| Year |
Citation |
Score |
| 2021 |
Wang Z, Qin K, Camacho MV, Cali I, Yuan J, Shen P, Greenlee J, Kong Q, Mastrianni JA, Zou WQ. Generation of human chronic wasting disease in transgenic mice. Acta Neuropathologica Communications. 9: 158. PMID 34565488 DOI: 10.1186/s40478-021-01262-y |
0.426 |
|
| 2019 |
Qin K, Zhao L, Gregory C, Solanki A, Mastrianni JA. "Dual Disease" TgAD/GSS mice exhibit enhanced Alzheimer's disease pathology and reveal PrP-dependent secretion of Aβ. Scientific Reports. 9: 8524. PMID 31189938 DOI: 10.1038/s41598-019-44317-w |
0.368 |
|
| 2019 |
Qin K, Zhao L, Solanki A, Busch C, Mastrianni J. Anle138b prevents PrP plaque accumulation in Tg(PrP-A116V) mice but does not mitigate clinical disease. The Journal of General Virology. PMID 31045489 DOI: 10.1099/Jgv.0.001262 |
0.499 |
|
| 2018 |
Cali I, Mikhail F, Qin K, Gregory C, Solanki A, Martinez MC, Zhao L, Appleby B, Gambetti P, Norstrom E, Mastrianni JA. Impaired transmissibility of atypical prions from genetic CJD. Neurology. Genetics. 4: e253. PMID 30109268 DOI: 10.1212/Nxg.0000000000000253 |
0.669 |
|
| 2018 |
Gu H, Kirchhein Y, Zhu T, Zhao G, Peng H, Du E, Liu J, Mastrianni JA, Farlow MR, Dodel R, Du Y. IVIG Delays Onset in a Mouse Model of Gerstmann-Sträussler-Scheinker Disease. Molecular Neurobiology. PMID 30027340 DOI: 10.1007/s12035-018-1228-0 |
0.387 |
|
| 2014 |
Mastrianni JA. Prion Diseases Rosenberg's Molecular and Genetic Basis of Neurological and Psychiatric Disease: Fifth Edition. 229-254. DOI: 10.1016/B978-0-12-410529-4.00021-8 |
0.392 |
|
| 2013 |
Cortes CJ, Qin K, Norstrom EM, Green WN, Bindokas VP, Mastrianni JA. Early Delivery of Misfolded PrP from ER to Lysosomes by Autophagy. International Journal of Cell Biology. 2013: 560421. PMID 24454378 DOI: 10.1155/2013/560421 |
0.726 |
|
| 2012 |
Cortes CJ, Qin K, Cook J, Solanki A, Mastrianni JA. Rapamycin delays disease onset and prevents PrP plaque deposition in a mouse model of Gerstmann-Sträussler-Scheinker disease. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 32: 12396-405. PMID 22956830 DOI: 10.1523/JNEUROSCI.6189-11.2012 |
0.429 |
|
| 2012 |
Leggett C, McGehee DS, Mastrianni J, Yang W, Bai T, Brorson JR. Tunicamycin produces TDP-43 cytoplasmic inclusions in cultured brain organotypic slices. Journal of the Neurological Sciences. 317: 66-73. PMID 22459357 DOI: 10.1016/J.Jns.2012.02.027 |
0.322 |
|
| 2011 |
Barria MA, Telling GC, Gambetti P, Mastrianni JA, Soto C. Generation of a new form of human PrP(Sc) in vitro by interspecies transmission from cervid prions. The Journal of Biological Chemistry. 286: 7490-5. PMID 21209079 DOI: 10.1074/Jbc.M110.198465 |
0.42 |
|
| 2010 |
Brown K, Mastrianni JA. The prion diseases. Journal of Geriatric Psychiatry and Neurology. 23: 277-98. PMID 20938044 DOI: 10.1055/S-2000-9396 |
0.432 |
|
| 2010 |
Zou WQ, Puoti G, Xiao X, Yuan J, Qing L, Cali I, Shimoji M, Langeveld JP, Castellani R, Notari S, Crain B, Schmidt RE, Geschwind M, Dearmond SJ, Cairns NJ, ... ... Mastrianni J, et al. Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. Annals of Neurology. 68: 162-72. PMID 20695009 DOI: 10.1002/Ana.22094 |
