Year |
Citation |
Score |
2023 |
Venkatraghavan V, Pascuzzo R, Bron EE, Moscatelli M, Grisoli M, Pickens A, Cohen ML, Schonberger LB, Gambetti P, Appleby BS, Klein S, Bizzi A. A discriminative event-based model for subtype diagnosis of sporadic Creutzfeldt-Jakob disease using brain MRI. Alzheimer's & Dementia : the Journal of the Alzheimer's Association. PMID 36749840 DOI: 10.1002/alz.12939 |
0.692 |
|
2022 |
Baiardi S, Mammana A, Rossi M, Ladogana A, Carlà B, Gambetti P, Capellari S, Parchi P. Phenotypic Heterogeneity of Variably Protease-Sensitive Prionopathy: A Report of Three Cases Carrying Different Genotypes at Codon 129. Viruses. 14. PMID 35215959 DOI: 10.3390/v14020367 |
0.693 |
|
2021 |
Baiardi S, Rossi M, Mammana A, Appleby BS, Barria MA, Calì I, Gambetti P, Gelpi E, Giese A, Ghetti B, Herms J, Ladogana A, Mikol J, Pal S, Ritchie DL, et al. Phenotypic diversity of genetic Creutzfeldt-Jakob disease: a histo-molecular-based classification. Acta Neuropathologica. PMID 34324063 DOI: 10.1007/s00401-021-02350-y |
0.775 |
|
2021 |
Cali I, Espinosa JC, Nemani SK, Marin-Moreno A, Camacho MV, Aslam R, Kitamoto T, Appleby BS, Torres JM, Gambetti P. Two distinct conformers of PrP type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo. Acta Neuropathologica Communications. 9: 55. PMID 33766126 DOI: 10.1186/s40478-021-01132-7 |
0.549 |
|
2020 |
Bizzi A, Pascuzzo R, Blevins J, Moscatelli MEM, Grisoli M, Lodi R, Doniselli FM, Castelli G, Cohen ML, Stamm A, Schonberger LB, Appleby BS, Gambetti P. Subtype diagnosis of sporadic Creutzfeldt-Jakob disease with diffusion MRI. Annals of Neurology. PMID 33274461 DOI: 10.1002/ana.25983 |
0.691 |
|
2020 |
Jones E, Hummerich H, Viré E, Uphill J, Dimitriadis A, Speedy H, Campbell T, Norsworthy P, Quinn L, Whitfield J, Linehan J, Jaunmuktane Z, Brandner S, Jat P, Nihat A, ... ... Gambetti P, et al. Identification of novel risk loci and causal insights for sporadic Creutzfeldt-Jakob disease: a genome-wide association study. The Lancet. Neurology. 19: 840-848. PMID 32949544 DOI: 10.1016/S1474-4422(20)30273-8 |
0.686 |
|
2020 |
Nemani SK, Xiao X, Cali I, Cracco L, Puoti G, Nigro M, Lavrich J, Bharara Singh A, Appleby BS, Sim VL, Notari S, Surewicz WK, Gambetti P. A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease. Acta Neuropathologica Communications. 8: 85. PMID 32560672 DOI: 10.1186/S40478-020-00966-X |
0.832 |
|
2020 |
Pascuzzo R, Oxtoby NP, Young AL, Blevins J, Castelli G, Garbarino S, Cohen ML, Schonberger LB, Gambetti P, Appleby BS, Alexander DC, Bizzi A. Prion propagation estimated from brain diffusion MRI is subtype dependent in sporadic Creutzfeldt-Jakob disease. Acta Neuropathologica. PMID 32535770 DOI: 10.1007/S00401-020-02168-0 |
0.703 |
|
2020 |
Bizzi A, Pascuzzo R, Blevins J, Grisoli M, Lodi R, Moscatelli MEM, Castelli G, Cohen ML, Schonberger LB, Foutz A, Safar JG, Appleby BS, Gambetti P. Evaluation of a New Criterion for Detecting Prion Disease With Diffusion Magnetic Resonance Imaging. Jama Neurology. PMID 32478816 DOI: 10.1001/Jamaneurol.2020.1319 |
0.678 |
|
2020 |
Cali I, Puoti G, Smucny J, Curtiss PM, Cracco L, Kitamoto T, Occhipinti R, Cohen ML, Appleby BS, Gambetti P. Co-existence of PrP types 1 and 2 in sporadic Creutzfeldt-Jakob disease of the VV subgroup: phenotypic and prion protein characteristics. Scientific Reports. 10: 1503. PMID 32001774 DOI: 10.1038/S41598-020-58446-0 |
0.814 |
|
2019 |
Camacho MV, Telling G, Kong Q, Gambetti P, Notari S. Role of prion protein glycosylation in replication of human prions by protein misfolding cyclic amplification. Laboratory Investigation; a Journal of Technical Methods and Pathology. PMID 31249376 DOI: 10.1038/S41374-019-0282-1 |
0.822 |
|
2019 |
Cracco L, Xiao X, Nemani SK, Lavrich J, Cali I, Ghetti B, Notari S, Surewicz WK, Gambetti P. Gerstmann-Sträussler-Scheinker disease revisited: accumulation of covalently-linked multimers of internal prion protein fragments. Acta Neuropathologica Communications. 7: 1. PMID 31142381 DOI: 10.1186/S40478-019-0734-2 |
0.81 |
|
2019 |
Cali I, Lavrich J, Moda F, Kofskey D, Nemani SK, Appleby B, Tagliavini F, Soto C, Gambetti P, Notari S. PMCA-replicated PrP in urine of vCJD patients maintains infectivity and strain characteristics of brain PrP: Transmission study. Scientific Reports. 9: 5191. PMID 30914754 DOI: 10.1038/S41598-019-41694-0 |
0.815 |
|
2019 |
Wang Z, Manca M, Foutz A, Camacho MV, Raymond GJ, Race B, Orru CD, Yuan J, Shen P, Li B, Lang Y, Dang J, Adornato A, Williams K, Maurer NR, ... Gambetti P, et al. Publisher Correction: Early preclinical detection of prions in the skin of prion-infected animals. Nature Communications. 10: 640. PMID 30718499 DOI: 10.1038/S41467-019-08648-6 |
0.76 |
|
2019 |
Wang Z, Manca M, Foutz A, Camacho MV, Raymond GJ, Race B, Orru CD, Yuan J, Shen P, Li B, Lang Y, Dang J, Adornato A, Williams K, Maurer NR, ... Gambetti P, et al. Early preclinical detection of prions in the skin of prion-infected animals. Nature Communications. 10: 247. PMID 30651538 DOI: 10.1038/S41467-018-08130-9 |
0.774 |
|
2019 |
Nonno R, Notari S, Di Bari MA, Cali I, Pirisinu L, d'Agostino C, Cracco L, Kofskey D, Vanni I, Lavrich J, Parchi P, Agrimi U, Gambetti P. Variable Protease-Sensitive Prionopathy Transmission to Bank Voles. Emerging Infectious Diseases. 25: 73-81. PMID 30561322 DOI: 10.3201/Eid2501.180807 |
0.834 |
|
2018 |
