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Pierluigi C. Gambetti, MD, University of Bologna - Publications

Affiliations: 
Pathology Case Western Reserve University, Cleveland Heights, OH, United States 
Area:
Neuropathology, prion, Alzheimer disease
Website:
http://googlist.ru
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269 high-probability publications. We are testing a new system for linking publications to authors. You can help! If you notice any inaccuracies, please sign in and mark papers as correct or incorrect matches. If you identify any major omissions or other inaccuracies in the publication list, please let us know.

Year Citation  Score
2023 Cracco L, Cali I, Cohen ML, Aslam R, Notari S, Kong Q, Newell KL, Ghetti B, Appleby BS, Gambetti P. Efficient transmission of human prion diseases to a glycan-free prion protein-expressing host. Brain : a Journal of Neurology. PMID 38000783 DOI: 10.1093/brain/awad399  0.842
2023 Pritzkow S, Ramirez F, Lyon A, Schulz PE, Appleby B, Moda F, Ramirez S, Notari S, Gambetti P, Soto C. Detection of prions in the urine of patients affected by sporadic Creutzfeldt-Jakob disease. Annals of Clinical and Translational Neurology. PMID 37814583 DOI: 10.1002/acn3.51919  0.695
2023 Venkatraghavan V, Pascuzzo R, Bron EE, Moscatelli M, Grisoli M, Pickens A, Cohen ML, Schonberger LB, Gambetti P, Appleby BS, Klein S, Bizzi A. A discriminative event-based model for subtype diagnosis of sporadic Creutzfeldt-Jakob disease using brain MRI. Alzheimer's & Dementia : the Journal of the Alzheimer's Association. PMID 36749840 DOI: 10.1002/alz.12939  0.691
2022 Baiardi S, Mammana A, Rossi M, Ladogana A, Carlà B, Gambetti P, Capellari S, Parchi P. Phenotypic Heterogeneity of Variably Protease-Sensitive Prionopathy: A Report of Three Cases Carrying Different Genotypes at Codon 129. Viruses. 14. PMID 35215959 DOI: 10.3390/v14020367  0.69
2021 Baiardi S, Rossi M, Mammana A, Appleby BS, Barria MA, Calì I, Gambetti P, Gelpi E, Giese A, Ghetti B, Herms J, Ladogana A, Mikol J, Pal S, Ritchie DL, et al. Phenotypic diversity of genetic Creutzfeldt-Jakob disease: a histo-molecular-based classification. Acta Neuropathologica. PMID 34324063 DOI: 10.1007/s00401-021-02350-y  0.773
2021 Cali I, Espinosa JC, Nemani SK, Marin-Moreno A, Camacho MV, Aslam R, Kitamoto T, Appleby BS, Torres JM, Gambetti P. Two distinct conformers of PrP type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo. Acta Neuropathologica Communications. 9: 55. PMID 33766126 DOI: 10.1186/s40478-021-01132-7  0.548
2020 Bizzi A, Pascuzzo R, Blevins J, Moscatelli MEM, Grisoli M, Lodi R, Doniselli FM, Castelli G, Cohen ML, Stamm A, Schonberger LB, Appleby BS, Gambetti P. Subtype diagnosis of sporadic Creutzfeldt-Jakob disease with diffusion MRI. Annals of Neurology. PMID 33274461 DOI: 10.1002/ana.25983  0.69
2020 Jones E, Hummerich H, Viré E, Uphill J, Dimitriadis A, Speedy H, Campbell T, Norsworthy P, Quinn L, Whitfield J, Linehan J, Jaunmuktane Z, Brandner S, Jat P, Nihat A, ... ... Gambetti P, et al. Identification of novel risk loci and causal insights for sporadic Creutzfeldt-Jakob disease: a genome-wide association study. The Lancet. Neurology. 19: 840-848. PMID 32949544 DOI: 10.1016/S1474-4422(20)30273-8  0.683
2020 Nemani SK, Xiao X, Cali I, Cracco L, Puoti G, Nigro M, Lavrich J, Bharara Singh A, Appleby BS, Sim VL, Notari S, Surewicz WK, Gambetti P. A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease. Acta Neuropathologica Communications. 8: 85. PMID 32560672 DOI: 10.1186/S40478-020-00966-X  0.833
2020 Pascuzzo R, Oxtoby NP, Young AL, Blevins J, Castelli G, Garbarino S, Cohen ML, Schonberger LB, Gambetti P, Appleby BS, Alexander DC, Bizzi A. Prion propagation estimated from brain diffusion MRI is subtype dependent in sporadic Creutzfeldt-Jakob disease. Acta Neuropathologica. PMID 32535770 DOI: 10.1007/S00401-020-02168-0  0.702
2020 Bizzi A, Pascuzzo R, Blevins J, Grisoli M, Lodi R, Moscatelli MEM, Castelli G, Cohen ML, Schonberger LB, Foutz A, Safar JG, Appleby BS, Gambetti P. Evaluation of a New Criterion for Detecting Prion Disease With Diffusion Magnetic Resonance Imaging. Jama Neurology. PMID 32478816 DOI: 10.1001/Jamaneurol.2020.1319  0.677
2020 Cali I, Puoti G, Smucny J, Curtiss PM, Cracco L, Kitamoto T, Occhipinti R, Cohen ML, Appleby BS, Gambetti P. Co-existence of PrP types 1 and 2 in sporadic Creutzfeldt-Jakob disease of the VV subgroup: phenotypic and prion protein characteristics. Scientific Reports. 10: 1503. PMID 32001774 DOI: 10.1038/S41598-020-58446-0  0.814
2019 Camacho MV, Telling G, Kong Q, Gambetti P, Notari S. Role of prion protein glycosylation in replication of human prions by protein misfolding cyclic amplification. Laboratory Investigation; a Journal of Technical Methods and Pathology. PMID 31249376 DOI: 10.1038/S41374-019-0282-1  0.821
2019 Cracco L, Xiao X, Nemani SK, Lavrich J, Cali I, Ghetti B, Notari S, Surewicz WK, Gambetti P. Gerstmann-Sträussler-Scheinker disease revisited: accumulation of covalently-linked multimers of internal prion protein fragments. Acta Neuropathologica Communications. 7: 1. PMID 31142381 DOI: 10.1186/S40478-019-0734-2  0.809
2019 Cali I, Lavrich J, Moda F, Kofskey D, Nemani SK, Appleby B, Tagliavini F, Soto C, Gambetti P, Notari S. PMCA-replicated PrP in urine of vCJD patients maintains infectivity and strain characteristics of brain PrP: Transmission study. Scientific Reports. 9: 5191. PMID 30914754 DOI: 10.1038/S41598-019-41694-0  0.814
2019 Wang Z, Manca M, Foutz A, Camacho MV, Raymond GJ, Race B, Orru CD, Yuan J, Shen P, Li B, Lang Y, Dang J, Adornato A, Williams K, Maurer NR, ... Gambetti P, et al. Publisher Correction: Early preclinical detection of prions in the skin of prion-infected animals. Nature Communications. 10: 640. PMID 30718499 DOI: 10.1038/S41467-019-08648-6  0.76
2019 Wang Z, Manca M, Foutz A, Camacho MV, Raymond GJ, Race B, Orru CD, Yuan J, Shen P, Li B, Lang Y, Dang J, Adornato A, Williams K, Maurer NR, ... Gambetti P, et al. Early preclinical detection of prions in the skin of prion-infected animals. Nature Communications. 10: 247. PMID 30651538 DOI: 10.1038/S41467-018-08130-9  0.773
2019 Nonno R, Notari S, Di Bari MA, Cali I, Pirisinu L, d'Agostino C, Cracco L, Kofskey D, Vanni I, Lavrich J, Parchi P, Agrimi U, Gambetti P. Variable Protease-Sensitive Prionopathy Transmission to Bank Voles. Emerging Infectious Diseases. 25: 73-81. PMID 30561322 DOI: 10.3201/Eid2501.180807  0.834
2018 Nemani SK, Notari S, Cali I, Alvarez VE, Kofskey D, Cohen M, Stern RA, Appleby B, Abrams J, Schonberger L, McKee A, Gambetti P. Co-occurrence of chronic traumatic encephalopathy and prion disease. Acta Neuropathologica Communications. 6: 140. PMID 30563563 DOI: 10.1186/S40478-018-0643-9  0.845
2018 Cali I, Mikhail F, Qin K, Gregory C, Solanki A, Martinez MC, Zhao L, Appleby B, Gambetti P, Norstrom E, Mastrianni JA. Impaired transmissibility of atypical prions from genetic CJD. Neurology. Genetics. 4: e253. PMID 30109268 DOI: 10.1212/Nxg.0000000000000253  0.614
2018 Cracco L, Appleby BS, Gambetti P. Fatal familial insomnia and sporadic fatal insomnia. Handbook of Clinical Neurology. 153: 271-299. PMID 29887141 DOI: 10.1016/B978-0-444-63945-5.00015-5  0.497
2018 Notari S, Appleby BS, Gambetti P. Variably protease-sensitive prionopathy. Handbook of Clinical Neurology. 153: 175-190. PMID 29887135 DOI: 10.1016/B978-0-444-63945-5.00010-6  0.769
2018 Cali I, Cohen ML, Haїk S, Parchi P, Giaccone G, Collins SJ, Kofskey D, Wang H, McLean CA, Brandel JP, Privat N, Sazdovitch V, Duyckaerts C, Kitamoto T, Belay ED, ... ... Gambetti P, et al. Iatrogenic Creutzfeldt-Jakob disease with Amyloid-β pathology: an international study. Acta Neuropathologica Communications. 6: 5. PMID 29310723 DOI: 10.1186/S40478-017-0503-Z  0.782
2017 Mente KP, O'Donnell JK, Jones SE, Cohen ML, Thompson NR, Bizzi A, Gambetti P, Safar JG, Appleby BS. Fluorodeoxyglucose Positron Emission Tomography (FDG-PET) Correlation of Histopathology and MRI in Prion Disease. Alzheimer Disease and Associated Disorders. PMID 28121634 DOI: 10.1097/Wad.0000000000000188  0.7
2017 Cracco L, Notari S, Cali I, Sy MS, Chen SG, Cohen ML, Ghetti B, Appleby BS, Zou WQ, Caughey B, Safar JG, Gambetti P. Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type. Scientific Reports. 7: 38280. PMID 28091514 DOI: 10.1038/Srep38280  0.836
2016 Foutz A, Appleby BS, Hamlin C, Liu X, Yang S, Cohen Y, Chen W, Blevins J, Fausett C, Wang H, Gambetti P, Zhang S, Hughson A, Tatsuoka C, Schonberger LB, et al. Diagnostic and Prognostic Value of Human Prion Detection in Cerebrospinal Fluid. Annals of Neurology. PMID 27893164 DOI: 10.1002/Ana.24833  0.657
2016 Choi JK, Cali I, Surewicz K, Kong Q, Gambetti P, Surewicz WK. Amyloid fibrils from the N-terminal prion protein fragment are infectious. Proceedings of the National Academy of Sciences of the United States of America. PMID 27849581 DOI: 10.1073/Pnas.1610716113  0.786
2016 Coulthart MB, Geschwind MD, Qureshi S, Phielipp N, Demarsh A, Abrams JY, Belay E, Gambetti P, Jansen GH, Lang AE, Schonberger LB. A case cluster of variant Creutzfeldt-Jakob disease linked to the Kingdom of Saudi Arabia. Brain : a Journal of Neurology. 139: 2609-2616. PMID 27671029 DOI: 10.1093/Brain/Aww206  0.305