0.505 |
|
| 2010 |
Mastrianni JA. The genetics of prion diseases. Genetics in Medicine : Official Journal of the American College of Medical Genetics. 12: 187-95. PMID 20216075 DOI: 10.1097/GIM.0b013e3181cd7374 |
0.425 |
|
| 2010 |
Mallik S, Yang W, Norstrom EM, Mastrianni JA. Live cell fluorescence resonance energy transfer predicts an altered molecular association of heterologous PrPSc with PrPC. The Journal of Biological Chemistry. 285: 8967-75. PMID 20086009 DOI: 10.1074/Jbc.M109.058107 |
0.733 |
|
| 2009 |
Yang W, Cook J, Rassbach B, Lemus A, DeArmond SJ, Mastrianni JA. A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 29: 10072-80. PMID 19675240 DOI: 10.1523/JNEUROSCI.2542-09.2009 |
0.399 |
|
| 2008 |
Tunnell E, Wollman R, Mallik S, Cortes CJ, Dearmond SJ, Mastrianni JA. A novel PRNP-P105S mutation associated with atypical prion disease and a rare PrPSc conformation. Neurology. 71: 1431-8. PMID 18955686 DOI: 10.1212/01.wnl.0000330237.94742.fa |
0.374 |
|
| 2008 |
Abalos GC, Cruite JT, Bellon A, Hemmers S, Akagi J, Mastrianni JA, Williamson RA, Solforosi L. Identifying key components of the PrPC-PrPSc replicative interface. The Journal of Biological Chemistry. 283: 34021-8. PMID 18826953 DOI: 10.1074/Jbc.M804475200 |
0.498 |
|
| 2008 |
Gambetti P, Dong Z, Yuan J, Xiao X, Zheng M, Alshekhlee A, Castellani R, Cohen M, Barria MA, Gonzalez-Romero D, Belay ED, Schonberger LB, Marder K, Harris C, Burke JR, ... ... Mastrianni JA, et al. A novel human disease with abnormal prion protein sensitive to protease. Annals of Neurology. 63: 697-708. PMID 18571782 DOI: 10.1002/Ana.21420 |
0.432 |
|
| 2007 |
Norstrom EM, Ciaccio MF, Rassbach B, Wollmann R, Mastrianni JA. Cytosolic prion protein toxicity is independent of cellular prion protein expression and prion propagation. Journal of Virology. 81: 2831-7. PMID 17182694 DOI: 10.1128/Jvi.02157-06 |
0.722 |
|
| 2006 |
Norstrom EM, Mastrianni JA. The charge structure of helix 1 in the prion protein regulates conversion to pathogenic PrPSc. Journal of Virology. 80: 8521-9. PMID 16912302 DOI: 10.1128/Jvi.00366-06 |
0.703 |
|
| 2006 |
Mastrianni JA. ONE FAMILYʼS HISTORY WITH PRION DISEASE PART HISTORY, PART MYSTERY, AND PART INVESTIGATIVE REPORT Neurology Today. 6: 32. DOI: 10.1097/00132985-200612050-00016 |
0.32 |
|
| 2005 |
Li X, Rowland LP, Mitsumoto H, Przedborski S, Bird TD, Schellenberg GD, Peskind E, Johnson N, Siddique T, Mesulam MM, Weintraub S, Mastrianni JA. Prion protein codon 129 genotype prevalence is altered in primary progressive aphasia. Annals of Neurology. 58: 858-64. PMID 16315279 DOI: 10.1002/Ana.20646 |
0.334 |
|
| 2005 |
Norstrom EM, Mastrianni JA. The AGAAAAGA palindrome in PrP is required to generate a productive PrPSc-PrPC complex that leads to prion propagation. The Journal of Biological Chemistry. 280: 27236-43. PMID 15917252 DOI: 10.1074/Jbc.M413441200 |
0.719 |
|
| 2003 |
Korth C, Kaneko K, Groth D, Heye N, Telling G, Mastrianni J, Parchi P, Gambetti P, Will R, Ironside J, Heinrich C, Tremblay P, DeArmond SJ, Prusiner SB. Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proceedings of the National Academy of Sciences of the United States of America. 100: 4784-9. PMID 12684540 DOI: 10.1073/Pnas.2627989100 |