Nemani SK, Notari S, Cali I, Alvarez VE, Kofskey D, Cohen M, Stern RA, Appleby B, Abrams J, Schonberger L, McKee A, Gambetti P. Co-occurrence of chronic traumatic encephalopathy and prion disease. Acta Neuropathologica Communications. 6: 140. PMID 30563563 DOI: 10.1186/S40478-018-0643-9 |
0.845 |
|
2018 |
Cali I, Mikhail F, Qin K, Gregory C, Solanki A, Martinez MC, Zhao L, Appleby B, Gambetti P, Norstrom E, Mastrianni JA. Impaired transmissibility of atypical prions from genetic CJD. Neurology. Genetics. 4: e253. PMID 30109268 DOI: 10.1212/Nxg.0000000000000253 |
0.615 |
|
2018 |
Cracco L, Appleby BS, Gambetti P. Fatal familial insomnia and sporadic fatal insomnia. Handbook of Clinical Neurology. 153: 271-299. PMID 29887141 DOI: 10.1016/B978-0-444-63945-5.00015-5 |
0.496 |
|
2018 |
Notari S, Appleby BS, Gambetti P. Variably protease-sensitive prionopathy. Handbook of Clinical Neurology. 153: 175-190. PMID 29887135 DOI: 10.1016/B978-0-444-63945-5.00010-6 |
0.77 |
|
2018 |
Cali I, Cohen ML, Haїk S, Parchi P, Giaccone G, Collins SJ, Kofskey D, Wang H, McLean CA, Brandel JP, Privat N, Sazdovitch V, Duyckaerts C, Kitamoto T, Belay ED, ... ... Gambetti P, et al. Iatrogenic Creutzfeldt-Jakob disease with Amyloid-β pathology: an international study. Acta Neuropathologica Communications. 6: 5. PMID 29310723 DOI: 10.1186/S40478-017-0503-Z |
0.784 |
|
2017 |
Mente KP, O'Donnell JK, Jones SE, Cohen ML, Thompson NR, Bizzi A, Gambetti P, Safar JG, Appleby BS. Fluorodeoxyglucose Positron Emission Tomography (FDG-PET) Correlation of Histopathology and MRI in Prion Disease. Alzheimer Disease and Associated Disorders. PMID 28121634 DOI: 10.1097/Wad.0000000000000188 |
0.701 |
|
2017 |
Cracco L, Notari S, Cali I, Sy MS, Chen SG, Cohen ML, Ghetti B, Appleby BS, Zou WQ, Caughey B, Safar JG, Gambetti P. Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type. Scientific Reports. 7: 38280. PMID 28091514 DOI: 10.1038/Srep38280 |
0.835 |
|
2016 |
Foutz A, Appleby BS, Hamlin C, Liu X, Yang S, Cohen Y, Chen W, Blevins J, Fausett C, Wang H, Gambetti P, Zhang S, Hughson A, Tatsuoka C, Schonberger LB, et al. Diagnostic and Prognostic Value of Human Prion Detection in Cerebrospinal Fluid. Annals of Neurology. PMID 27893164 DOI: 10.1002/Ana.24833 |
0.658 |
|
2016 |
Choi JK, Cali I, Surewicz K, Kong Q, Gambetti P, Surewicz WK. Amyloid fibrils from the N-terminal prion protein fragment are infectious. Proceedings of the National Academy of Sciences of the United States of America. PMID 27849581 DOI: 10.1073/Pnas.1610716113 |
0.786 |
|
2016 |
Coulthart MB, Geschwind MD, Qureshi S, Phielipp N, Demarsh A, Abrams JY, Belay E, Gambetti P, Jansen GH, Lang AE, Schonberger LB. A case cluster of variant Creutzfeldt-Jakob disease linked to the Kingdom of Saudi Arabia. Brain : a Journal of Neurology. 139: 2609-2616. PMID 27671029 DOI: 10.1093/Brain/Aww206 |
0.304 |
|
2016 |
Umeh CC, Kalakoti P, Greenberg MK, Notari S, Cohen Y, Gambetti P, Oblak AL, Ghetti B, Mari Z. Clinicopathological Correlates in a PRNP P102L Mutation Carrier with Rapidly Progressing Parkinsonism-dystonia. Movement Disorders Clinical Practice. 3: 355-358. PMID 27617269 DOI: 10.1002/Mdc3.12307 |
0.72 |
|
2016 |
Balendra R, Uphill J, Collinson C, Druyeh R, Adamson G, Hummerich H, Zerr I, Gambetti P, Collinge J, Mead S. Variants of PLCXD3 are not associated with variant or sporadic Creutzfeldt-Jakob disease in a large international study. Bmc Medical Genetics. 17: 28. PMID 27055460 DOI: 10.1186/S12881-016-0278-2 |
0.434 |
|
2016 |
Pirisinu L, Di Bari MA, D'Agostino C, Marcon S, Riccardi G, Poleggi A, Cohen ML, Appleby BS, Gambetti P, Ghetti B, Agrimi U, Nonno R. Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases. Scientific Reports. 6: 20443. PMID 26841849 DOI: 10.1038/Srep20443 |
0.707 |
|
2016 |
Minikel EV, Vallabh SM, Lek M, Estrada K, Samocha KE, Sathirapongsasuti JF, McLean CY, Tung JY, Yu LP, Gambetti P, Blevins J, Zhang S, Cohen Y, Chen W, Yamada M, et al. Quantifying prion disease penetrance using large population control cohorts. Science Translational Medicine. 8: 322ra9. PMID 26791950 DOI: 10.1126/Scitranslmed.Aad5169 |
0.73 |
|
2016 |
Ghetti B, Murrell JR, Richardson RM, Epperson F, Gambetti P, Oblak AL. P4-228: Neuronal Intracytoplasmic PrP Deposits in Dominantly Inherited Creutzfeldt-Jakob Disease Associated With the PRNP
E200K-129V Haplotype Alzheimer's & Dementia. 12: P1116-P1117. DOI: 10.1016/J.Jalz.2016.06.2320 |
0.36 |
|
2015 |
Orrú CD, Groveman BR, Raymond LD, Hughson AG, Nonno R, Zou W, Ghetti B, Gambetti P, Caughey B. Correction: Bank Vole Prion Protein As an Apparently Universal Substrate for RT-QuIC-Based Detection and Discrimination of Prion Strains. Plos Pathogens. 11: e1005117. PMID 26284358 DOI: 10.1371/Journal.Ppat.1005117 |
0.537 |
|
2015 |
Hudson G, Uphill J, Hummerich H, Blevins J, Gambetti P, Zerr I, Collinge J, Mead S, Chinnery PF. Inherited mtDNA variations are not strong risk factors in human prion disease. Neurobiology of Aging. 36: 2908.e1-3. PMID 26239179 DOI: 10.1016/J.Neurobiolaging.2015.07.005 |
0.339 |
|
2015 |
Cali I, Miller CJ, Parisi JE, Geschwind MD, Gambetti P, Schonberger LB. Distinct pathological phenotypes of Creutzfeldt-Jakob disease in recipients of prion-contaminated growth hormone. Acta Neuropathologica Communications. 3: 37. PMID 26108478 DOI: 10.1186/S40478-015-0214-2 |
0.684 |
|
2015 |
Orrú CD, Groveman BR, Raymond LD, Hughson AG, Nonno R, Zou W, Ghetti B, Gambetti P, Caughey B. Bank Vole Prion Protein As an Apparently Universal Substrate for RT-QuIC-Based Detection and Discrimination of Prion Strains. Plos Pathogens. 11: e1004983. PMID 26086786 DOI: 10.1371/Journal.Ppat.1004983 |