2016 Umeh CC, Kalakoti P, Greenberg MK, Notari S, Cohen Y, Gambetti P, Oblak AL, Ghetti B, Mari Z. Clinicopathological Correlates in a PRNP P102L Mutation Carrier with Rapidly Progressing Parkinsonism-dystonia. Movement Disorders Clinical Practice. 3: 355-358. PMID 27617269 DOI: 10.1002/Mdc3.12307  0.717
2016 Balendra R, Uphill J, Collinson C, Druyeh R, Adamson G, Hummerich H, Zerr I, Gambetti P, Collinge J, Mead S. Variants of PLCXD3 are not associated with variant or sporadic Creutzfeldt-Jakob disease in a large international study. Bmc Medical Genetics. 17: 28. PMID 27055460 DOI: 10.1186/S12881-016-0278-2  0.436
2016 Pirisinu L, Di Bari MA, D'Agostino C, Marcon S, Riccardi G, Poleggi A, Cohen ML, Appleby BS, Gambetti P, Ghetti B, Agrimi U, Nonno R. Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases. Scientific Reports. 6: 20443. PMID 26841849 DOI: 10.1038/Srep20443  0.706
2016 Minikel EV, Vallabh SM, Lek M, Estrada K, Samocha KE, Sathirapongsasuti JF, McLean CY, Tung JY, Yu LP, Gambetti P, Blevins J, Zhang S, Cohen Y, Chen W, Yamada M, et al. Quantifying prion disease penetrance using large population control cohorts. Science Translational Medicine. 8: 322ra9. PMID 26791950 DOI: 10.1126/Scitranslmed.Aad5169  0.728
2016 Ghetti B, Murrell JR, Richardson RM, Epperson F, Gambetti P, Oblak AL. P4-228: Neuronal Intracytoplasmic PrP Deposits in Dominantly Inherited Creutzfeldt-Jakob Disease Associated With the PRNP E200K-129V Haplotype Alzheimer's & Dementia. 12: P1116-P1117. DOI: 10.1016/J.Jalz.2016.06.2320  0.361
2015 Orrú CD, Groveman BR, Raymond LD, Hughson AG, Nonno R, Zou W, Ghetti B, Gambetti P, Caughey B. Correction: Bank Vole Prion Protein As an Apparently Universal Substrate for RT-QuIC-Based Detection and Discrimination of Prion Strains. Plos Pathogens. 11: e1005117. PMID 26284358 DOI: 10.1371/Journal.Ppat.1005117  0.537
2015 Hudson G, Uphill J, Hummerich H, Blevins J, Gambetti P, Zerr I, Collinge J, Mead S, Chinnery PF. Inherited mtDNA variations are not strong risk factors in human prion disease. Neurobiology of Aging. 36: 2908.e1-3. PMID 26239179 DOI: 10.1016/J.Neurobiolaging.2015.07.005  0.34
2015 Cali I, Miller CJ, Parisi JE, Geschwind MD, Gambetti P, Schonberger LB. Distinct pathological phenotypes of Creutzfeldt-Jakob disease in recipients of prion-contaminated growth hormone. Acta Neuropathologica Communications. 3: 37. PMID 26108478 DOI: 10.1186/S40478-015-0214-2  0.684
2015 Orrú CD, Groveman BR, Raymond LD, Hughson AG, Nonno R, Zou W, Ghetti B, Gambetti P, Caughey B. Bank Vole Prion Protein As an Apparently Universal Substrate for RT-QuIC-Based Detection and Discrimination of Prion Strains. Plos Pathogens. 11: e1004983. PMID 26086786 DOI: 10.1371/Journal.Ppat.1004983  0.607
2015 Maheshwari A, Fischer M, Gambetti P, Parker A, Ram A, Soto C, Concha-Marambio L, Cohen Y, Belay ED, Maddox RA, Mead S, Goodman C, Kass JS, Schonberger LB, Hussein HM. Recent US Case of Variant Creutzfeldt-Jakob Disease-Global Implications. Emerging Infectious Diseases. 21: 750-9. PMID 25897712 DOI: 10.3201/Eid2105.142017  0.376
2015 Del Pilar-Morales EA, Cali I, Chapas J, Bertrán-Pasarell J, Puoti G, Gambetti P, Nobo U. Sporadic Creutzfeldt-Jakob disease in a native Puerto Rican patient. Puerto Rico Health Sciences Journal. 34: 40-3. PMID 25856877  0.78
2015 Figini M, Alexander DC, Redaelli V, Fasano F, Grisoli M, Baselli G, Gambetti P, Tagliavini F, Bizzi A. Mathematical models for the diffusion magnetic resonance signal abnormality in patients with prion diseases. Neuroimage. Clinical. 7: 142-54. PMID 25610776 DOI: 10.1016/J.Nicl.2014.11.017  0.565
2015 Ghoshal N, Perry A, McKeel D, Schmidt RE, Carter D, Norton J, Zou WQ, Xiao X, Puoti G, Notari S, Gambetti P, Morris JC, Cairns NJ. Variably Protease-sensitive Prionopathy in an Apparent Cognitively Normal 93-Year-Old. Alzheimer Disease and Associated Disorders. 29: 173-6. PMID 24845762 DOI: 10.1097/Wad.0000000000000049  0.762
2014 Xiao X, Yuan J, Qing L, Cali I, Mikol J, Delisle MB, Uro-Coste E, Zeng L, Abouelsaad M, Gazgalis D, Martinez MC, Wang GX, Brown P, Ironside JW, Gambetti P, et al. Comparative Study of Prions in Iatrogenic and Sporadic Creutzfeldt-Jakob Disease. Journal of Clinical & Cellular Immunology. 5. PMID 25419482 DOI: 10.4172/2155-9899.1000240  0.821
2014 Notari S, Xiao X, Espinosa JC, Cohen Y, Qing L, Aguilar-Calvo P, Kofskey D, Cali I, Cracco L, Kong Q, Torres JM, Zou W, Gambetti P. Transmission characteristics of variably protease-sensitive prionopathy. Emerging Infectious Diseases. 20: 2006-14. PMID 25418590 DOI: 10.3201/Eid2012.140548  0.843
2014 Slattery CF, Beck JA, Harper L, Adamson G, Abdi Z, Uphill J, Campbell T, Druyeh R, Mahoney CJ, Rohrer JD, Kenny J, Lowe J, Leung KK, Barnes J, Clegg SL, ... ... Gambetti P, et al. R47H TREM2 variant increases risk of typical early-onset Alzheimer's disease but not of prion or frontotemporal dementia. Alzheimer's & Dementia : the Journal of the Alzheimer's Association. 10: 602-608.e4. PMID 25160042 DOI: 10.1016/J.Jalz.2014.05.1751  0.354
2014 Moda F, Gambetti P, Notari S, Concha-Marambio L, Catania M, Park KW, Maderna E, Suardi S, Haïk S, Brandel JP, Ironside J, Knight R, Tagliavini F, Soto C. Prions in the urine of patients with variant Creutzfeldt-Jakob disease. The New England Journal of Medicine. 371: 530-9. PMID 25099577 DOI: 10.1056/Nejmoa1404401  0.748
2014 Cannon A, Bieniek KF, Lin WL, Notari S, Zou WQ, Gambetti P, Pedraza O, Graff-Radford NR, Ferman TJ, Dickson DW. Concurrent variably protease-sensitive prionopathy and amyotrophic lateral sclerosis. Acta Neuropathologica. 128: 313-5. PMID 24928712 DOI: 10.1007/S00401-014-1309-8  0.78
2014 Ghetti BF, Miller DC, Zou W, Cohen Y, Richardson R, Oblak AL, Gambetti P, Murrell JR. Early Onset And Rapid Course Of Alzheimer Disease Associated With The I143T Psen1 Mutation Alzheimers & Dementia. 10: 629. DOI: 10.1016/J.Jalz.2014.05.1095  0.601
2013 Zou WQ, Gambetti P, Xiao X, Yuan J, Langeveld J, Pirisinu L. Prions in variably protease-sensitive prionopathy: an update. Pathogens (Basel, Switzerland). 2: 457-71. PMID 25437202 DOI: 10.3390/Pathogens2030457  0.691
2013 Kim MO, Cali I, Oehler A, Fong JC, Wong K, See T, Katz JS, Gambetti P, Bettcher BM, Dearmond SJ, Geschwind MD. Genetic CJD with a novel E200G mutation in the prion protein gene and comparison with E200K mutation cases. Acta Neuropathologica Communications. 1: 80. PMID 24330864 DOI: 10.1186/2051-5960-1-80  0.653
2013 Kong Q, Mills JL, Kundu B, Li X, Qing L, Surewicz K, Cali I, Huang S, Zheng M, Swietnicki W, Sönnichsen FD, Gambetti P, Surewicz WK. Thermodynamic stabilization of the folded domain of prion protein inhibits prion infection in vivo. Cell Reports. 4: 248-54. PMID 23871665 DOI: 10.1016/J.Celrep.2013.06.030  0.789
2013 Pirisinu L, Nonno R, Esposito E, Benestad SL, Gambetti P, Agrimi U, Zou WQ. Small ruminant nor98 prions share biochemical features with human gerstmann-sträussler-scheinker disease and variably protease-sensitive prionopathy. Plos One. 8: e66405. PMID 23826096 DOI: 10.1371/Journal.Pone.0066405  0.668
2013 Xiao X, Yuan J, Haïk S, Cali I, Zhan Y, Moudjou M, Li B, Laplanche JL, Laude H, Langeveld J, Gambetti P, Kitamoto T, Kong Q, Brandel JP, Cobb BA, et al. Glycoform-selective prion formation in sporadic and familial forms of prion disease. Plos One. 8: e58786. PMID 23527023 DOI: 10.1371/Journal.Pone.0058786  0.834
2013 Xiao X, Cali I, Dong Z, Puoti G, Yuan J, Qing L, Wang H, Kong Q, Gambetti P, Zou WQ. Protease-sensitive prions with 144-bp insertion mutations. Aging. 5: 155-73. PMID 23515139  0.839
2013 Gambetti P. Creationism and Evolutionism in Prions American Journal of Pathology. 182: 623-627. PMID 23380581 DOI: 10.1016/J.Ajpath.2012.12.016  0.401
2013 Xiao X, Yuan J, Haïk S, Cali I, Zhan Y, Moudjou M, Li B, Laplanche J, Laude H, Langeveld J, Gambetti P, Kitamoto T, Kong Q, Brandel J, Cobb BA, et al. Correction: Glycoform-Selective Prion Formation in Sporadic and Familial Forms of Prion Disease Plos One. 8. DOI: 10.1371/Annotation/5391F30A-0875-4145-A1Ea-74Aedbbcd1E4  0.806
2012 Diack AB, Ritchie D, Bishop M, Pinion V, Brandel JP, Haik S, Tagliavini F, Van Duijn C, Belay ED, Gambetti P, Schonberger LB, Piccardo P, Will RG, Manson JC. Constant transmission properties of variant Creutzfeldt-Jakob disease in 5 countries. Emerging Infectious Diseases. 18: 1574-9. PMID 23017202 DOI: 10.3201/eid1810.120792  0.356
2012 Parchi P, de Boni L, Saverioni D, Cohen ML, Ferrer I, Gambetti P, Gelpi E, Giaccone G, Hauw JJ, Höftberger R, Ironside JW, Jansen C, Kovacs GG, Rozemuller A, Seilhean D, et al. Consensus classification of human prion disease histotypes allows reliable identification of molecular subtypes: an inter-rater study among surveillance centres in Europe and USA. Acta Neuropathologica. 124: 517-29. PMID 22744790 DOI: 10.1007/S00401-012-1002-8  0.754
2012 Puoti G, Bizzi A, Forloni G, Safar JG, Tagliavini F, Gambetti P. Sporadic human prion diseases: molecular insights and diagnosis. The Lancet. Neurology. 11: 618-28. PMID 22710755 DOI: 10.1016/S1474-4422(12)70063-7  0.785
2012 Notari S, Qing L, Pocchiari M, Dagdanova A, Hatcher K, Dogterom A, Groisman JF, Lumholtz IB, Puopolo M, Lasmezas C, Chen SG, Kong Q, Gambetti P. Assessing prion infectivity of human urine in sporadic Creutzfeldt-Jakob disease. Emerging Infectious Diseases. 18: 21-8. PMID 22260924 DOI: 10.3201/Eid1801.110589  0.818
