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Ernesto Bongarzone - Publications

Affiliations: 
Anatomy and Cell Biology University of Illinois at Chicago, Chicago, IL, United States 
Area:
Cell Biology, Molecular Biology, Oncology
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37 high-probability publications. We are testing a new system for linking publications to authors. You can help! If you notice any inaccuracies, please sign in and mark papers as correct or incorrect matches. If you identify any major omissions or other inaccuracies in the publication list, please let us know.

Year Citation  Score
2022 Reiter CR, Rebiai R, Kwak A, Marshall J, Wozniak D, Scesa G, Nguyen D, Rue E, Pathmasiri C, Pijewski R, van Breemen R, Cologna S, Crocker SJ, Givogri MI, Bongarzone ER. The Pathogenic Sphingolipid Psychosine is Secreted in Extracellular Vesicles in the Brain of a Mouse Model of Krabbe Disease. Asn Neuro. 14: 17590914221087817. PMID 35300522 DOI: 10.1177/17590914221087817  0.32
2021 Bradbury AM, Bongarzone ER, Sands MS. Krabbe Disease: New Hope for an Old Disease. Neuroscience Letters. 135841. PMID 33766733 DOI: 10.1016/j.neulet.2021.135841  0.326
2021 Rebiai R, Givogri MI, Gowrishankar S, Cologna SM, Alford ST, Bongarzone ER. Synaptic Function and Dysfunction in Lysosomal Storage Diseases. Frontiers in Cellular Neuroscience. 15: 619777. PMID 33746713 DOI: 10.3389/fncel.2021.619777  0.342
2020 Weinstock NI, Kreher C, Favret J, Nguyen D, Bongarzone ER, Wrabetz L, Laura Feltri M, Shin D. Brainstem development requires galactosylceramidase and is critical for pathogenesis in a model of Krabbe disease. Nature Communications. 11: 5356. PMID 33097716 DOI: 10.1038/s41467-020-19179-w  0.352
2019 Reiter CR, Bongarzone ER. The Role of Vesicle Trafficking and Release in Oligodendrocyte Biology. Neurochemical Research. PMID 31782103 DOI: 10.1007/s11064-019-02913-2  0.342
2019 Sural-Fehr T, Singh H, Cantuti-Catelvetri L, Zhu H, Marshall MS, Rebiai R, Jastrzebski MJ, Givogri MI, Rasenick MM, Bongarzone ER. Inhibition of IGF-1-PI3K-Akt-mTORC2 in lipid rafts increases neuronal vulnerability in a genetic lysosomal glycosphingolipidosis. Disease Models & Mechanisms. PMID 31036560 DOI: 10.1242/Dmm.036590  0.554
2018 Bradbury AM, Rafi MA, Bagel J, Brisson BK, Marshall MS, Pesayco Salvador J, Jiang X, Swain GP, Prociuk ML, O'Donnell P, Fitzgerald C, Ory DS, Bongarzone ER, Shelton GD, Wenger DA, et al. AAVrh10 gene therapy ameliorates central and peripheral nervous system disease in canine globoid cell leukodystrophy (Krabbe disease). Human Gene Therapy. PMID 29316812 DOI: 10.1089/Hum.2017.151  0.322
2016 Marshall MS, Bongarzone ER. Beyond Krabbe's disease: The potential contribution of galactosylceramidase deficiency to neuronal vulnerability in late-onset synucleinopathies. Journal of Neuroscience Research. 94: 1328-32. PMID 27638614 DOI: 10.1002/jnr.23751  0.326
2016 Sural-Fehr T, Bongarzone ER. How membrane dysfunction influences neuronal survival pathways in sphingolipid storage disorders. Journal of Neuroscience Research. 94: 1042-8. PMID 27638590 DOI: 10.1002/jnr.23763  0.313
2016 Cantuti-Castelvetri L, Bongarzone ER. Synaptic failure: The achilles tendon of sphingolipidoses. Journal of Neuroscience Research. 94: 1031-6. PMID 27638588 DOI: 10.1002/jnr.23753  0.667
2016 Bongarzone ER, Escolar ML, Gray SJ, Kafri T, Vite CH, Sands MS. Insights into the Pathogenesis and Treatment of Krabbe Disease. Pediatric Endocrinology Reviews : Per. 13: 689-96. PMID 27491217  0.38
2016 Zhu H, Ornaghi F, Belin S, Givogri MI, Wrabetz L, Bongarzone ER. Generation of a LacZ reporter transgenic mouse line for the stereological analysis of oligodendrocyte loss in galactosylceramidase deficiency. Journal of Neuroscience Research. PMID 27426866 DOI: 10.1002/Jnr.23839  0.523