0.606 |
|
2015 |
Maheshwari A, Fischer M, Gambetti P, Parker A, Ram A, Soto C, Concha-Marambio L, Cohen Y, Belay ED, Maddox RA, Mead S, Goodman C, Kass JS, Schonberger LB, Hussein HM. Recent US Case of Variant Creutzfeldt-Jakob Disease-Global Implications. Emerging Infectious Diseases. 21: 750-9. PMID 25897712 DOI: 10.3201/Eid2105.142017 |
0.375 |
|
2015 |
Del Pilar-Morales EA, Cali I, Chapas J, Bertrán-Pasarell J, Puoti G, Gambetti P, Nobo U. Sporadic Creutzfeldt-Jakob disease in a native Puerto Rican patient. Puerto Rico Health Sciences Journal. 34: 40-3. PMID 25856877 |
0.781 |
|
2015 |
Figini M, Alexander DC, Redaelli V, Fasano F, Grisoli M, Baselli G, Gambetti P, Tagliavini F, Bizzi A. Mathematical models for the diffusion magnetic resonance signal abnormality in patients with prion diseases. Neuroimage. Clinical. 7: 142-54. PMID 25610776 DOI: 10.1016/J.Nicl.2014.11.017 |
0.565 |
|
2015 |
Ghoshal N, Perry A, McKeel D, Schmidt RE, Carter D, Norton J, Zou WQ, Xiao X, Puoti G, Notari S, Gambetti P, Morris JC, Cairns NJ. Variably Protease-sensitive Prionopathy in an Apparent Cognitively Normal 93-Year-Old. Alzheimer Disease and Associated Disorders. 29: 173-6. PMID 24845762 DOI: 10.1097/Wad.0000000000000049 |
0.762 |
|
2014 |
Xiao X, Yuan J, Qing L, Cali I, Mikol J, Delisle MB, Uro-Coste E, Zeng L, Abouelsaad M, Gazgalis D, Martinez MC, Wang GX, Brown P, Ironside JW, Gambetti P, et al. Comparative Study of Prions in Iatrogenic and Sporadic Creutzfeldt-Jakob Disease. Journal of Clinical & Cellular Immunology. 5. PMID 25419482 DOI: 10.4172/2155-9899.1000240 |
0.821 |
|
2014 |
Notari S, Xiao X, Espinosa JC, Cohen Y, Qing L, Aguilar-Calvo P, Kofskey D, Cali I, Cracco L, Kong Q, Torres JM, Zou W, Gambetti P. Transmission characteristics of variably protease-sensitive prionopathy. Emerging Infectious Diseases. 20: 2006-14. PMID 25418590 DOI: 10.3201/Eid2012.140548 |
0.842 |
|
2014 |
Slattery CF, Beck JA, Harper L, Adamson G, Abdi Z, Uphill J, Campbell T, Druyeh R, Mahoney CJ, Rohrer JD, Kenny J, Lowe J, Leung KK, Barnes J, Clegg SL, ... ... Gambetti P, et al. R47H TREM2 variant increases risk of typical early-onset Alzheimer's disease but not of prion or frontotemporal dementia. Alzheimer's & Dementia : the Journal of the Alzheimer's Association. 10: 602-608.e4. PMID 25160042 DOI: 10.1016/J.Jalz.2014.05.1751 |
0.353 |
|
2014 |
Moda F, Gambetti P, Notari S, Concha-Marambio L, Catania M, Park KW, Maderna E, Suardi S, Haïk S, Brandel JP, Ironside J, Knight R, Tagliavini F, Soto C. Prions in the urine of patients with variant Creutzfeldt-Jakob disease. The New England Journal of Medicine. 371: 530-9. PMID 25099577 DOI: 10.1056/Nejmoa1404401 |
0.749 |
|
2014 |
Cannon A, Bieniek KF, Lin WL, Notari S, Zou WQ, Gambetti P, Pedraza O, Graff-Radford NR, Ferman TJ, Dickson DW. Concurrent variably protease-sensitive prionopathy and amyotrophic lateral sclerosis. Acta Neuropathologica. 128: 313-5. PMID 24928712 DOI: 10.1007/S00401-014-1309-8 |
0.781 |
|
2014 |
Ghetti BF, Miller DC, Zou W, Cohen Y, Richardson R, Oblak AL, Gambetti P, Murrell JR. Early Onset And Rapid Course Of Alzheimer Disease Associated With The I143T Psen1 Mutation Alzheimers & Dementia. 10: 629. DOI: 10.1016/J.Jalz.2014.05.1095 |
0.601 |
|
2013 |
Zou WQ, Gambetti P, Xiao X, Yuan J, Langeveld J, Pirisinu L. Prions in variably protease-sensitive prionopathy: an update. Pathogens (Basel, Switzerland). 2: 457-71. PMID 25437202 DOI: 10.3390/Pathogens2030457 |
0.69 |
|
2013 |
Kim MO, Cali I, Oehler A, Fong JC, Wong K, See T, Katz JS, Gambetti P, Bettcher BM, Dearmond SJ, Geschwind MD. Genetic CJD with a novel E200G mutation in the prion protein gene and comparison with E200K mutation cases. Acta Neuropathologica Communications. 1: 80. PMID 24330864 DOI: 10.1186/2051-5960-1-80 |
0.654 |
|
2013 |
Kong Q, Mills JL, Kundu B, Li X, Qing L, Surewicz K, Cali I, Huang S, Zheng M, Swietnicki W, Sönnichsen FD, Gambetti P, Surewicz WK. Thermodynamic stabilization of the folded domain of prion protein inhibits prion infection in vivo. Cell Reports. 4: 248-54. PMID 23871665 DOI: 10.1016/J.Celrep.2013.06.030 |
0.789 |
|
2013 |
Pirisinu L, Nonno R, Esposito E, Benestad SL, Gambetti P, Agrimi U, Zou WQ. Small ruminant nor98 prions share biochemical features with human gerstmann-sträussler-scheinker disease and variably protease-sensitive prionopathy. Plos One. 8: e66405. PMID 23826096 DOI: 10.1371/Journal.Pone.0066405 |
0.667 |
|
2013 |
Xiao X, Yuan J, Haïk S, Cali I, Zhan Y, Moudjou M, Li B, Laplanche JL, Laude H, Langeveld J, Gambetti P, Kitamoto T, Kong Q, Brandel JP, Cobb BA, et al. Glycoform-selective prion formation in sporadic and familial forms of prion disease. Plos One. 8: e58786. PMID 23527023 DOI: 10.1371/Journal.Pone.0058786 |
0.834 |
|
2013 |
Xiao X, Cali I, Dong Z, Puoti G, Yuan J, Qing L, Wang H, Kong Q, Gambetti P, Zou WQ. Protease-sensitive prions with 144-bp insertion mutations. Aging. 5: 155-73. PMID 23515139 |
0.838 |
|
2013 |
Gambetti P. Creationism and Evolutionism in Prions American Journal of Pathology. 182: 623-627. PMID 23380581 DOI: 10.1016/J.Ajpath.2012.12.016 |
0.4 |
|
2013 |
Xiao X, Yuan J, Haïk S, Cali I, Zhan Y, Moudjou M, Li B, Laplanche J, Laude H, Langeveld J, Gambetti P, Kitamoto T, Kong Q, Brandel J, Cobb BA, et al. Correction: Glycoform-Selective Prion Formation in Sporadic and Familial Forms of Prion Disease Plos One. 8. DOI: 10.1371/Annotation/5391F30A-0875-4145-A1Ea-74Aedbbcd1E4 |