2011 Chitravas N, Jung RS, Kofskey DM, Blevins JE, Gambetti P, Leigh RJ, Cohen ML. Treatable neurological disorders misdiagnosed as Creutzfeldt-Jakob disease. Annals of Neurology. 70: 437-44. PMID 21674591 DOI: 10.1002/ana.22454  0.617
2011 Gambetti P, Puoti G, Zou WQ. Variably protease-sensitive prionopathy: a novel disease of the prion protein. Journal of Molecular Neuroscience : Mn. 45: 422-4. PMID 21584652 DOI: 10.1007/S12031-011-9543-1  0.795
2011 Barria MA, Telling GC, Gambetti P, Mastrianni JA, Soto C. Generation of a new form of human PrP(Sc) in vitro by interspecies transmission from cervid prions. The Journal of Biological Chemistry. 286: 7490-5. PMID 21209079 DOI: 10.1074/Jbc.M110.198465  0.446
2011 Gambetti P, Cali I, Notari S, Kong Q, Zou WQ, Surewicz WK. Molecular biology and pathology of prion strains in sporadic human prion diseases. Acta Neuropathologica. 121: 79-90. PMID 21058033 DOI: 10.1007/S00401-010-0761-3  0.83
2011 Budka H, Head MW, Ironside JW, Gambetti P, Parchi P, Tagliavini F. Sporadic Creutzfeldt-Jakob Disease Neurodegeneration: the Molecular Pathology of Dementia and Movement Disorders: Second Edition. 322-335. DOI: 10.1002/9781444341256.Ch32  0.656
2010 Zou WQ, Puoti G, Xiao X, Yuan J, Qing L, Cali I, Shimoji M, Langeveld JP, Castellani R, Notari S, Crain B, Schmidt RE, Geschwind M, Dearmond SJ, Cairns NJ, ... ... Gambetti P, et al. Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. Annals of Neurology. 68: 162-72. PMID 20695009 DOI: 10.1002/Ana.22094  0.833
2010 Dagdanova A, Ilchenko S, Notari S, Yang Q, Obrenovich ME, Hatcher K, McAnulty P, Huang L, Zou W, Kong Q, Gambetti P, Chen SG. Characterization of the prion protein in human urine. The Journal of Biological Chemistry. 285: 30489-95. PMID 20670940 DOI: 10.1074/Jbc.M110.161794  0.823
2010 Kim JI, Cali I, Surewicz K, Kong Q, Raymond GJ, Atarashi R, Race B, Qing L, Gambetti P, Caughey B, Surewicz WK. Mammalian prions generated from bacterially expressed prion protein in the absence of any mammalian cofactors. The Journal of Biological Chemistry. 285: 14083-7. PMID 20304915 DOI: 10.1074/Jbc.C110.113464  0.784
2010 Notari S, Moleres FJ, Hunter SB, Belay ED, Schonberger LB, Cali I, Parchi P, Shieh WJ, Brown P, Zaki S, Zou WQ, Gambetti P. Multiorgan detection and characterization of protease-resistant prion protein in a case of variant CJD examined in the United States. Plos One. 5: e8765. PMID 20098730 DOI: 10.1371/Journal.Pone.0008765  0.83
2010 Ghoshal N, Cairns NJ, Puoti G, Gambetti P, Morris JC. P1-050: Protease-sensitive prionopathy in a cognitively normal 93-year-old Alzheimer's & Dementia. 6: S188-S188. DOI: 10.1016/J.Jalz.2010.05.597  0.599
2009 Kim JI, Surewicz K, Gambetti P, Surewicz WK. The role of glycophosphatidylinositol anchor in the amplification of the scrapie isoform of prion protein in vitro. Febs Letters. 583: 3671-5. PMID 19854187 DOI: 10.1016/J.Febslet.2009.10.049  0.406
2009 Ghoshal N, Cali I, Perrin RJ, Josephson SA, Sun N, Gambetti P, Morris JC. Codistribution of amyloid beta plaques and spongiform degeneration in familial Creutzfeldt-Jakob disease with the E200K-129M haplotype. Archives of Neurology. 66: 1240-6. PMID 19822779 DOI: 10.1001/Archneurol.2009.224  0.649
2009 Cali I, Castellani R, Alshekhlee A, Cohen Y, Blevins J, Yuan J, Langeveld JP, Parchi P, Safar JG, Zou WQ, Gambetti P. Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt-Jakob disease: its effect on the phenotype and prion-type characteristics. Brain : a Journal of Neurology. 132: 2643-58. PMID 19734292 DOI: 10.1093/Brain/Awp196  0.829
2009 Xiao X, Miravalle L, Yuan J, McGeehan J, Dong Z, Wyza R, MacLennan GT, Golichowski AM, Kneale G, King N, Kong Q, Spina S, Vidal R, Ghetti B, Roos K, ... Gambetti P, et al. Failure to detect the presence of prions in the uterine and gestational tissues from a Gravida with Creutzfeldt-Jakob disease. The American Journal of Pathology. 174: 1602-8. PMID 19349373 DOI: 10.2353/Ajpath.2009.081045  0.757
2009 Zou WQ, Gambetti P. Variant Creutzfeldt-Jakob disease: French versus British. Annals of Neurology. 65: 233-5. PMID 19334065 DOI: 10.1002/ana.21637  0.662
2008 Provini F, Cortelli P, Montagna P, Gambetti P, Lugaresi E. Fatal insomnia and agrypnia excitata: sleep and the limbic system. Revue Neurologique. 164: 692-700. PMID 18805303 DOI: 10.1016/J.Neurol.2007.11.003  0.499
2008 Castilla J, Morales R, Saá P, Barria M, Gambetti P, Soto C. Cell-free propagation of prion strains. The Embo Journal. 27: 2557-66. PMID 18800058 DOI: 10.1038/Emboj.2008.181  0.41
2008 Notari S, Strammiello R, Capellari S, Giese A, Cescatti M, Grassi J, Ghetti B, Langeveld JP, Zou WQ, Gambetti P, Kretzschmar HA, Parchi P. Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease. The Journal of Biological Chemistry. 283: 30557-65. PMID 18753138 DOI: 10.1074/Jbc.M801877200  0.84
2008 Mehta LR, Huddleston BJ, Skalabrin EJ, Burns JB, Zou WQ, Gambetti P, Chin SS. Sporadic fatal insomnia masquerading as a paraneoplastic cerebellar syndrome. Archives of Neurology. 65: 971-3. PMID 18625868 DOI: 10.1001/Archneur.65.7.971  0.627
2008 Gambetti P, Dong Z, Yuan J, Xiao X, Zheng M, Alshekhlee A, Castellani R, Cohen M, Barria MA, Gonzalez-Romero D, Belay ED, Schonberger LB, Marder K, Harris C, Burke JR, et al. A novel human disease with abnormal prion protein sensitive to protease. Annals of Neurology. 63: 697-708. PMID 18571782 DOI: 10.1002/Ana.21420  0.852
2008 Kong Q, Zheng M, Casalone C, Qing L, Huang S, Chakraborty B, Wang P, Chen F, Cali I, Corona C, Martucci F, Iulini B, Acutis P, Wang L, Liang J, ... ... Gambetti P, et al. Evaluation of the human transmission risk of an atypical bovine spongiform encephalopathy prion strain. Journal of Virology. 82: 3697-701. PMID 18234793 DOI: 10.1128/Jvi.02561-07  0.805
2008 Yuan J, Dong Z, Guo JP, McGeehan J, Xiao X, Wang J, Cali I, McGeer PL, Cashman NR, Bessen R, Surewicz WK, Kneale G, Petersen RB, Gambetti P, Zou WQ. Accessibility of a critical prion protein region involved in strain recognition and its implications for the early detection of prions. Cellular and Molecular Life Sciences : Cmls. 65: 631-43. PMID 18193391 DOI: 10.1007/S00018-007-7478-Z  0.789
2008 Ghoshal N, Perrin RJ, Josephson SA, Sun NA, Clark CM, Cali I, Gambetti P, Morris JC. P2-207: Co-distribution of Aβ plaques and spongiform degeneration in familial Creutzfeldt-Jakob disease with E200K-129M haplotype Alzheimer's & Dementia. 4: T431-T432. DOI: 10.1016/J.Jalz.2008.05.1282  0.617
2007 Lefebvre-Roque M, Kremmer E, Gilch S, Zou WQ, Féraudet C, Gilles CM, Salès N, Grassi J, Gambetti P, Baron T, Schätzl H, Lasmézas CI. Toxic effects of intracerebral PrP antibody administration during the course of BSE infection in mice. Prion. 1: 198-206. PMID 19164902 DOI: 10.4161/Pri.1.3.4870  0.551
2007 Zou WQ, Gambetti P. Prion: the chameleon protein. Cellular and Molecular Life Sciences : Cmls. 64: 3266-70. PMID 17965827 DOI: 10.1007/S00018-007-7380-8  0.67
2007 Notari S, Capellari S, Langeveld J, Giese A, Strammiello R, Gambetti P, Kretzschmar HA, Parchi P. A refined method for molecular typing reveals that co-occurrence of PrP(Sc) types in Creutzfeldt-Jakob disease is not the rule. Laboratory Investigation; a Journal of Technical Methods and Pathology. 87: 1103-12. PMID 17893675 DOI: 10.1038/Labinvest.3700676  0.801
2007 Huang S, Liang J, Zheng M, Li X, Wang M, Wang P, Vanegas D, Wu D, Chakraborty B, Hays AP, Chen K, Chen SG, Booth S, Cohen M, Gambetti P, et al. Inducible overexpression of wild-type prion protein in the muscles leads to a primary myopathy in transgenic mice. Proceedings of the National Academy of Sciences of the United States of America. 104: 6800-5. PMID 17420473 DOI: 10.1073/Pnas.0608885104  0.752
2007 Allen CT, Sonnen J, Leslie MJ, Kidoguchi L, Harris C, Gambetti P, Montine TJ. Washington statewide pathology surveillance for prion disease. Annals of Neurology. 61: 371-2. PMID 17358023 DOI: 10.1002/Ana.21096  0.443
2006 Hatcher K, Harris C, Gambetti P, Chen SG. Advances in Prion Disease Surveillance. Advances in Clinical Chemistry. 41: 263-292. PMID 28682752 DOI: 10.1016/S0065-2423(05)41008-2  0.544
2006 Yuan J, Xiao X, McGeehan J, Dong Z, Cali I, Fujioka H, Kong Q, Kneale G, Gambetti P, Zou WQ. Insoluble aggregates and protease-resistant conformers of prion protein in uninfected human brains. The Journal of Biological Chemistry. 281: 34848-58. PMID 16987816 DOI: 10.1074/Jbc.M602238200  0.804
2006 Cali I, Castellani R, Yuan J, Al-Shekhlee A, Cohen ML, Xiao X, Moleres FJ, Parchi P, Zou WQ, Gambetti P. Classification of sporadic Creutzfeldt-Jakob disease revisited. Brain : a Journal of Neurology. 129: 2266-77. PMID 16923954 DOI: 10.1093/Brain/Awl224  0.816
2006 Tabaton M, Gambetti P. Soluble amyloid-beta in the brain: the scarlet pimpernel. Journal of Alzheimer's Disease : Jad. 9: 127-32. PMID 16914851 DOI: 10.3233/Jad-2006-9S315  0.579
2006 Colucci M, Moleres FJ, Xie ZL, Ray-Chaudhury A, Gutti S, Butefisch CM, Cervenakova L, Wang W, Goldfarb LG, Kong Q, Ghetti B, Chen SG, Gambetti P. Gerstmann-Sträussler-Scheinker: a new phenotype with 'curly' PrP deposits. Journal of Neuropathology and Experimental Neurology. 65: 642-51. PMID 16825951 DOI: 10.1097/01.Jnen.0000228198.81797.4D  0.791
2006 Cortelli P, Perani D, Montagna P, Gallassi R, Tinuper P, Provini F, Federica P, Avoni P, Ferrillo F, Anchisi D, Moresco RM, Fazio F, Parchi P, Baruzzi A, Lugaresi E, ... Gambetti P, et al. Pre-symptomatic diagnosis in fatal familial insomnia: serial neurophysiological and 18FDG-PET studies. Brain : a Journal of Neurology. 129: 668-75. PMID 16399807 DOI: 10.1093/Brain/Awl003  0.678
