009 |
Hamid R, Cogan JD, Hedges LK, Austin E, Phillips JA, Newman JH, Loyd JE. Penetrance of pulmonary arterial hypertension is modulated by the expression of normal BMPR2 allele. Human Mutation. 30: 649-54. PMID 19206171 DOI: 10.1002/Humu.20922 |
0.45 |
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| 2008 |
Phillips JA, Poling JS, Phillips CA, Stanton KC, Austin ED, Cogan JD, Wheeler L, Yu C, Newman JH, Dietz HC, Loyd JE. Synergistic heterozygosity for TGFbeta1 SNPs and BMPR2 mutations modulates the age at diagnosis and penetrance of familial pulmonary arterial hypertension. Genetics in Medicine : Official Journal of the American College of Medical Genetics. 10: 359-65. PMID 18496036 DOI: 10.1097/Gim.0B013E318172Dcdf |
0.528 |
|
| 2007 |
Austin ED, Loyd JE. Genetics and mediators in pulmonary arterial hypertension. Clinics in Chest Medicine. 28: 43-57, vii-viii. PMID 17338927 DOI: 10.1016/J.Ccm.2006.11.007 |
0.59 |
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