0.806 |
|
2012 |
Diack AB, Ritchie D, Bishop M, Pinion V, Brandel JP, Haik S, Tagliavini F, Van Duijn C, Belay ED, Gambetti P, Schonberger LB, Piccardo P, Will RG, Manson JC. Constant transmission properties of variant Creutzfeldt-Jakob disease in 5 countries. Emerging Infectious Diseases. 18: 1574-9. PMID 23017202 DOI: 10.3201/eid1810.120792 |
0.354 |
|
2012 |
Parchi P, de Boni L, Saverioni D, Cohen ML, Ferrer I, Gambetti P, Gelpi E, Giaccone G, Hauw JJ, Höftberger R, Ironside JW, Jansen C, Kovacs GG, Rozemuller A, Seilhean D, et al. Consensus classification of human prion disease histotypes allows reliable identification of molecular subtypes: an inter-rater study among surveillance centres in Europe and USA. Acta Neuropathologica. 124: 517-29. PMID 22744790 DOI: 10.1007/S00401-012-1002-8 |
0.754 |
|
2012 |
Puoti G, Bizzi A, Forloni G, Safar JG, Tagliavini F, Gambetti P. Sporadic human prion diseases: molecular insights and diagnosis. The Lancet. Neurology. 11: 618-28. PMID 22710755 DOI: 10.1016/S1474-4422(12)70063-7 |
0.785 |
|
2012 |
Notari S, Qing L, Pocchiari M, Dagdanova A, Hatcher K, Dogterom A, Groisman JF, Lumholtz IB, Puopolo M, Lasmezas C, Chen SG, Kong Q, Gambetti P. Assessing prion infectivity of human urine in sporadic Creutzfeldt-Jakob disease. Emerging Infectious Diseases. 18: 21-8. PMID 22260924 DOI: 10.3201/Eid1801.110589 |
0.819 |
|
2011 |
Chitravas N, Jung RS, Kofskey DM, Blevins JE, Gambetti P, Leigh RJ, Cohen ML. Treatable neurological disorders misdiagnosed as Creutzfeldt-Jakob disease. Annals of Neurology. 70: 437-44. PMID 21674591 DOI: 10.1002/ana.22454 |
0.618 |
|
2011 |
Gambetti P, Puoti G, Zou WQ. Variably protease-sensitive prionopathy: a novel disease of the prion protein. Journal of Molecular Neuroscience : Mn. 45: 422-4. PMID 21584652 DOI: 10.1007/S12031-011-9543-1 |
0.795 |
|
2011 |
Barria MA, Telling GC, Gambetti P, Mastrianni JA, Soto C. Generation of a new form of human PrP(Sc) in vitro by interspecies transmission from cervid prions. The Journal of Biological Chemistry. 286: 7490-5. PMID 21209079 DOI: 10.1074/Jbc.M110.198465 |
0.443 |
|
2011 |
Gambetti P, Cali I, Notari S, Kong Q, Zou WQ, Surewicz WK. Molecular biology and pathology of prion strains in sporadic human prion diseases. Acta Neuropathologica. 121: 79-90. PMID 21058033 DOI: 10.1007/S00401-010-0761-3 |
0.829 |
|
2011 |
Budka H, Head MW, Ironside JW, Gambetti P, Parchi P, Tagliavini F. Sporadic Creutzfeldt-Jakob Disease Neurodegeneration: the Molecular Pathology of Dementia and Movement Disorders: Second Edition. 322-335. DOI: 10.1002/9781444341256.Ch32 |
0.657 |
|
2010 |
Zou WQ, Puoti G, Xiao X, Yuan J, Qing L, Cali I, Shimoji M, Langeveld JP, Castellani R, Notari S, Crain B, Schmidt RE, Geschwind M, Dearmond SJ, Cairns NJ, ... ... Gambetti P, et al. Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. Annals of Neurology. 68: 162-72. PMID 20695009 DOI: 10.1002/Ana.22094 |
0.832 |
|
2010 |
Dagdanova A, Ilchenko S, Notari S, Yang Q, Obrenovich ME, Hatcher K, McAnulty P, Huang L, Zou W, Kong Q, Gambetti P, Chen SG. Characterization of the prion protein in human urine. The Journal of Biological Chemistry. 285: 30489-95. PMID 20670940 DOI: 10.1074/Jbc.M110.161794 |
0.822 |
|
2010 |
Kim JI, Cali I, Surewicz K, Kong Q, Raymond GJ, Atarashi R, Race B, Qing L, Gambetti P, Caughey B, Surewicz WK. Mammalian prions generated from bacterially expressed prion protein in the absence of any mammalian cofactors. The Journal of Biological Chemistry. 285: 14083-7. PMID 20304915 DOI: 10.1074/Jbc.C110.113464 |
0.784 |
|
2010 |
Notari S, Moleres FJ, Hunter SB, Belay ED, Schonberger LB, Cali I, Parchi P, Shieh WJ, Brown P, Zaki S, Zou WQ, Gambetti P. Multiorgan detection and characterization of protease-resistant prion protein in a case of variant CJD examined in the United States. Plos One. 5: e8765. PMID 20098730 DOI: 10.1371/Journal.Pone.0008765 |
0.83 |
|
2010 |
Ghoshal N, Cairns NJ, Puoti G, Gambetti P, Morris JC. P1-050: Protease-sensitive prionopathy in a cognitively normal 93-year-old Alzheimer's & Dementia. 6: S188-S188. DOI: 10.1016/J.Jalz.2010.05.597 |
0.601 |
|
2009 |
Kim JI, Surewicz K, Gambetti P, Surewicz WK. The role of glycophosphatidylinositol anchor in the amplification of the scrapie isoform of prion protein in vitro. Febs Letters. 583: 3671-5. PMID 19854187 DOI: 10.1016/J.Febslet.2009.10.049 |
0.405 |
|
2009 |
Ghoshal N, Cali I, Perrin RJ, Josephson SA, Sun N, Gambetti P, Morris JC. Codistribution of amyloid beta plaques and spongiform degeneration in familial Creutzfeldt-Jakob disease with the E200K-129M haplotype. Archives of Neurology. 66: 1240-6. PMID 19822779 DOI: 10.1001/Archneurol.2009.224 |
0.649 |
|
2009 |
Cali I, Castellani R, Alshekhlee A, Cohen Y, Blevins J, Yuan J, Langeveld JP, Parchi P, Safar JG, Zou WQ, Gambetti P. Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt-Jakob disease: its effect on the phenotype and prion-type characteristics. Brain : a Journal of Neurology. 132: 2643-58. PMID 19734292 DOI: 10.1093/Brain/Awp196 |
0.829 |
|
2009 |
Xiao X, Miravalle L, Yuan J, McGeehan J, Dong Z, Wyza R, MacLennan GT, Golichowski AM, Kneale G, King N, Kong Q, Spina S, Vidal R, Ghetti B, Roos K, ... Gambetti P, et al. Failure to detect the presence of prions in the uterine and gestational tissues from a Gravida with Creutzfeldt-Jakob disease. The American Journal of Pathology. 174: 1602-8. PMID 19349373 DOI: 10.2353/Ajpath.2009.081045 |