2006 Xie Z, O'Rourke KI, Dong Z, Jenny AL, Langenberg JA, Belay ED, Schonberger LB, Petersen RB, Zou W, Kong Q, Gambetti P, Chen SG. Chronic wasting disease of elk and deer and Creutzfeldt-Jakob disease: comparative analysis of the scrapie prion protein. The Journal of Biological Chemistry. 281: 4199-206. PMID 16338930 DOI: 10.1074/Jbc.M509052200  0.843
2005 Pastore M, Chin SS, Bell KL, Dong Z, Yang Q, Yang L, Yuan J, Chen SG, Gambetti P, Zou WQ. Creutzfeldt-Jakob disease (CJD) with a mutation at codon 148 of prion protein gene: relationship with sporadic CJD. The American Journal of Pathology. 167: 1729-38. PMID 16314483 DOI: 10.1016/S0002-9440(10)61254-0  0.772
2005 Belay ED, Sejvar JJ, Shieh WJ, Wiersma ST, Zou WQ, Gambetti P, Hunter S, Maddox RA, Crockett L, Zaki SR, Schonberger LB. Variant Creutzfeldt-Jakob disease death, United States. Emerging Infectious Diseases. 11: 1351-4. PMID 16229761 DOI: 10.3201/eid1109.050371  0.559
2005 Kong Q, Huang S, Zou W, Vanegas D, Wang M, Wu D, Yuan J, Zheng M, Bai H, Deng H, Chen K, Jenny AL, O'Rourke K, Belay ED, Schonberger LB, ... ... Gambetti P, et al. Chronic wasting disease of elk: transmissibility to humans examined by transgenic mouse models. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 25: 7944-9. PMID 16135751 DOI: 10.1523/Jneurosci.2467-05.2005  0.813
2005 Piccini A, Russo C, Gliozzi A, Relini A, Vitali A, Borghi R, Giliberto L, Armirotti A, D'Arrigo C, Bachi A, Cattaneo A, Canale C, Torrassa S, Saido TC, Markesbery W, ... Gambetti P, et al. beta-amyloid is different in normal aging and in Alzheimer disease. The Journal of Biological Chemistry. 280: 34186-92. PMID 16103127 DOI: 10.1074/Jbc.M501694200  0.655
2005 Petersen RB, Siedlak SL, Lee HG, Kim YS, Nunomura A, Tagliavini F, Ghetti B, Cras P, Moreira PI, Castellani RJ, Guentchev M, Budka H, Ironside JW, Gambetti P, Smith MA, et al. Redox metals and oxidative abnormalities in human prion diseases. Acta Neuropathologica. 110: 232-8. PMID 16096758 DOI: 10.1007/S00401-005-1034-4  0.831
2005 Zaidi SI, Richardson SL, Capellari S, Song L, Smith MA, Ghetti B, Sy MS, Gambetti P, Petersen RB. Characterization of the F198S prion protein mutation: enhanced glycosylation and defective refolding. Journal of Alzheimer's Disease : Jad. 7: 159-71; discussion 1. PMID 15851854 DOI: 10.3233/Jad-2005-7209  0.731
2005 Zou WQ, Gambetti P. From microbes to prions the final proof of the prion hypothesis. Cell. 121: 155-7. PMID 15851020 DOI: 10.1016/j.cell.2005.04.002  0.621
2005 Pan T, Li R, Kang SC, Pastore M, Wong BS, Ironside J, Gambetti P, Sy MS. Biochemical fingerprints of prion diseases: scrapie prion protein in human prion diseases that share prion genotype and type. Journal of Neurochemistry. 92: 132-42. PMID 15606903 DOI: 10.1111/J.1471-4159.2004.02859.X  0.651
2005 Yuan J, Kinter M, McGeehan J, Perry G, Kneale G, Gambetti P, Zou WQ. Concealment of epitope by reduction and alkylation in prion protein. Biochemical and Biophysical Research Communications. 326: 652-9. PMID 15596149 DOI: 10.1016/j.bbrc.2004.11.088  0.666
2004 Mishra RS, Basu S, Gu Y, Luo X, Zou WQ, Mishra R, Li R, Chen SG, Gambetti P, Fujioka H, Singh N. Protease-resistant human prion protein and ferritin are cotransported across Caco-2 epithelial cells: implications for species barrier in prion uptake from the intestine. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 24: 11280-90. PMID 15601934 DOI: 10.1523/Jneurosci.2864-04.2004  0.779
2004 Chrétien F, Le Pavec G, Vallat-Decouvelaere AV, Delisle MB, Uro-Coste E, Ironside JW, Gambetti P, Parchi P, Créminon C, Dormont D, Mikol J, Gray F, Gras G. Expression of excitatory amino acid transporter-1 (EAAT-1) in brain macrophages and microglia of patients with prion diseases. Journal of Neuropathology and Experimental Neurology. 63: 1058-71. PMID 15535133 DOI: 10.1093/Jnen/63.10.1058  0.596
2004 Sadowski M, Pankiewicz J, Scholtzova H, Tsai J, Li Y, Carp RI, Meeker HC, Gambetti P, Debnath M, Mathis CA, Shao L, Gan WB, Klunk WE, Wisniewski T. Targeting prion amyloid deposits in vivo. Journal of Neuropathology and Experimental Neurology. 63: 775-84. PMID 15290902 DOI: 10.1093/Jnen/63.7.775  0.4
2004 Belay ED, Maddox RA, Williams ES, Miller MW, Gambetti P, Schonberger LB. Chronic wasting disease and potential transmission to humans. Emerging Infectious Diseases. 10: 977-84. PMID 15207045 DOI: 10.3201/eid0905.020577  0.373
2004 Vitali A, Piccini A, Borghi R, Fornaro P, Siedlak SL, Smith MA, Gambetti P, Ghetti B, Tabaton M. Soluble amyloid beta-protein is increased in frontotemporal dementia with tau gene mutations. Journal of Alzheimer's Disease : Jad. 6: 45-51. PMID 15004327 DOI: 10.3233/Jad-2004-6106  0.603
2004 Notari S, Capellari S, Giese A, Westner I, Baruzzi A, Ghetti B, Gambetti P, Kretzschmar HA, Parchi P. Effects of different experimental conditions on the PrPSc core generated by protease digestion: implications for strain typing and molecular classification of CJD. The Journal of Biological Chemistry. 279: 16797-804. PMID 14754888 DOI: 10.1074/Jbc.M313220200  0.8
2004 Zou WQ, Zheng J, Gray DM, Gambetti P, Chen SG. Antibody to DNA detects scrapie but not normal prion protein. Proceedings of the National Academy of Sciences of the United States of America. 101: 1380-5. PMID 14734804 DOI: 10.1073/Pnas.0307825100  0.698
2004 Spacey SD, Pastore M, McGillivray B, Fleming J, Gambetti P, Feldman H. Fatal familial insomnia: the first account in a family of Chinese descent. Archives of Neurology. 61: 122-5. PMID 14732629 DOI: 10.1001/Archneur.61.1.122  0.592
2004 Kong Q, Surewicz WK, Petersen RB, Zou W, Chen SG, Gambetti P, Parchi P, Capellari S, Goldfarb L, Montagna P, Lugaresi E, Piccardo P, Ghetti B. 14 Inherited Prion Diseases Cold Spring Harbor Monograph Archive. 41: 673-775. DOI: 10.1101/087969693.41.673  0.809
2004 Piccini A, Vitali A, Borghi R, Giliberto L, Patrone E, D'Arrigo C, Saido T, Markesbery W, Gambetti P, Tabaton M. P1-167 Soluble abeta shows a different composition in normal aging and Alzheimer's disease Neurobiology of Aging. 25: S143. DOI: 10.1016/S0197-4580(04)80480-9  0.579
2004 Zou WQ, Gambetti P. Modeling of human prions and prion diseases in vitro and in vivo Drug Discovery Today: Disease Models. 1: 157-164. DOI: 10.1016/J.Ddmod.2004.09.011  0.638
2003 Gambetti P, Kong Q, Zou W, Parchi P, Chen SG. Sporadic and familial CJD: classification and characterisation. British Medical Bulletin. 66: 213-39. PMID 14522861 DOI: 10.1093/Bmb/66.1.213  0.82
2003 Zou WQ, Capellari S, Parchi P, Sy MS, Gambetti P, Chen SG. Identification of novel proteinase K-resistant C-terminal fragments of PrP in Creutzfeldt-Jakob disease. The Journal of Biological Chemistry. 278: 40429-36. PMID 12917418 DOI: 10.1074/Jbc.M308550200  0.808
2003 Montagna P, Gambetti P, Cortelli P, Lugaresi E. Familial and sporadic fatal insomnia. The Lancet. Neurology. 2: 167-76. PMID 12849238 DOI: 10.1016/S1474-4422(03)00323-5  0.56
2003 Gambetti P, Parchi P, Chen SG. Hereditary Creutzfeldt-Jakob disease and fatal familial insomnia. Clinics in Laboratory Medicine. 23: 43-64. PMID 12733424 DOI: 10.1016/S0272-2712(02)00065-3  0.717
2003 Korth C, Kaneko K, Groth D, Heye N, Telling G, Mastrianni J, Parchi P, Gambetti P, Will R, Ironside J, Heinrich C, Tremblay P, DeArmond SJ, Prusiner SB. Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proceedings of the National Academy of Sciences of the United States of America. 100: 4784-9. PMID 12684540 DOI: 10.1073/Pnas.2627989100  0.57
2003 Belay ED, Maddox RA, Gambetti P, Schonberger LB. Monitoring the occurrence of emerging forms of Creutzfeldt-Jakob disease in the United States. Neurology. 60: 176-181. PMID 12557850 DOI: 10.1212/01.Wnl.0000036913.87823.D6  0.414
2003 Zou W, Colucci M, Gambetti P, Chen SG. Characterization of prion proteins. Methods in Molecular Biology (Clifton, N.J.). 217: 305-14. PMID 12491943 DOI: 10.1385/1-59259-330-5:305  0.719
2002 Plazzi G, Montagna P, Beelke M, Nobili L, De Carli F, Cortelli P, Vandi S, Avoni P, Tinuper P, Gambetti P, Lugaresi E, Ferrillo F. Does the prion protein gene 129 codon polymorphism influence sleep? Evidence from a fatal familial insomnia kindred. Clinical Neurophysiology : Official Journal of the International Federation of Clinical Neurophysiology. 113: 1948-53. PMID 12464332 DOI: 10.1016/S1388-2457(02)00308-5  0.509
2002 Capellari S, Parchi P, Wolff BD, Campbell J, Atkinson R, Posey DM, Petersen RB, Gambetti P. Creutzfeldt-Jakob disease associated with a deletion of two repeats in the prion protein gene. Neurology. 59: 1628-30. PMID 12451210 DOI: 10.1212/01.Wnl.0000035533.86833.28  0.783
2002 Liu T, Li R, Pan T, Liu D, Petersen RB, Wong BS, Gambetti P, Sy MS. Intercellular transfer of the cellular prion protein. The Journal of Biological Chemistry. 277: 47671-8. PMID 12359724 DOI: 10.1074/Jbc.M207458200  0.572
2002 Dagvadorj A, Petersen RB, Lee HS, Cervenakova L, Shatunov A, Budka H, Brown P, Gambetti P, Goldfarb LG. Spontaneous mutations in the prion protein gene causing transmissible spongiform encephalopathy. Annals of Neurology. 52: 355-9. PMID 12205650 DOI: 10.1002/Ana.10267  0.585
2002 Sy MS, Gambetti P, Wong BS. Human prion diseases. The Medical Clinics of North America. 86: 551-71, vi-vii. PMID 12168559 DOI: 10.1016/S0025-7125(02)00004-4  0.433