0.437 |
|
| 2002 |
Mastrianni J, Roos RP. "Out, damned spot! out, I say!...": issues related to prion decontamination. Neurology. 59: 488-9. PMID 12196639 DOI: 10.1212/Wnl.59.4.488 |
0.477 |
|
| 2001 |
Mastrianni JA, Capellari S, Telling GC, Han D, Bosque P, Prusiner SB, DeArmond SJ. Inherited prion disease caused by the V210I mutation: transmission to transgenic mice. Neurology. 57: 2198-205. PMID 11756597 DOI: 10.1212/Wnl.57.12.2198 |
0.36 |
|
| 2000 |
Worrall BB, Rowland LP, Chin SS, Mastrianni JA. Amyotrophy in prion diseases. Archives of Neurology. 57: 33-8. PMID 10634430 DOI: 10.1001/Archneur.57.1.33 |
0.315 |
|
| 1999 |
Mastrianni JA, Nixon R, Layzer R, Telling GC, Han D, DeArmond SJ, Prusiner SB. Prion protein conformation in a patient with sporadic fatal insomnia. The New England Journal of Medicine. 340: 1630-8. PMID 10341275 DOI: 10.1056/Nejm199905273402104 |
0.385 |
|
| 1998 |
Mastrianni JA. The prion diseases: Creutzfeldt-Jakob, Gerstmann-Straussler-Scheinker, and related disorders Journal of Geriatric Psychiatry and Neurology. 11: 78-97. PMID 9877529 |
0.384 |
|
| 1998 |
Hegde RS, Mastrianni JA, Scott MR, DeFea KA, Tremblay P, Torchia M, DeArmond SJ, Prusiner SB, Lingappa VR. A transmembrane form of the prion protein in neurodegenerative disease. Science (New York, N.Y.). 279: 827-34. PMID 9452375 DOI: 10.1126/Science.279.5352.827 |
0.448 |
|
| 1997 |
MacGowan DJL, Delanty N, Petito F, Edgar M, Mastrianni J, DeArmond SJ. Isolated myoclonic alien hand as the sole presentation of pathologically established Creutzfeldt-Jakob disease: A report of two patients Journal of Neurology Neurosurgery and Psychiatry. 63: 404-407. PMID 9328266 DOI: 10.1136/Jnnp.63.3.404 |
0.378 |
|
| 1996 |
Telling GC, Parchi P, DeArmond SJ, Cortelli P, Montagna P, Gabizon R, Mastrianni J, Lugaresi E, Gambetti P, Prusiner SB. Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science (New York, N.Y.). 274: 2079-82. PMID 8953038 DOI: 10.1126/Science.274.5295.2079 |
0.506 |
|
| 1996 |
Mastrianni JA, Iannicola C, Myers RM, DeArmond S, Prusiner SB. Mutation of the prion protein gene at codon 208 in familial Creutzfeldt-Jakob disease. Neurology. 47: 1305-12. PMID 8909447 DOI: 10.1212/Wnl.47.5.1305 |
0.307 |
|
| 1996 |
Nixon R, Mastrianni J, Roberts J, Prusiner S, DeArmond S. SPORADIC OCCURRENCE OF FATAL THALAMIC INSOMNIA WITHOUT A PRION PROTEIN GENE MUTATION Journal of Neuropathology and Experimental Neurology. 55: 661. DOI: 10.1097/00005072-199605000-00232 |
0.318 |
|
| 1995 |
Spudich S, Mastrianni JA, Wrensch M, Gabizon R, Meiner Z, Kahana I, Rosenmann H, Kahana E, Prusiner SB. Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene. Molecular Medicine (Cambridge, Mass.). 1: 607-13. PMID 8529127 DOI: 10.1007/Bf03401601 |
0.375 |
|
| 1995 |
Telling GC, Scott M, Mastrianni J, Gabizon R, Torchia M, Cohen FE, DeArmond SJ, Prusiner SB. Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein. Cell. 83: 79-90. PMID 7553876 DOI: 10.1016/0092-8674(95)90236-8 |
0.468 |
|
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