0.757 |
|
2009 |
Zou WQ, Gambetti P. Variant Creutzfeldt-Jakob disease: French versus British. Annals of Neurology. 65: 233-5. PMID 19334065 DOI: 10.1002/ana.21637 |
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2008 |
Provini F, Cortelli P, Montagna P, Gambetti P, Lugaresi E. Fatal insomnia and agrypnia excitata: sleep and the limbic system. Revue Neurologique. 164: 692-700. PMID 18805303 DOI: 10.1016/J.Neurol.2007.11.003 |
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2008 |
Castilla J, Morales R, Saá P, Barria M, Gambetti P, Soto C. Cell-free propagation of prion strains. The Embo Journal. 27: 2557-66. PMID 18800058 DOI: 10.1038/Emboj.2008.181 |
0.408 |
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2008 |
Notari S, Strammiello R, Capellari S, Giese A, Cescatti M, Grassi J, Ghetti B, Langeveld JP, Zou WQ, Gambetti P, Kretzschmar HA, Parchi P. Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease. The Journal of Biological Chemistry. 283: 30557-65. PMID 18753138 DOI: 10.1074/Jbc.M801877200 |
0.84 |
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2008 |
Mehta LR, Huddleston BJ, Skalabrin EJ, Burns JB, Zou WQ, Gambetti P, Chin SS. Sporadic fatal insomnia masquerading as a paraneoplastic cerebellar syndrome. Archives of Neurology. 65: 971-3. PMID 18625868 DOI: 10.1001/Archneur.65.7.971 |
0.626 |
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2008 |
Gambetti P, Dong Z, Yuan J, Xiao X, Zheng M, Alshekhlee A, Castellani R, Cohen M, Barria MA, Gonzalez-Romero D, Belay ED, Schonberger LB, Marder K, Harris C, Burke JR, et al. A novel human disease with abnormal prion protein sensitive to protease. Annals of Neurology. 63: 697-708. PMID 18571782 DOI: 10.1002/Ana.21420 |
0.852 |
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2008 |
Kong Q, Zheng M, Casalone C, Qing L, Huang S, Chakraborty B, Wang P, Chen F, Cali I, Corona C, Martucci F, Iulini B, Acutis P, Wang L, Liang J, ... ... Gambetti P, et al. Evaluation of the human transmission risk of an atypical bovine spongiform encephalopathy prion strain. Journal of Virology. 82: 3697-701. PMID 18234793 DOI: 10.1128/Jvi.02561-07 |
0.804 |
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2008 |
Yuan J, Dong Z, Guo JP, McGeehan J, Xiao X, Wang J, Cali I, McGeer PL, Cashman NR, Bessen R, Surewicz WK, Kneale G, Petersen RB, Gambetti P, Zou WQ. Accessibility of a critical prion protein region involved in strain recognition and its implications for the early detection of prions. Cellular and Molecular Life Sciences : Cmls. 65: 631-43. PMID 18193391 DOI: 10.1007/S00018-007-7478-Z |
0.789 |
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2008 |
Ghoshal N, Perrin RJ, Josephson SA, Sun NA, Clark CM, Cali I, Gambetti P, Morris JC. P2-207: Co-distribution of Aβ plaques and spongiform degeneration in familial Creutzfeldt-Jakob disease with E200K-129M haplotype Alzheimer's & Dementia. 4: T431-T432. DOI: 10.1016/J.Jalz.2008.05.1282 |
0.618 |
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2007 |
Lefebvre-Roque M, Kremmer E, Gilch S, Zou WQ, Féraudet C, Gilles CM, Salès N, Grassi J, Gambetti P, Baron T, Schätzl H, Lasmézas CI. Toxic effects of intracerebral PrP antibody administration during the course of BSE infection in mice. Prion. 1: 198-206. PMID 19164902 DOI: 10.4161/Pri.1.3.4870 |
0.551 |
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2007 |
Zou WQ, Gambetti P. Prion: the chameleon protein. Cellular and Molecular Life Sciences : Cmls. 64: 3266-70. PMID 17965827 DOI: 10.1007/S00018-007-7380-8 |
0.668 |
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2007 |
Notari S, Capellari S, Langeveld J, Giese A, Strammiello R, Gambetti P, Kretzschmar HA, Parchi P. A refined method for molecular typing reveals that co-occurrence of PrP(Sc) types in Creutzfeldt-Jakob disease is not the rule. Laboratory Investigation; a Journal of Technical Methods and Pathology. 87: 1103-12. PMID 17893675 DOI: 10.1038/Labinvest.3700676 |
0.803 |
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2007 |
Huang S, Liang J, Zheng M, Li X, Wang M, Wang P, Vanegas D, Wu D, Chakraborty B, Hays AP, Chen K, Chen SG, Booth S, Cohen M, Gambetti P, et al. Inducible overexpression of wild-type prion protein in the muscles leads to a primary myopathy in transgenic mice. Proceedings of the National Academy of Sciences of the United States of America. 104: 6800-5. PMID 17420473 DOI: 10.1073/Pnas.0608885104 |
0.753 |
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2007 |
Allen CT, Sonnen J, Leslie MJ, Kidoguchi L, Harris C, Gambetti P, Montine TJ. Washington statewide pathology surveillance for prion disease. Annals of Neurology. 61: 371-2. PMID 17358023 DOI: 10.1002/Ana.21096 |
0.442 |
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2006 |
Hatcher K, Harris C, Gambetti P, Chen SG. Advances in Prion Disease Surveillance. Advances in Clinical Chemistry. 41: 263-292. PMID 28682752 DOI: 10.1016/S0065-2423(05)41008-2 |
0.543 |
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2006 |
Yuan J, Xiao X, McGeehan J, Dong Z, Cali I, Fujioka H, Kong Q, Kneale G, Gambetti P, Zou WQ. Insoluble aggregates and protease-resistant conformers of prion protein in uninfected human brains. The Journal of Biological Chemistry. 281: 34848-58. PMID 16987816 DOI: 10.1074/Jbc.M602238200 |
0.805 |