2002 Chen SG, Gambetti P. A journey through the species barrier. Neuron. 34: 854-6. PMID 12086631 DOI: 10.1016/S0896-6273(02)00736-5  0.461
2002 Pan T, Li R, Wong BS, Liu T, Gambetti P, Sy MS. Heterogeneity of normal prion protein in two- dimensional immunoblot: presence of various glycosylated and truncated forms. Journal of Neurochemistry. 81: 1092-101. PMID 12065622 DOI: 10.1046/J.1471-4159.2002.00909.X  0.385
2002 Taratuto AL, Piccardo P, Reich EG, Chen SG, Sevlever G, Schultz M, Luzzi AA, Rugiero M, Abecasis G, Endelman M, Garcia AM, Capellari S, Xie Z, Lugaresi E, Gambetti P, et al. Insomnia associated with thalamic involvement in E200K Creutzfeldt-Jakob disease. Neurology. 58: 362-7. PMID 11839833 DOI: 10.1212/Wnl.58.3.362  0.756
2001 Gambetti P, Parchi P, Capellari S, Russo C, Tabaton M, Teller JK, Chen SG. Mechanisms of phenotypic heterogeneity in prion, Alzheimer and other conformational diseases. Journal of Alzheimer's Disease : Jad. 3: 87-95. PMID 12214077 DOI: 10.3233/Jad-2001-3113  0.839
2001 Wong BS, Brown DR, Pan T, Whiteman M, Liu T, Bu X, Li R, Gambetti P, Olesik J, Rubenstein R, Sy MS. Oxidative impairment in scrapie-infected mice is associated with brain metals perturbations and altered antioxidant activities. Journal of Neurochemistry. 79: 689-98. PMID 11701772 DOI: 10.1046/J.1471-4159.2001.00625.X  0.329
2001 Ferrillo F, Plazzi G, Nobili L, Beelke M, De Carli F, Cortelli P, Tinuper P, Avoni P, Vandi S, Gambetti P, Lugaresi E, Montagna P. Absence of sleep EEG markers in fatal familial insomnia healthy carriers: a spectral analysis study. Clinical Neurophysiology : Official Journal of the International Federation of Clinical Neurophysiology. 112: 1888-92. PMID 11595148 DOI: 10.1016/S1388-2457(01)00600-9  0.494
2001 Belay ED, Gambetti P, Schonberger LB, Parchi P, Lyon DR, Capellari S, McQuiston JH, Bradley K, Dowdle G, Crutcher JM, Nichols CR. Creutzfeldt-Jakob disease in unusually young patients who consumed venison. Archives of Neurology. 58: 1673-8. PMID 11594928 DOI: 10.1001/Archneur.58.10.1673  0.695
2001 Wong BS, Chen SG, Colucci M, Xie Z, Pan T, Liu T, Li R, Gambetti P, Sy MS, Brown DR. Aberrant metal binding by prion protein in human prion disease. Journal of Neurochemistry. 78: 1400-8. PMID 11579148 DOI: 10.1046/J.1471-4159.2001.00522.X  0.685
2001 Pan T, Colucci M, Wong BS, Li R, Liu T, Petersen RB, Chen S, Gambetti P, Sy MS. Novel differences between two human prion strains revealed by two-dimensional gel electrophoresis. The Journal of Biological Chemistry. 276: 37284-8. PMID 11489910 DOI: 10.1074/Jbc.M107358200  0.754
2001 Wong BS, Green AJ, Li R, Xie Z, Pan T, Liu T, Chen SG, Gambetti P, Sy MS. Absence of protease-resistant prion protein in the cerebrospinal fluid of Creutzfeldt-Jakob disease. The Journal of Pathology. 194: 9-14. PMID 11329135 DOI: 10.1002/Path.872  0.571
2001 Hannah EL, Belay ED, Gambetti P, Krause G, Parchi P, Capellari S, Hoffman RE, Schonberger LB. Creutzfeldt-Jakob disease after receipt of a previously unimplicated brand of dura mater graft. Neurology. 56: 1080-3. PMID 11320182 DOI: 10.1212/Wnl.56.8.1080  0.65
2001 Wong BS, Liu T, Paisley D, Li R, Pan T, Chen SG, Perry G, Petersen RB, Smith MA, Melton DW, Gambetti P, Brown DR, Sy MS. Induction of HO-1 and NOS in doppel-expressing mice devoid of PrP: implications for doppel function. Molecular and Cellular Neurosciences. 17: 768-75. PMID 11312611 DOI: 10.1006/Mcne.2001.0963  0.696
2001 Liu T, Li R, Wong BS, Liu D, Pan T, Petersen RB, Gambetti P, Sy MS. Normal cellular prion protein is preferentially expressed on subpopulations of murine hemopoietic cells. Journal of Immunology (Baltimore, Md. : 1950). 166: 3733-42. PMID 11238614 DOI: 10.4049/Jimmunol.166.6.3733  0.538
2001 Wong BS, Liu T, Li R, Pan T, Petersen RB, Smith MA, Gambetti P, Perry G, Manson JC, Brown DR, Sy MS. Increased levels of oxidative stress markers detected in the brains of mice devoid of prion protein. Journal of Neurochemistry. 76: 565-72. PMID 11208919 DOI: 10.1046/J.1471-4159.2001.00028.X  0.661
2001 Li R, Liu D, Zanusso G, Liu T, Fayen JD, Huang JH, Petersen RB, Gambetti P, Sy MS. The expression and potential function of cellular prion protein in human lymphocytes. Cellular Immunology. 207: 49-58. PMID 11161453 DOI: 10.1006/Cimm.2000.1751  0.701
2000 Wong BS, Vénien-Bryan C, Williamson RA, Burton DR, Gambetti P, Sy MS, Brown DR, Jones IM. Copper refolding of prion protein. Biochemical and Biophysical Research Communications. 276: 1217-24. PMID 11027613 DOI: 10.1006/BBRC.2000.3604  0.343
2000 Jin T, Gu Y, Zanusso G, Sy M, Kumar A, Cohen M, Gambetti P, Singh N. The chaperone protein BiP binds to a mutant prion protein and mediates its degradation by the proteasome. The Journal of Biological Chemistry. 275: 38699-704. PMID 10970892 DOI: 10.1074/Jbc.M005543200  0.83
2000 Li R, Liu T, Wong BS, Pan T, Morillas M, Swietnicki W, O'Rourke K, Gambetti P, Surewicz WK, Sy MS. Identification of an epitope in the C terminus of normal prion protein whose expression is modulated by binding events in the N terminus. Journal of Molecular Biology. 301: 567-73. PMID 10966770 DOI: 10.1006/Jmbi.2000.3986  0.328
2000 Wong BS, Pan T, Liu T, Li R, Petersen RB, Jones IM, Gambetti P, Brown DR, Sy MS. Prion disease: A loss of antioxidant function? Biochemical and Biophysical Research Communications. 275: 249-52. PMID 10964653 DOI: 10.1006/Bbrc.2000.3158  0.645
2000 Parchi P, Zou W, Wang W, Brown P, Capellari S, Ghetti B, Kopp N, Schulz-Schaeffer WJ, Kretzschmar HA, Head MW, Ironside JW, Gambetti P, Chen SG. Genetic influence on the structural variations of the abnormal prion protein. Proceedings of the National Academy of Sciences of the United States of America. 97: 10168-72. PMID 10963679 DOI: 10.1073/Pnas.97.18.10168  0.794
2000 Bütefisch CM, Gambetti P, Cervenakova L, Park KY, Hallett M, Goldfarb LG. Inherited prion encephalopathy associated with the novel PRNP H187R mutation: a clinical study. Neurology. 55: 517-22. PMID 10953183 DOI: 10.1212/WNL.55.4.517  0.362
2000 Capellari S, Parchi P, Russo CM, Sanford J, Sy MS, Gambetti P, Petersen RB. Effect of the E200K mutation on prion protein metabolism. Comparative study of a cell model and human brain. The American Journal of Pathology. 157: 613-22. PMID 10934164 DOI: 10.1016/S0002-9440(10)64572-5  0.815
2000 Wong BS, Pan T, Liu T, Li R, Gambetti P, Sy MS. Differential contribution of superoxide dismutase activity by prion protein in vivo. Biochemical and Biophysical Research Communications. 273: 136-9. PMID 10873575 DOI: 10.1006/Bbrc.2000.2911  0.365
2000 Parchi P, Capellari S, Gambetti P. Intracerebral distribution of the abnormal isoform of the prion protein in sporadic Creutzfeldt-Jakob disease and fatal insomnia. Microscopy Research and Technique. 50: 16-25. PMID 10871544 DOI: 10.1002/1097-0029(20000701)50:1<16::Aid-Jemt4>3.0.Co;2-Y  0.769
2000 Russo C, Schettini G, Saido TC, Hulette C, Lippa C, Lannfelt L, Ghetti B, Gambetti P, Tabaton M, Teller JK. Presenilin-1 mutations in Alzheimer's disease. Nature. 405: 531-2. PMID 10850703 DOI: 10.1038/35014735  0.763
2000 Brown DR, Iordanova IK, Wong BS, Vénien-Bryan C, Hafiz F, Glasssmith LL, Sy MS, Gambetti P, Jones IM, Clive C, Haswell SJ. Functional and structural differences between the prion protein from two alleles prnp(a) and prnp(b) of mouse. European Journal of Biochemistry / Febs. 267: 2452-9. PMID 10759872 DOI: 10.1046/J.1432-1327.2000.01275.X  0.41
2000 Swietnicki W, Morillas M, Chen SG, Gambetti P, Surewicz WK. Aggregation and fibrillization of the recombinant human prion protein huPrP90-231. Biochemistry. 39: 424-31. PMID 10631004 DOI: 10.1021/Bi991967M  0.514
2000 Wong B, Brown DR, Clive C, Haswell S, Sy M, Gambetti P, Williamson RA, Burton DR, Jones IM. Effect of copper on recombinant mouse prion protein Biochemical Society Transactions. 28: A36-A36. DOI: 10.1042/Bst028A036B  0.347
2000 Gambetti P. Human prion diseases Neurobiology of Aging. 21: 280. DOI: 10.1016/S0197-4580(00)83208-X  0.422
2000 Scaravilli F, Cordery RJ, Kretzschmar H, Gambetti P, Brink B, Fritz V, Temlett J, Kaplan C, Fish D, An SF, Schulz-Schaeffer WJ, Rossor MN. Sporadic fatal insomnia: A case study Annals of Neurology. 48: 665-669. DOI: 10.1002/1531-8249(200010)48:4<665::Aid-Ana15>3.0.Co;2-D  0.387
1999 Morillas M, Swietnicki W, Gambetti P, Surewicz WK. Membrane environment alters the conformational structure of the recombinant human prion protein. Journal of Biological Chemistry. 274: 36859-36865. PMID 10601237 DOI: 10.1074/Jbc.274.52.36859  0.322
1999 Xu X, Shi YC, Wu X, Gambetti P, Sui D, Cui MZ. Identification of a novel PSD-95/Dlg/ZO-1 (PDZ)-like protein interacting with the C terminus of presenilin-1. Journal of Biological Chemistry. 274: 32543-32546. PMID 10551805 DOI: 10.1074/Jbc.274.46.32543  0.334
1999 Worrall BB, Herman ST, Capellari S, Lynch T, Chin S, Gambetti P, Parchi P. Type 1 protease resistant prion protein and valine homozygosity at codon 129 of PRNP identify a subtype of sporadic Creutzfeldt-Jakob disease. Journal of Neurology, Neurosurgery, and Psychiatry. 67: 671-4. PMID 10519879 DOI: 10.1136/Jnnp.67.5.671  0.732
1999 Parchi P, Giese A, Capellari S, Brown P, Schulz-Schaeffer W, Windl O, Zerr I, Budka H, Kopp N, Piccardo P, Poser S, Rojiani A, Streichemberger N, Julien J, Vital C, ... ... Gambetti P, et al. Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Annals of Neurology. 46: 224-33. PMID 10443888 DOI: 10.1002/1531-8249(199908)46:2<224::Aid-Ana12>3.0.Co;2-W  0.746