2015 Salazar K, Martínez M, Ulloa V, Bertinat R, Martínez F, Jara N, Espinoza F, Bongarzone ER, Nualart F. SVCT2 Overexpression in Neuroblastoma Cells Induces Cellular Branching that is Associated with ERK Signaling. Molecular Neurobiology. PMID 26646539 DOI: 10.1007/s12035-015-9553-z  0.303
2015 Cantuti-Castelvetri L, Maravilla E, Marshall M, Tamayo T, D'auria L, Monge J, Jeffries J, Sural-Fehr T, Lopez-Rosas A, Li G, Garcia K, van Breemen R, Vite C, Garcia J, Bongarzone ER. Mechanism of neuromuscular dysfunction in Krabbe disease. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 35: 1606-16. PMID 25632136 DOI: 10.1523/Jneurosci.2431-14.2015  0.646
2014 Smith BR, Santos MB, Marshall MS, Cantuti-Castelvetri L, Lopez-Rosas A, Li G, van Breemen R, Claycomb KI, Gallea JI, Celej MS, Crocker SJ, Givogri MI, Bongarzone ER. Neuronal inclusions of α-synuclein contribute to the pathogenesis of Krabbe disease. The Journal of Pathology. 232: 509-21. PMID 24415155 DOI: 10.1002/Path.4328  0.694
2013 Hawkins-Salsbury JA, Parameswar AR, Jiang X, Schlesinger PH, Bongarzone E, Ory DS, Demchenko AV, Sands MS. Psychosine, the cytotoxic sphingolipid that accumulates in globoid cell leukodystrophy, alters membrane architecture. Journal of Lipid Research. 54: 3303-11. PMID 24006512 DOI: 10.1016/J.Ymgme.2012.11.108  0.347
2013 Cantuti Castelvetri L, Givogri MI, Hebert A, Smith B, Song Y, Kaminska A, Lopez-Rosas A, Morfini G, Pigino G, Sands M, Brady ST, Bongarzone ER. The sphingolipid psychosine inhibits fast axonal transport in Krabbe disease by activation of GSK3β and deregulation of molecular motors. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 33: 10048-56. PMID 23761900 DOI: 10.1523/Jneurosci.0217-13.2013  0.336
2012 Zhu H, Lopez-Rosas A, Qiu X, Van Breemen RB, Bongarzone ER. Detection of the neurotoxin psychosine in samples of peripheral blood: application in diagnostics and follow-up of Krabbe disease. Archives of Pathology & Laboratory Medicine. 136: 709-10. PMID 22742542 DOI: 10.5858/Arpa.2011-0667-Le  0.474
2012 Cantuti-Castelvetri L, Zhu H, Givogri MI, Chidavaenzi RL, Lopez-Rosas A, Bongarzone ER. Psychosine induces the dephosphorylation of neurofilaments by deregulation of PP1 and PP2A phosphatases. Neurobiology of Disease. 46: 325-35. PMID 22326830 DOI: 10.1016/J.Nbd.2012.01.013  0.679
2012 Zhu H, Lopez-Rosas A, Qiu X, Breemen RBV, Bongarzone E. Erratum: Detection of the neurotoxin psychosine in samples of peripheral blood: Application in diagnostics and follow-up of krabbe disease (Archives of Pathology and Laboratory Medicine (2012) 136:7 (709-710)) Archives of Pathology & Laboratory Medicine. 136. DOI: 10.5858/1543-2165-136.9.973  0.521
2012 Maegawa G, Moser A, Hubbard W, Bongarzone E, Ribbens J, Maegawa G. Development of a Psychosine Assay to Identify Therapeutic Small Molecules for Krabbe Disease Molecular Genetics and Metabolism. 105: S45. DOI: 10.1016/J.Ymgme.2011.11.109  0.387
2011 Smith B, Galbiati F, Castelvetri LC, Givogri MI, Lopez-Rosas A, Bongarzone ER. Peripheral neuropathy in the Twitcher mouse involves the activation of axonal caspase 3. Asn Neuro. 3. PMID 21929508 DOI: 10.1042/An20110019  0.356
2011 Castelvetri LC, Givogri MI, Zhu H, Smith B, Lopez-Rosas A, Qiu X, van Breemen R, Bongarzone ER. Axonopathy is a compounding factor in the pathogenesis of Krabbe disease. Acta Neuropathologica. 122: 35-48. PMID 21373782 DOI: 10.1007/S00401-011-0814-2  0.615
2010 Bongarzone E, Cantuti L, Givogri MI, Lopez-Rosas A, Pigino G, Morfini G, Brady S. 18. Axonopathy in a mouse model of Krabbe disease Molecular Genetics and Metabolism. 99: S11-S12. DOI: 10.1016/J.Ymgme.2009.10.035  0.36
2009 White AB, Givogri MI, Lopez-Rosas A, Cao H, van Breemen R, Thinakaran G, Bongarzone ER. Psychosine accumulates in membrane microdomains in the brain of krabbe patients, disrupting the raft architecture. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 29: 6068-77. PMID 19439584 DOI: 10.1523/Jneurosci.5597-08.2009  0.329