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2006 |
Cali I, Castellani R, Yuan J, Al-Shekhlee A, Cohen ML, Xiao X, Moleres FJ, Parchi P, Zou WQ, Gambetti P. Classification of sporadic Creutzfeldt-Jakob disease revisited. Brain : a Journal of Neurology. 129: 2266-77. PMID 16923954 DOI: 10.1093/Brain/Awl224 |
0.815 |
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2006 |
Tabaton M, Gambetti P. Soluble amyloid-beta in the brain: the scarlet pimpernel. Journal of Alzheimer's Disease : Jad. 9: 127-32. PMID 16914851 DOI: 10.3233/Jad-2006-9S315 |
0.579 |
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2006 |
Colucci M, Moleres FJ, Xie ZL, Ray-Chaudhury A, Gutti S, Butefisch CM, Cervenakova L, Wang W, Goldfarb LG, Kong Q, Ghetti B, Chen SG, Gambetti P. Gerstmann-Sträussler-Scheinker: a new phenotype with 'curly' PrP deposits. Journal of Neuropathology and Experimental Neurology. 65: 642-51. PMID 16825951 DOI: 10.1097/01.Jnen.0000228198.81797.4D |
0.791 |
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2006 |
Cortelli P, Perani D, Montagna P, Gallassi R, Tinuper P, Provini F, Federica P, Avoni P, Ferrillo F, Anchisi D, Moresco RM, Fazio F, Parchi P, Baruzzi A, Lugaresi E, ... Gambetti P, et al. Pre-symptomatic diagnosis in fatal familial insomnia: serial neurophysiological and 18FDG-PET studies. Brain : a Journal of Neurology. 129: 668-75. PMID 16399807 DOI: 10.1093/Brain/Awl003 |
0.679 |
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2006 |
Xie Z, O'Rourke KI, Dong Z, Jenny AL, Langenberg JA, Belay ED, Schonberger LB, Petersen RB, Zou W, Kong Q, Gambetti P, Chen SG. Chronic wasting disease of elk and deer and Creutzfeldt-Jakob disease: comparative analysis of the scrapie prion protein. The Journal of Biological Chemistry. 281: 4199-206. PMID 16338930 DOI: 10.1074/Jbc.M509052200 |
0.842 |
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2005 |
Pastore M, Chin SS, Bell KL, Dong Z, Yang Q, Yang L, Yuan J, Chen SG, Gambetti P, Zou WQ. Creutzfeldt-Jakob disease (CJD) with a mutation at codon 148 of prion protein gene: relationship with sporadic CJD. The American Journal of Pathology. 167: 1729-38. PMID 16314483 DOI: 10.1016/S0002-9440(10)61254-0 |
0.773 |
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2005 |
Belay ED, Sejvar JJ, Shieh WJ, Wiersma ST, Zou WQ, Gambetti P, Hunter S, Maddox RA, Crockett L, Zaki SR, Schonberger LB. Variant Creutzfeldt-Jakob disease death, United States. Emerging Infectious Diseases. 11: 1351-4. PMID 16229761 DOI: 10.3201/eid1109.050371 |
0.559 |
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2005 |
Kong Q, Huang S, Zou W, Vanegas D, Wang M, Wu D, Yuan J, Zheng M, Bai H, Deng H, Chen K, Jenny AL, O'Rourke K, Belay ED, Schonberger LB, ... ... Gambetti P, et al. Chronic wasting disease of elk: transmissibility to humans examined by transgenic mouse models. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 25: 7944-9. PMID 16135751 DOI: 10.1523/Jneurosci.2467-05.2005 |
0.813 |
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2005 |
Piccini A, Russo C, Gliozzi A, Relini A, Vitali A, Borghi R, Giliberto L, Armirotti A, D'Arrigo C, Bachi A, Cattaneo A, Canale C, Torrassa S, Saido TC, Markesbery W, ... Gambetti P, et al. beta-amyloid is different in normal aging and in Alzheimer disease. The Journal of Biological Chemistry. 280: 34186-92. PMID 16103127 DOI: 10.1074/Jbc.M501694200 |
0.655 |
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2005 |
Petersen RB, Siedlak SL, Lee HG, Kim YS, Nunomura A, Tagliavini F, Ghetti B, Cras P, Moreira PI, Castellani RJ, Guentchev M, Budka H, Ironside JW, Gambetti P, Smith MA, et al. Redox metals and oxidative abnormalities in human prion diseases. Acta Neuropathologica. 110: 232-8. PMID 16096758 DOI: 10.1007/S00401-005-1034-4 |
0.831 |
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2005 |
Zaidi SI, Richardson SL, Capellari S, Song L, Smith MA, Ghetti B, Sy MS, Gambetti P, Petersen RB. Characterization of the F198S prion protein mutation: enhanced glycosylation and defective refolding. Journal of Alzheimer's Disease : Jad. 7: 159-71; discussion 1. PMID 15851854 DOI: 10.3233/Jad-2005-7209 |
0.732 |
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2005 |
Zou WQ, Gambetti P. From microbes to prions the final proof of the prion hypothesis. Cell. 121: 155-7. PMID 15851020 DOI: 10.1016/j.cell.2005.04.002 |
0.62 |
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2005 |
Pan T, Li R, Kang SC, Pastore M, Wong BS, Ironside J, Gambetti P, Sy MS. Biochemical fingerprints of prion diseases: scrapie prion protein in human prion diseases that share prion genotype and type. Journal of Neurochemistry. 92: 132-42. PMID 15606903 DOI: 10.1111/J.1471-4159.2004.02859.X |
0.652 |
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2005 |
Yuan J, Kinter M, McGeehan J, Perry G, Kneale G, Gambetti P, Zou WQ. Concealment of epitope by reduction and alkylation in prion protein. Biochemical and Biophysical Research Communications. 326: 652-9. PMID 15596149 DOI: 10.1016/j.bbrc.2004.11.088 |
0.666 |
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2004 |
Mishra RS, Basu S, Gu Y, Luo X, Zou WQ, Mishra R, Li R, Chen SG, Gambetti P, Fujioka H, Singh N. Protease-resistant human prion protein and ferritin are cotransported across Caco-2 epithelial cells: implications for species barrier in prion uptake from the intestine. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 24: 11280-90. PMID 15601934 DOI: 10.1523/Jneurosci.2864-04.2004 |