1999 Zanusso G, Petersen RB, Jin T, Jing Y, Kanoush R, Ferrari S, Gambetti P, Singh N. Proteasomal degradation and N-terminal protease resistance of the codon 145 mutant prion protein. The Journal of Biological Chemistry. 274: 23396-404. PMID 10438517 DOI: 10.1074/Jbc.274.33.23396  0.821
1999 Cortelli P, Gambetti P, Montagna P, Lugaresi E. Fatal familial insomnia: clinical features and molecular genetics. Journal of Sleep Research. 8: 23-9. PMID 10389103 DOI: 10.1046/J.1365-2869.1999.00005.X  0.577
1999 Parchi P, Capellari S, Chin S, Schwarz HB, Schecter NP, Butts JD, Hudkins P, Burns DK, Powers JM, Gambetti P. A subtype of sporadic prion disease mimicking fatal familial insomnia. Neurology. 52: 1757-63. PMID 10371520 DOI: 10.1212/Wnl.52.9.1757  0.755
1999 Hainfellner JA, Parchi P, Kitamoto T, Jarius C, Gambetti P, Budka H. A novel phenotype in familial Creutzfeldt-Jakob disease: prion protein gene E200K mutation coupled with valine at codon 129 and type 2 protease-resistant prion protein. Annals of Neurology. 45: 812-6. PMID 10360778 DOI: 10.1002/1531-8249(199906)45:6<812::Aid-Ana20>3.0.Co;2-2  0.629
1999 Gambetti P, Parchi P. Insomnia in prion diseases: sporadic and familial. The New England Journal of Medicine. 340: 1675-7. PMID 10341282 DOI: 10.1056/Nejm199905273402111  0.573
1999 Gambetti P, Petersen RB, Parchi P, Chen SG, Capellari S, Goldfarb L, Gabizon R, Montagna P, Lugaresi E, Piccardo P, Ghetti B. 13 Inherited Prion Diseases Cold Spring Harbor Monograph Archive. 38: 509-583. DOI: 10.1101/087969547.38.509  0.809
1999 Gold M, Rojiani AM, Parchi P, Gambetti P, Gibbs CJ, Kenney K. SPORADIC CREUTZFELDT-JAKOB DISEASE (sCJD) - A SOUTHWEST FLORIDA EXPERIENCE Journal of Neuropathology and Experimental Neurology. 58: 552. DOI: 10.1097/00005072-199905000-00182  0.591
1999 Ghetti B, Gambetti P. Chapter 5 Human Prion Diseases Advances in Cell Aging and Gerontology. 3: 135-187. DOI: 10.1016/S1566-3124(08)60025-5  0.5
1998 Gambetti P, Russo C. Human brain amyloidoses Nephrology Dialysis Transplantation. 13: 33-40. PMID 9870435 DOI: 10.1093/Ndt/13.Suppl_7.33  0.581
1998 Russo C, Angelini G, Dapino D, Piccini A, Piombo G, Schettini G, Chen S, Teller JK, Zaccheo D, Gambetti P, Tabaton M. Opposite roles of apolipoprotein E in normal brains and in Alzheimer's disease. Proceedings of the National Academy of Sciences of the United States of America. 95: 15598-602. PMID 9861015 DOI: 10.1073/Pnas.95.26.15598  0.75
1998 Padovani A, D'Alessandro M, Parchi P, Cortelli P, Anzola GP, Montagna P, Vignolo LA, Petraroli R, Pocchiari M, Lugaresi E, Gambetti P. Fatal familial insomnia in a new Italian kindred. Neurology. 51: 1491-4. PMID 9818894 DOI: 10.1212/Wnl.51.5.1491  0.682
1998 Swietnicki W, Petersen RB, Gambetti P, Surewicz WK. Familial mutations and the thermodynamic stability of the recombinant human prion protein. The Journal of Biological Chemistry. 273: 31048-52. PMID 9813003 DOI: 10.1074/Jbc.273.47.31048  0.641
1998 Zanusso G, Liu D, Ferrari S, Hegyi I, Yin X, Aguzzi A, Hornemann S, Liemann S, Glockshuber R, Manson JC, Brown P, Petersen RB, Gambetti P, Sy MS. Prion protein expression in different species: analysis with a panel of new mAbs. Proceedings of the National Academy of Sciences of the United States of America. 95: 8812-6. PMID 9671761 DOI: 10.1073/Pnas.95.15.8812  0.741
1998 Gambetti P, Lugaresi E. Conclusions of the symposium. Brain Pathology (Zurich, Switzerland). 8: 571-5. PMID 9669714 DOI: 10.1111/J.1750-3639.1998.Tb00185.X  0.574
1998 Parchi P, Petersen RB, Chen SG, Autilio-Gambetti L, Capellari S, Monari L, Cortelli P, Montagna P, Lugaresi E, Gambetti P. Molecular pathology of fatal familial insomnia. Brain Pathology (Zurich, Switzerland). 8: 539-48. PMID 9669705 DOI: 10.1111/J.1750-3639.1998.Tb00176.X  0.827
1998 Dorandeu A, Wingertsmann L, Chrétien F, Delisle MB, Vital C, Parchi P, Montagna P, Lugaresi E, Ironside JW, Budka H, Gambetti P, Gray F. Neuronal apoptosis in fatal familial insomnia. Brain Pathology (Zurich, Switzerland). 8: 531-7. PMID 9669704 DOI: 10.1111/J.1750-3639.1998.Tb00175.X  0.647
1998 Lugaresi E, Tobler I, Gambetti P, Montagna P. The pathophysiology of fatal familial insomnia. Brain Pathology (Zurich, Switzerland). 8: 521-6. PMID 9669702 DOI: 10.1111/J.1750-3639.1998.Tb00173.X  0.47
1998 Montagna P, Cortelli P, Avoni P, Tinuper P, Plazzi G, Gallassi R, Portaluppi F, Julien J, Vital C, Delisle MB, Gambetti P, Lugaresi E. Clinical features of fatal familial insomnia: phenotypic variability in relation to a polymorphism at codon 129 of the prion protein gene. Brain Pathology (Zurich, Switzerland). 8: 515-20. PMID 9669701 DOI: 10.1111/J.1750-3639.1998.Tb00172.X  0.574
1998 Vital C, Gray F, Vital A, Parchi P, Capellari S, Petersen RB, Ferrer X, Jarnier D, Julien J, Gambetti P. Prion encephalopathy with insertion of octapeptide repeats: the number of repeats determines the type of cerebellar deposits. Neuropathology and Applied Neurobiology. 24: 125-30. PMID 9634208 DOI: 10.1046/J.1365-2990.1998.00098.X  0.745
1998 Smine A, Xu X, Nishiyama K, Katada T, Gambetti P, Yadav SP, Wu X, Shi Y, Yasuhara S, Homburger V, Okamoto T. Regulation of Brain G-protein Go by Alzheimer’s Disease Gene Presenilin-1 Journal of Biological Chemistry. 273: 16281-16288. PMID 9632688 DOI: 10.1074/Jbc.273.26.16281  0.339
1998 Welch WJ, Gambetti P. Chaperoning brain diseases Nature. 392: 23-24. PMID 9510241 DOI: 10.1038/32049  0.45
1998 Mizutani T, Inose T, Nakajima S, Kakimi S, Uchigata M, Ikeda K, Gambetti P, Takasu T. Familial parkinsonism and dementia with ballooned neurons, argyrophilic neuronal inclusions, atypical neurofibrillary tangles, tau-negative astrocytic fibrillary tangles, and Lewy bodies. Acta Neuropathologica. 95: 15-27. PMID 9452818 DOI: 10.1007/S004010050761  0.509
1997 Singh N, Zanusso G, Chen SG, Fujioka H, Richardson S, Gambetti P, Petersen RB. Prion protein aggregation reverted by low temperature in transfected cells carrying a prion protein gene mutation. The Journal of Biological Chemistry. 272: 28461-70. PMID 9353306 DOI: 10.1074/Jbc.272.45.28461  0.835
1997 Swietnicki W, Petersen R, Gambetti P, Surewicz WK. pH-dependent stability and conformation of the recombinant human prion protein PrP(90-231) Journal of Biological Chemistry. 272: 27517-27520. PMID 9346881 DOI: 10.1074/Jbc.272.44.27517  0.573
1997 Chen SG, Parchi P, Brown P, Capellari S, Zou W, Cochran EJ, Vnencak-Jones CL, Julien J, Vital C, Mikol J, Lugaresi E, Autilio-Gambetti L, Gambetti P. Allelic origin of the abnormal prion protein isoform in familial prion diseases. Nature Medicine. 3: 1009-15. PMID 9288728 DOI: 10.1038/Nm0997-1009  0.83
1997 Raymond GJ, Hope J, Kocisko DA, Priola SA, Raymond LD, Bossers A, Ironside J, Will RG, Chen SG, Petersen RB, Gambetti P, Rubenstein R, Smits MA, Lansbury PT, Caughey B. Molecular assessment of the potential transmissibilities of BSE and scrapie to humans. Nature. 388: 285-8. PMID 9230438 DOI: 10.1038/40876  0.684
1997 Russo C, Saido TC, DeBusk LM, Tabaton M, Gambetti P, Teller JK. Heterogeneity of water-soluble amyloid beta-peptide in Alzheimer's disease and Down's syndrome brains. Febs Letters. 409: 411-6. PMID 9224700 DOI: 10.1016/S0014-5793(97)00564-4  0.708
1997 Gambetti P. Prion in progressive subcortical gliosis revisited Neurology. 49: 309-310. PMID 9222220 DOI: 10.1212/Wnl.49.1.309-C  0.388
1997 Capellari S, Vital C, Parchi P, Petersen RB, Ferrer X, Jarnier D, Pegoraro E, Gambetti P, Julien J. Familial prion disease with a novel 144-bp insertion in the prion protein gene in a Basque family. Neurology. 49: 133-41. PMID 9222181 DOI: 10.1212/Wnl.49.1.133  0.8
1997 Cortelli P, Perani D, Parchi P, Grassi F, Montagna P, De Martin M, Castellani R, Tinuper P, Gambetti P, Lugaresi E, Fazio F. Cerebral metabolism in fatal familial insomnia: relation to duration, neuropathology, and distribution of protease-resistant prion protein. Neurology. 49: 126-33. PMID 9222180 DOI: 10.1212/Wnl.49.1.126  0.775
1997 Castellani RJ, Parchi P, Madoff L, Gambetti P, McKeever P. Biopsy diagnosis of Creutzfeldt-Jakob disease by western blot: a case report. Human Pathology. 28: 623-6. PMID 9158712 DOI: 10.1016/S0046-8177(97)90086-1  0.771
1996 Telling GC, Parchi P, DeArmond SJ, Cortelli P, Montagna P, Gabizon R, Mastrianni J, Lugaresi E, Gambetti P, Prusiner SB. Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science (New York, N.Y.). 274: 2079-82. PMID 8953038 DOI: 10.1126/Science.274.5295.2079  0.731
1996 Parchi P, Castellani R, Capellari S, Ghetti B, Young K, Chen SG, Farlow M, Dickson DW, Sima AA, Trojanowski JQ, Petersen RB, Gambetti P. Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Annals of Neurology. 39: 767-78. PMID 8651649 DOI: 10.1002/Ana.410390613  0.839
1996 Castellani R, Parchi P, Stahl J, Capellari S, Cohen M, Gambetti P. Early pathologic and biochemical changes in Creutzfeldt-Jakob disease: study of brain biopsies. Neurology. 46: 1690-3. PMID 8649571 DOI: 10.1212/Wnl.46.6.1690  0.785
1996 Petersen RB, Parchi P, Richardson SL, Urig CB, Gambetti P. Effect of the D178N mutation and the codon 129 polymorphism on the metabolism of the prion protein. The Journal of Biological Chemistry. 271: 12661-8. PMID 8647879 DOI: 10.1074/Jbc.271.21.12661  0.741