2009 Galbiati F, Givogri MI, Cantuti L, Lopez Rosas A, Cao H, van Breemen R, Bongarzone ER. Combined hematopoietic and lentiviral gene-transfer therapies in newborn twitcher mice reveal contemporaneous neurodegeneration and demyelination in Krabbe disease Journal of Neuroscience Research. 87: 1748-1759. PMID 19185028 DOI: 10.1002/Jnr.22006  0.323
2008 Givogri MI, Bottai D, Zhu HL, Fasano S, Lamorte G, Brambilla R, Vescovi A, Wrabetz L, Bongarzone E. Multipotential neural precursors transplanted into the metachromatic leukodystrophy brain fail to generate oligodendrocytes but contribute to limit brain dysfunction. Developmental Neuroscience. 30: 340-57. PMID 18667806 DOI: 10.1159/000150127  0.548
2008 Givogri MI, Bottai D, Zhu HL, Fasano S, Lamorte G, Brambilla R, Vescovi A, Wrabetz L, Bongarzone E. Multipotential neural precursors transplanted into the metachromatic leukodystrophy brain fail to generate oligodendrocytes but contribute to limit brain dysfunction (Developmental Neuroscience DOI: 10.1159/000150127) Developmental Neuroscience. 30: 357. DOI: 10.1159/000159456  0.516
2007 Galbiati F, Basso V, Cantuti L, Givogri MI, Lopez-Rosas A, Perez N, Vasu C, Cao H, van Breemen R, Mondino A, Bongarzone ER. Autonomic denervation of lymphoid organs leads to epigenetic immune atrophy in a mouse model of Krabbe disease. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 27: 13730-8. PMID 18077684 DOI: 10.1523/Jneurosci.3379-07.2007  0.348
2007 Badaloni A, Bonanomi D, Albieri I, Givogri I, Bongarzone E, Valtorta F, Consalez GG. Transgenic mice expressing a dual, CRE-inducible reporter for the analysis of axon guidance and synaptogenesis. Genesis (New York, N.Y. : 2000). 45: 405-12. PMID 17554764 DOI: 10.1002/Dvg.20307  0.434
2007 Galbiati F, Clementi G, Superchi D, Givogri MI, Bongarzone ER. Effects of irradiation on the postnatal development of the brain in a genetic mouse model of globoid cell leukodystrophy. Neurochemical Research. 32: 377-88. PMID 17203404 DOI: 10.1007/s11064-006-9247-z  0.325
2006 Dolcetta D, Perani L, Givogri MI, Galbiati F, Amadio S, Del Carro U, Finocchiaro G, Fanzani A, Marchesini S, Naldini L, Roncarolo MG, Bongarzone E. Design and optimization of lentiviral vectors for transfer of GALC expression in Twitcher brain. The Journal of Gene Medicine. 8: 962-71. PMID 16732552 DOI: 10.1002/Jgm.924  0.386
2006 Givogri MI, Galbiati F, Fasano S, Amadio S, Perani L, Superchi D, Morana P, Del Carro U, Marchesini S, Brambilla R, Wrabetz L, Bongarzone E. Oligodendroglial progenitor cell therapy limits central neurological deficits in mice with metachromatic leukodystrophy. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 26: 3109-19. PMID 16554462 DOI: 10.1523/Jneurosci.4366-05.2006  0.412
2004 Dolcetta D, Perani L, Givogri MI, Galbiati F, Orlacchio A, Martino S, Roncarolo MG, Bongarzone E. Analysis of galactocerebrosidase activity in the mouse brain by a new histological staining method Journal of Neuroscience Research. 77: 462-464. PMID 15248301 DOI: 10.1002/Jnr.20169  0.404
2004 Jacobs EC, Bongarzone ER, Campagnoni CW, Campagnoni AT. Embryonic expression of the soma-restricted products of the myelin proteolipid gene in motor neurons and muscle. Neurochemical Research. 29: 997-1002. PMID 15139298 DOI: 10.1023/B:Nere.0000021244.38279.C4  0.308
2003 Jacobs EC, Bongarzone ER, Campagnoni CW, Kampf K, Campagnoni AT. Soma-restricted products of the myelin proteolipid gene are expressed primarily in neurons in the developing mouse nervous system. Developmental Neuroscience. 25: 96-104. PMID 12966208 DOI: 10.1159/000072259  0.318
1994 Escobar Cabrera OE, Bongarzone ER, Soto EF, Pasquini JM. Single intracerebral injection of apotransferrin in young rats induces increased myelination Developmental Neuroscience. 16: 248-254. PMID 7768203 DOI: 10.1159/000112116  0.313
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