0.779 |
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2004 |
Chrétien F, Le Pavec G, Vallat-Decouvelaere AV, Delisle MB, Uro-Coste E, Ironside JW, Gambetti P, Parchi P, Créminon C, Dormont D, Mikol J, Gray F, Gras G. Expression of excitatory amino acid transporter-1 (EAAT-1) in brain macrophages and microglia of patients with prion diseases. Journal of Neuropathology and Experimental Neurology. 63: 1058-71. PMID 15535133 DOI: 10.1093/Jnen/63.10.1058 |
0.598 |
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2004 |
Sadowski M, Pankiewicz J, Scholtzova H, Tsai J, Li Y, Carp RI, Meeker HC, Gambetti P, Debnath M, Mathis CA, Shao L, Gan WB, Klunk WE, Wisniewski T. Targeting prion amyloid deposits in vivo. Journal of Neuropathology and Experimental Neurology. 63: 775-84. PMID 15290902 DOI: 10.1093/Jnen/63.7.775 |
0.398 |
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2004 |
Belay ED, Maddox RA, Williams ES, Miller MW, Gambetti P, Schonberger LB. Chronic wasting disease and potential transmission to humans. Emerging Infectious Diseases. 10: 977-84. PMID 15207045 DOI: 10.3201/eid0905.020577 |
0.37 |
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2004 |
Vitali A, Piccini A, Borghi R, Fornaro P, Siedlak SL, Smith MA, Gambetti P, Ghetti B, Tabaton M. Soluble amyloid beta-protein is increased in frontotemporal dementia with tau gene mutations. Journal of Alzheimer's Disease : Jad. 6: 45-51. PMID 15004327 DOI: 10.3233/Jad-2004-6106 |
0.603 |
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2004 |
Notari S, Capellari S, Giese A, Westner I, Baruzzi A, Ghetti B, Gambetti P, Kretzschmar HA, Parchi P. Effects of different experimental conditions on the PrPSc core generated by protease digestion: implications for strain typing and molecular classification of CJD. The Journal of Biological Chemistry. 279: 16797-804. PMID 14754888 DOI: 10.1074/Jbc.M313220200 |
0.802 |
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2004 |
Zou WQ, Zheng J, Gray DM, Gambetti P, Chen SG. Antibody to DNA detects scrapie but not normal prion protein. Proceedings of the National Academy of Sciences of the United States of America. 101: 1380-5. PMID 14734804 DOI: 10.1073/Pnas.0307825100 |
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2004 |
Spacey SD, Pastore M, McGillivray B, Fleming J, Gambetti P, Feldman H. Fatal familial insomnia: the first account in a family of Chinese descent. Archives of Neurology. 61: 122-5. PMID 14732629 DOI: 10.1001/Archneur.61.1.122 |
0.594 |
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2004 |
Kong Q, Surewicz WK, Petersen RB, Zou W, Chen SG, Gambetti P, Parchi P, Capellari S, Goldfarb L, Montagna P, Lugaresi E, Piccardo P, Ghetti B. 14 Inherited Prion Diseases Cold Spring Harbor Monograph Archive. 41: 673-775. DOI: 10.1101/087969693.41.673 |
0.808 |
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2004 |
Piccini A, Vitali A, Borghi R, Giliberto L, Patrone E, D'Arrigo C, Saido T, Markesbery W, Gambetti P, Tabaton M. P1-167 Soluble abeta shows a different composition in normal aging and Alzheimer's disease Neurobiology of Aging. 25: S143. DOI: 10.1016/S0197-4580(04)80480-9 |
0.579 |
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2004 |
Zou WQ, Gambetti P. Modeling of human prions and prion diseases in vitro and in vivo Drug Discovery Today: Disease Models. 1: 157-164. DOI: 10.1016/J.Ddmod.2004.09.011 |
0.637 |
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2003 |
Gambetti P, Kong Q, Zou W, Parchi P, Chen SG. Sporadic and familial CJD: classification and characterisation. British Medical Bulletin. 66: 213-39. PMID 14522861 DOI: 10.1093/Bmb/66.1.213 |
0.821 |
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2003 |
Zou WQ, Capellari S, Parchi P, Sy MS, Gambetti P, Chen SG. Identification of novel proteinase K-resistant C-terminal fragments of PrP in Creutzfeldt-Jakob disease. The Journal of Biological Chemistry. 278: 40429-36. PMID 12917418 DOI: 10.1074/Jbc.M308550200 |
0.809 |
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2003 |
Montagna P, Gambetti P, Cortelli P, Lugaresi E. Familial and sporadic fatal insomnia. The Lancet. Neurology. 2: 167-76. PMID 12849238 DOI: 10.1016/S1474-4422(03)00323-5 |
0.56 |
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2003 |
Gambetti P, Parchi P, Chen SG. Hereditary Creutzfeldt-Jakob disease and fatal familial insomnia. Clinics in Laboratory Medicine. 23: 43-64. PMID 12733424 DOI: 10.1016/S0272-2712(02)00065-3 |
0.718 |
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2003 |
Korth C, Kaneko K, Groth D, Heye N, Telling G, Mastrianni J, Parchi P, Gambetti P, Will R, Ironside J, Heinrich C, Tremblay P, DeArmond SJ, Prusiner SB. Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proceedings of the National Academy of Sciences of the United States of America. 100: 4784-9. PMID 12684540 DOI: 10.1073/Pnas.2627989100 |
0.571 |
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2003 |
Belay ED, Maddox RA, Gambetti P, Schonberger LB. Monitoring the occurrence of emerging forms of Creutzfeldt-Jakob disease in the United States. Neurology. 60: 176-181. PMID 12557850 DOI: 10.1212/01.Wnl.0000036913.87823.D6 |
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2003 |
Zou W, Colucci M, Gambetti P, Chen SG. Characterization of prion proteins. Methods in Molecular Biology (Clifton, N.J.). 217: 305-14. PMID 12491943 DOI: 10.1385/1-59259-330-5:305 |