1996 LeBlanc AC, Xue R, Gambetti P. Amyloid precursor protein metabolism in primary cell cultures of neurons, astrocytes, and microglia Journal of Neurochemistry. 66: 2300-2310. PMID 8632152 DOI: 10.1046/J.1471-4159.1996.66062300.X  0.325
1996 Castellani R, Smith MA, Richey PL, Kalaria R, Gambetti P, Perry G. Evidence for oxidative stress in Pick disease and corticobasal degeneration. Brain Research. 696: 268-71. PMID 8574681 DOI: 10.1016/0006-8993(95)00535-X  0.562
1996 Gambetti P. Approaches to Prions: Prion Diseases. Science. 273: 1052-1053. DOI: 10.1126/Science.273.5278.1052B  0.421
1996 Parchi P, Petersen RB, Gambetti P. New topics in familial prion diseases Seminars in Virology. 7: 181-187. DOI: 10.1006/Smvy.1996.0023  0.748
1995 Montagna P, Cortelli P, Gambetti P, Lugaresi E. Fatal familial insomnia: sleep, neuroendocrine and vegetative alterations. Advances in Neuroimmunology. 5: 13-21. PMID 7795890 DOI: 10.1016/0960-5428(94)00042-M  0.492
1995 Gambetti P, Parchi P, Petersen RB, Chen SG, Lugaresi E. Fatal familial insomnia and familial Creutzfeldt-Jakob disease: clinical, pathological and molecular features. Brain Pathology (Zurich, Switzerland). 5: 43-51. PMID 7767490 DOI: 10.1111/J.1750-3639.1995.Tb00576.X  0.792
1995 Porialuppi F, Cortelli P, Avoni P, Vergnani L, Maltoni P, Pavani A, Sforza E, Manfredini R, Montagna P, Roiter I, Gambetti P, Fersini C, Lugaresi E. Dissociated 24-Hour patterns of somatotropin and prolactin in fatal familial insomnia Neuroendocrinology. 61: 731-737. PMID 7659197 DOI: 10.1159/000126901  0.492
1995 Créange A, Gray F, Cesaro P, Adle-Biassette H, Duvoux C, Cherqui D, Bell J, Parchi P, Gambetti P, Degos JD. Creutzfeldt-Jakob disease after liver transplantation. Annals of Neurology. 38: 269-72. PMID 7654078 DOI: 10.1002/Ana.410380223  0.577
1995 Chen SG, Teplow DB, Parchi P, Teller JK, Gambetti P, Autilio-Gambetti L. Truncated forms of the human prion protein in normal brain and in prion diseases. The Journal of Biological Chemistry. 270: 19173-80. PMID 7642585 DOI: 10.1074/Jbc.270.32.19173  0.809
1995 Parchi P, Gambetti P. Human prion diseases. Current Opinion in Neurology. 8: 286-93. PMID 7582044 DOI: 10.1097/00019052-199508000-00007  0.622
1995 Bethea CL, Hess DL, Widmann AA, Henningfeld JM, Kjær A, Knigge U, Warberg J, Mena F, Aguayo D, Pacheco P, Morales MT, Portaluppi F, Cortelli P, Avoni P, Vergnani L, ... ... Gambetti P, et al. Subject Index Vol. 61, 1995 Neuroendocrinology. 61: 741-742. DOI: 10.1159/000126905  0.444
1995 Bethea CL, Hess DL, Widmann AA, Henningfeld JM, Kjær A, Knigge U, Warberg J, Mena F, Aguayo D, Pacheco P, Morales MT, Portaluppi F, Cortelli P, Avoni P, Vergnani L, ... ... Gambetti P, et al. Contents, Vol. 61, 1995 Neuroendocrinology. 61. DOI: 10.1159/000126886  0.413
1995 Créange A, Gray F, Cesaro P, Bell J, Parchi P, Gambetti P, Degos J-. CREUTZFELDT-JAKOB DISEASE AFTER LIVER TRANSPLANT Journal of Neuropathology and Experimental Neurology. 54: 449. DOI: 10.1097/00005072-199505000-00168  0.508
1995 Petersen RB, Tresser NJ, Richardson SL, Gali M, Goren H, Gambetti P. A FAMILY WITH OCULOLEPTOMENINGEAL AMYLOIDOSIS AND DEMENTIA HAS A MUTATION IN THE TRANSTHYRETIN GENE Journal of Neuropathology and Experimental Neurology. 54: 413. DOI: 10.1097/00005072-199505000-00027  0.735
1994 Leblanc AC, Gambetti P. Production of Alzheimer 4-kDa β-Amyloid Peptide Requires the C-Terminal Cytosolic Domain of the Amyloid Precursor Protein Biochemical and Biophysical Research Communications. 204: 1371-1380. PMID 7980616 DOI: 10.1006/Bbrc.1994.2615  0.317
1994 Gray F, Chrétien F, Cesaro P, Chatelain J, Beaudry P, Laplanche JL, Mikol J, Bell J, Gambetti P, Degos JD. Creutzfeldt-Jakob disease and cerebral amyloid angiopathy. Acta Neuropathologica. 88: 106-11. PMID 7941967 DOI: 10.1007/Bf00294366  0.382
1994 Lanska DJ, Currier RD, Cohen M, Gambetti P, Smith EE, Bebin J, Jackson JF, Whitehouse PJ, Markesbery WR. Familial progressive subcortical gliosis. Neurology. 44: 1633-43. PMID 7936288 DOI: 10.1212/Wnl.44.9.1633  0.596
1994 Gambetti P. Structural lesions and their relationship to Alzheimer's disease Neurobiology of Aging. 15: 101-103. PMID 7700429 DOI: 10.1016/0197-4580(94)90183-X  0.334
1993 Perani D, Cortelli P, Lucignani G, Montagna P, Tinuper P, Gallassi R, Gambetti P, Lenzi GL, Lugaresi E, Fazio F. [18F]FDG PET in fatal familial insomnia: the functional effects of thalamic lesions. Neurology. 43: 2565-9. PMID 8255458 DOI: 10.1212/Wnl.43.12.2565  0.546
1993 LeBlanc A, Xue R, Gambetti P. Amyloid Protein Precursor (App) Expression And Metabolism In Human Nervous System Primary Cultures From Normal And Alzheimer Disease (Ad) Individuals Journal of Neuropathology and Experimental Neurology. 52: 333. DOI: 10.1097/00005072-199305000-00293  0.376
1993 Tabaton M, Cammarata S, Mandybur T, Richey P, Kawai M, Perry G, Gambetti P. Erratum: Senile plaques in cerebral amyloid angiopathy show accumulation of amyloid precursor protein without cytoskeletal abnormalities (Brain Research, 593: 299-303 (1992)) Brain Research. 600. DOI: 10.1016/0006-8993(93)90419-N  0.767
1992 Gallassi R, Morreale A, Montagna P, Gambetti P, Lugaresi E. "Fatal familial insomnia": neuropsychological study of a disease with thalamic degeneration. Cortex; a Journal Devoted to the Study of the Nervous System and Behavior. 28: 175-87. PMID 1499304 DOI: 10.1016/S0010-9452(13)80046-9  0.521
1992 Cohen M, Lanska D, Roessmann U, Karaman B, Ganz E, Whitehouse P, Gambetti P. Amyloidoma of the CNS. I. Clinical and pathologic study. Neurology. 42: 2019-23. PMID 1407586 DOI: 10.1212/Wnl.42.10.2019  0.709
1992 Montagna P, Cortelli P, Avoni P, Marchello LP, Monari L, Tinuper P, Gambetti P, Lugaresi E. Abnormal sympathetic skin responses in thalamic lesions. Electroencephalography and Clinical Neurophysiology. 85: 225-7. PMID 1376682 DOI: 10.1016/0168-5597(92)90137-Z  0.662
1991 LeBlanc AC, Chen HY, Autilio-Gambetti L, Gambetti P. Differential APP gene expression in rat cerebral cortex, meninges, and primary astroglial, microglial and neuronal cultures. Febs Letters. 292: 171-8. PMID 1959603 DOI: 10.1016/0014-5793(91)80861-V  0.61
1991 Bizzi A, Schaetzle B, Patton A, Gambetti P, Autilio-Gambetti L. Axonal transport of two major components of the ubiquitin system: free ubiquitin and ubiquitin carboxyl-terminal hydrolase PGP 9.5. Brain Research. 548: 292-9. PMID 1714333 DOI: 10.1016/0006-8993(91)91135-N  0.727
1991 Schiffer D, Autilio-Gambetti L, Chiò A, Gambetti P, Giordana MT, Gullotta F, Migheli A, Vigliani MC. Ubiquitin in motor neuron disease: study at the light and electron microscope. Journal of Neuropathology and Experimental Neurology. 50: 463-73. PMID 1648124 DOI: 10.1097/00005072-199107000-00007  0.649
1991 Perry G, Kawai M, Tabaton M, Onorato M, Mulvihill P, Richey P, Morandi A, Connolly J, Gambetti P. Neuropil threads of Alzheimer's disease show a marked alteration of the normal cytoskeleton The Journal of Neuroscience. 11: 1748-1755. DOI: 10.1523/Jneurosci.11-06-01748.1991  0.759
1990 Migheli A, Autilio-Gambetti L, Gambetti P, Mocellini C, Vigliani MC, Schiffer D. Ubiquitinated filamentous inclusions in spinal cord of patients with motor neuron disease. Neuroscience Letters. 114: 5-10. PMID 2166261 DOI: 10.1016/0304-3940(90)90419-A  0.625
1990 Schiffer D, Autilio-Gambetti L, Chio A, Gambetti P, Giordana MT, Gullotta F, Migheli A, Vigliani MC. Immunohistochemistry And Immunoelectron Microscopy Of Ubiquitin In Als: 49 Journal of Neuropathology and Experimental Neurology. 49: 277. DOI: 10.1097/00005072-199005000-00055  0.576
1989 Monaco S, Autilio-Gambetti L, Lasek RJ, Katz MJ, Gambetti P. Experimental increase of neurofilament transport rate: decreases in neurofilament number and in axon diameter. Journal of Neuropathology and Experimental Neurology. 48: 23-32. PMID 2908896 DOI: 10.1097/00005072-198901000-00003  0.657
1989 Tabaton M, Mandybur TI, Perry G, Onorato M, Autilio-Gambetti L, Gambetti P. The widespread alteration of neurites in Alzheimer's disease may be unrelated to amyloid deposition. Annals of Neurology. 26: 771-8. PMID 2557796 DOI: 10.1002/ana.410260614  0.768
1988 Tabaton M, Perry G, Autilio-Gambetti L, Manetto V, Gambetti P. Influence of neuronal location on antigenic properties of neurofibrillary tangles. Annals of Neurology. 23: 604-10. PMID 3408241 DOI: 10.1002/ana.410230613  0.775
1988 Perry G, Lipphardt S, Mulvihill P, Kancherla M, Mijares M, Gambetti P, Sharma S, Maggiora L, Cornette J, Lobl T. Amyloid precursor protein in senile plaques of Alzheimer disease. Lancet (London, England). 2: 746. PMID 2901596 DOI: 10.1016/S0140-6736(88)90219-X  0.608
1988 Manetto V, Perry G, Tabaton M, Mulvihill P, Fried VA, Smith HT, Gambetti P, Autilio-Gambetti L. Ubiquitin is associated with abnormal cytoplasmic filaments characteristic of neurodegenerative diseases. Proceedings of the National Academy of Sciences of the United States of America. 85: 4501-5. PMID 2837768 DOI: 10.1073/Pnas.85.12.4501  0.832
1988 Medori R, Autilio-Gambetti L, Jenich H, Gambetti P. Changes in axon size and slow axonal transport are related in experimental diabetic neuropathy. Neurology. 38: 597-601. PMID 2451191 DOI: 10.1212/Wnl.38.4.597  0.723
1988 Medori R, Jenich H, Autilio-Gambetti L, Gambetti P. Experimental diabetic neuropathy: similar changes of slow axonal transport and axonal size in different animal models. The Journal of Neuroscience. 8: 1814-1821. DOI: 10.1523/Jneurosci.08-05-01814.1988  0.725
1987 Perry G, Friedman R, Kang DH, Manetto V, Autilio-Gambetti L, Gambetti P. Antibodies to the neuronal cytoskeleton are elicited by Alzheimer paired helical filament fractions. Brain Research. 420: 233-42. PMID 3676758 DOI: 10.1016/0006-8993(87)91243-1  0.802
1987 Morandi A, Gambetti P, Arora PK, Sayre LM. Mechanism of neurotoxic action of beta,beta'-iminodipropionitrile (IDPN): N-hydroxylation enhances neurotoxic potency. Brain Research. 437: 69-76. PMID 3427483 DOI: 10.1016/0006-8993(87)91527-7  0.484
1987 Bertholf RL, Gambetti P. Aluminum and Alzheimer's disease: perspectives for a cytoskeletal mechanism. Critical Reviews in Clinical Laboratory Sciences. 25: 195-210. PMID 3315463 DOI: 10.3109/10408368709105882  0.432
1987 Galloway PG, Perry G, Kosik KS, Gambetti P. Hirano bodies contain tau protein. Brain Research. 403: 337-40. PMID 3103867 DOI: 10.1016/0006-8993(87)90071-0  0.766
1987 Galloway PG, Perry G, Gambetti P. Hirano body filaments contain actin and actin-associated proteins. Journal of Neuropathology and Experimental Neurology. 46: 185-99. PMID 3029338 DOI: 10.1097/00005072-198703000-00006  0.741
1987 Pappolla M, Penton R, Weiss HS, Miller CH, Sahenk Z, Autilio-Gambetti L, Gambetti P. Carbon disulfide axonopathy. Another experimental model characterized by acceleration of neurofilament transport and distinct changes of axonal size. Brain Research. 424: 272-80. PMID 2445451 DOI: 10.1016/0006-8993(87)91471-5  0.711
1987 Perry G, Mulvihill P, Manetto V, Autilio-Gambetti L, Gambetti P. Immunocytochemical properties of Alzheimer straight filaments The Journal of Neuroscience. 7: 3736-3738. DOI: 10.1523/Jneurosci.07-11-03736.1987  0.784
1987 Onorato M, Gambetti P, Kosik K, Perry G. ELECTRON MICROSCOPIC LOCALIZATION OF TAU IN ALZHEIMER NFT AND PHF. Journal of Neuropathology and Experimental Neurology. 46: 334. DOI: 10.1097/00005072-198705000-00013  0.489
1987 Galloway P, Perry G, Gambetti P. Hirano body filaments contain actin and actin-associated proteins Alzheimer Disease & Associated Disorders. 1: 207-208. DOI: 10.1097/00002093-198701030-00034  0.723
1986 Mitsumoto H, Gambetti P. Impaired slow axonal transport in wobbler mouse motor neuron disease Annals of Neurology. 19: 36-43. PMID 3947038 DOI: 10.1002/Ana.410190108  0.303
1986 Lugaresi E, Medori R, Montagna P, Baruzzi A, Cortelli P, Lugaresi A, Tinuper P, Zucconi M, Gambetti P. Fatal familial insomnia and dysautonomia with selective degeneration of thalamic nuclei. The New England Journal of Medicine. 315: 997-1003. PMID 3762620 DOI: 10.1056/Nejm198610163151605  0.711
1986 Perry G, Selkoe DJ, Block BR, Stewart D, Autilio-Gambetti L, Gambetti P. Electron microscopic localization of Alzheimer neurofibrillary tangle components recognized by an antiserum to paired helical filaments. Journal of Neuropathology and Experimental Neurology. 45: 161-8. PMID 2419516 DOI: 10.1097/00005072-198603000-00006  0.697
1986 Autilio-Gambetti L, Crane R, Gambetti P. Binding of Bodian's silver and monoclonal antibodies to defined regions of human neurofilament subunits: Bodian's silver reacts with a highly charged unique domain of neurofilaments. Journal of Neurochemistry. 46: 366-70. PMID 2416873 DOI: 10.1111/J.1471-4159.1986.Tb12977.X  0.588
1986 Gambetti P, Perry G, Autilio-Gambetti L. Paired helical filaments: Do they contain neurofilament epitopes? Neurobiology of Aging. 7: 451-452. DOI: 10.1016/0197-4580(86)90066-7  0.693
1985 Perry G, Rizzuto N, Autilio-Gambetti L, Gambetti P. Paired helical filaments from Alzheimer disease patients contain cytoskeletal components. Proceedings of the National Academy of Sciences of the United States of America. 82: 3916-20. PMID 3889918 DOI: 10.1097/00002093-198701030-00023  0.772
1985 Monaco S, Autilio-Gambetti L, Zabel D, Gambetti P. Giant axonal neuropathy: acceleration of neurofilament transport in optic axons. Proceedings of the National Academy of Sciences of the United States of America. 82: 920-4. PMID 2579382 DOI: 10.1073/Pnas.82.3.920  0.755
1985 Sayre LM, Autilio-Gambetti L, Gambetti P. Pathogenesis of experimental giant neurofilamentous axonopathies: a unified hypothesis based on chemical modification of neurofilaments. Brain Research. 357: 69-83. PMID 2412663 DOI: 10.1016/0165-0173(85)90008-6  0.615
1984 Pappolla M, Monaco S, Weiss H, Miller C, Sahenk Z, Autillo-Gambetti L, Gambetti P. 38 Slow Axonal Transport In Carbon Disulfide (Cs2) Giant Axonopathy Journal of Neuropathology and Experimental Neurology. 43: 305. DOI: 10.1097/00005072-198405000-00047  0.542
1983 Ghetti B, Gambetti P. Comparative immunocytochemical characterization of neurofibrillary tangles in experimental maytansine and aluminum encephalopathies Brain Research. 276: 388-393. PMID 6354362 DOI: 10.1016/0006-8993(83)90754-0  0.3
1983 Gambetti P, Shecket G, Ghetti B, Hirano A, Dahl D. Neurofibrillary changes in human brain. An immunocytochemical study with a neurofilament antiserum. Journal of Neuropathology and Experimental Neurology. 42: 69-79. PMID 6337236 DOI: 10.1097/00005072-198301000-00006  0.821
1983 Papasozomenos SC, Autilio-Gambetti L, Gambetti P. Distribution of proteins migrating with fast axonal transport. Their relationship to smooth endoplasmic reticulum. Brain Research. 278: 232-5. PMID 6196088 DOI: 10.1016/0006-8993(83)90243-3  0.77
1982 Velasco ME, Roessmann U, Gambetti P. The presence of glial fibrillary acidic protein in the human pituitary gland. Journal of Neuropathology and Experimental Neurology. 41: 150-63. PMID 7062085 DOI: 10.1097/00005072-198203000-00005  0.71
1982 Autilio-Gambetti L, Sipple J, Sudilovsky O, Gambetti P. Intermediate filaments of Schwann cells. Journal of Neurochemistry. 38: 774-80. PMID 7035618 DOI: 10.1111/j.1471-4159.1982.tb08698.x  0.596
1982 Papasozomenos SC, Yoon M, Crane R, Autilio-Gambetti L, Gambetti P. Redistribution of proteins of fast axonal transport following administration of beta,beta'-iminodipropionitrile: a quantitative autoradiographic study. The Journal of Cell Biology. 95: 672-5. PMID 6183280 DOI: 10.1083/jcb.95.2.672  0.767
1981 Papasozomenos SC, Autilio-Gambetti L, Gambetti P. Reorganization of axoplasmic organelles following beta, beta'-iminodipropionitrile administration. The Journal of Cell Biology. 91: 866-71. PMID 7199048 DOI: 10.1083/Jcb.91.3.866  0.76
1981 Autilio-Gambetti L, Velasco ME, Sipple J, Gambetti P. Immunochemical characterization of antisera to rat neurofilament subunits. Journal of Neurochemistry. 37: 1260-5. PMID 7028920 DOI: 10.1111/j.1471-4159.1981.tb04676.x  0.708
1981 Gambetti P, Autilio Gambetti L, Papasozomenos SC. Bodian's silver method stains neurofilament polypeptides. Science (New York, N.Y.). 213: 1521-2. PMID 6169146 DOI: 10.1126/Science.6169146  0.663
1980 Boller F, Mizutani T, Roessmann U, Gambetti P. Parkinson disease, dementia, and Alzheimer disease: clinicopathological correlations. Annals of Neurology. 7: 329-35. PMID 7377758 DOI: 10.1002/Ana.410070408  0.628
1980 Roessmann U, Velasco ME, Sindely SD, Gambetti P. Glial fibrillary acidic protein (GFAP) in ependymal cells during development. An immunocytochemical study. Brain Research. 200: 13-21. PMID 6998542 DOI: 10.1016/0006-8993(80)91090-2  0.708
1980 Gambetti P, Roessmann U, Velasco ME. Immunofluorescence technique for rapid diagnosis of glial tumors. The American Journal of Surgical Pathology. 4: 277-80. PMID 6994513 DOI: 10.1097/00000478-198006000-00009  0.7
1980 Velasco ME, Dahl D, Roessmann U, Gambetti P. Immunohistochemical localization of glial fibrillary acidic protein in human glial neoplasms. Cancer. 45: 484-94. PMID 6243508 DOI: 10.1002/1097-0142(19800201)45:3<484::Aid-Cncr2820450312>3.0.Co;2-9  0.723
1980 Gambetti P, Autilio-Gambetti L, Peck K. Lack of glia-axon transfer of proteins in the normal optic system of goldfish. Brain Research. 200: 59-68. PMID 6158361 DOI: 10.1016/0006-8993(80)91094-X  0.601
1980 Papasozomenos S, Autilio-Gambetti L, Gambetti P. 129 Axonal Transport Of Dna During Regeneration Journal of Neuropathology and Experimental Neurology. 39: 380. DOI: 10.1097/00005072-198005000-00137  0.578
1977 Peck K, Gambetti P, Autilio-Gambetti L. Glio-Axonal Transfer Of Protein In Regenerating Goldfish Optic System: 96 Journal of Neuropathology and Experimental Neurology. 36: 622. DOI: 10.1097/00005072-197705000-00112  0.597
1974 Gonatas NK, Stieber A, Gonatas J, Gambetti P, Antoine JC, Avrameas S. Ultrastructural autoradiographic detection of intracellular immunoglobulins with iodinated Fab fragments of antibody. The combined use of ultrastructural autoradiography and peroxidase cytochemistry for the detection of two antigens (double labeling). The Journal of Histochemistry and Cytochemistry : Official Journal of the Histochemistry Society. 22: 999-1009. PMID 4427074 DOI: 10.1177/22.11.999  0.509
1971 Gambetti P, DiMauro S, Baker L. Nervous system in Pompe's disease. Ultrastructure and biochemistry. Journal of Neuropathology and Experimental Neurology. 30: 412-430. PMID 5284681 DOI: 10.1097/00005072-197107000-00008  0.386
1969 Gonatas NK, Gambetti P, Tucker SH, Evangelista I, Baird HW. Cytoplasmic inclusions in juvenile amaurotic idiocy. The Journal of Pediatrics. 75: 796-805. PMID 5347429 DOI: 10.1016/S0022-3476(69)80302-1  0.521
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