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2002 |
Plazzi G, Montagna P, Beelke M, Nobili L, De Carli F, Cortelli P, Vandi S, Avoni P, Tinuper P, Gambetti P, Lugaresi E, Ferrillo F. Does the prion protein gene 129 codon polymorphism influence sleep? Evidence from a fatal familial insomnia kindred. Clinical Neurophysiology : Official Journal of the International Federation of Clinical Neurophysiology. 113: 1948-53. PMID 12464332 DOI: 10.1016/S1388-2457(02)00308-5 |
0.509 |
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2002 |
Capellari S, Parchi P, Wolff BD, Campbell J, Atkinson R, Posey DM, Petersen RB, Gambetti P. Creutzfeldt-Jakob disease associated with a deletion of two repeats in the prion protein gene. Neurology. 59: 1628-30. PMID 12451210 DOI: 10.1212/01.Wnl.0000035533.86833.28 |
0.784 |
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2002 |
Liu T, Li R, Pan T, Liu D, Petersen RB, Wong BS, Gambetti P, Sy MS. Intercellular transfer of the cellular prion protein. The Journal of Biological Chemistry. 277: 47671-8. PMID 12359724 DOI: 10.1074/Jbc.M207458200 |
0.572 |
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2002 |
Dagvadorj A, Petersen RB, Lee HS, Cervenakova L, Shatunov A, Budka H, Brown P, Gambetti P, Goldfarb LG. Spontaneous mutations in the prion protein gene causing transmissible spongiform encephalopathy. Annals of Neurology. 52: 355-9. PMID 12205650 DOI: 10.1002/Ana.10267 |
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2002 |
Sy MS, Gambetti P, Wong BS. Human prion diseases. The Medical Clinics of North America. 86: 551-71, vi-vii. PMID 12168559 DOI: 10.1016/S0025-7125(02)00004-4 |
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2002 |
Chen SG, Gambetti P. A journey through the species barrier. Neuron. 34: 854-6. PMID 12086631 DOI: 10.1016/S0896-6273(02)00736-5 |
0.462 |
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2002 |
Pan T, Li R, Wong BS, Liu T, Gambetti P, Sy MS. Heterogeneity of normal prion protein in two- dimensional immunoblot: presence of various glycosylated and truncated forms. Journal of Neurochemistry. 81: 1092-101. PMID 12065622 DOI: 10.1046/J.1471-4159.2002.00909.X |
0.385 |
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2002 |
Taratuto AL, Piccardo P, Reich EG, Chen SG, Sevlever G, Schultz M, Luzzi AA, Rugiero M, Abecasis G, Endelman M, Garcia AM, Capellari S, Xie Z, Lugaresi E, Gambetti P, et al. Insomnia associated with thalamic involvement in E200K Creutzfeldt-Jakob disease. Neurology. 58: 362-7. PMID 11839833 DOI: 10.1212/Wnl.58.3.362 |
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2001 |
Gambetti P, Parchi P, Capellari S, Russo C, Tabaton M, Teller JK, Chen SG. Mechanisms of phenotypic heterogeneity in prion, Alzheimer and other conformational diseases. Journal of Alzheimer's Disease : Jad. 3: 87-95. PMID 12214077 DOI: 10.3233/Jad-2001-3113 |
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2001 |
Wong BS, Brown DR, Pan T, Whiteman M, Liu T, Bu X, Li R, Gambetti P, Olesik J, Rubenstein R, Sy MS. Oxidative impairment in scrapie-infected mice is associated with brain metals perturbations and altered antioxidant activities. Journal of Neurochemistry. 79: 689-98. PMID 11701772 DOI: 10.1046/J.1471-4159.2001.00625.X |
0.329 |
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2001 |
Ferrillo F, Plazzi G, Nobili L, Beelke M, De Carli F, Cortelli P, Tinuper P, Avoni P, Vandi S, Gambetti P, Lugaresi E, Montagna P. Absence of sleep EEG markers in fatal familial insomnia healthy carriers: a spectral analysis study. Clinical Neurophysiology : Official Journal of the International Federation of Clinical Neurophysiology. 112: 1888-92. PMID 11595148 DOI: 10.1016/S1388-2457(01)00600-9 |
0.494 |
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2001 |
Belay ED, Gambetti P, Schonberger LB, Parchi P, Lyon DR, Capellari S, McQuiston JH, Bradley K, Dowdle G, Crutcher JM, Nichols CR. Creutzfeldt-Jakob disease in unusually young patients who consumed venison. Archives of Neurology. 58: 1673-8. PMID 11594928 DOI: 10.1001/Archneur.58.10.1673 |
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2001 |
Wong BS, Chen SG, Colucci M, Xie Z, Pan T, Liu T, Li R, Gambetti P, Sy MS, Brown DR. Aberrant metal binding by prion protein in human prion disease. Journal of Neurochemistry. 78: 1400-8. PMID 11579148 DOI: 10.1046/J.1471-4159.2001.00522.X |
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2001 |
Pan T, Colucci M, Wong BS, Li R, Liu T, Petersen RB, Chen S, Gambetti P, Sy MS. Novel differences between two human prion strains revealed by two-dimensional gel electrophoresis. The Journal of Biological Chemistry. 276: 37284-8. PMID 11489910 DOI: 10.1074/Jbc.M107358200 |
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2001 |
Wong BS, Green AJ, Li R, Xie Z, Pan T, Liu T, Chen SG, Gambetti P, Sy MS. Absence of protease-resistant prion protein in the cerebrospinal fluid of Creutzfeldt-Jakob disease. The Journal of Pathology. 194: 9-14. PMID 11329135 DOI: 10.1002/Path.872 |
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2001 |
Hannah EL, Belay ED, Gambetti P, Krause G, Parchi P, Capellari S, Hoffman RE, Schonberger LB. Creutzfeldt-Jakob disease after receipt of a previously unimplicated brand of dura mater graft. Neurology. 56: 1080-3. PMID 11320182 DOI: 10.1212/Wnl.56.8.1080 |
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2001 |
Wong BS, Liu T, Paisley D, Li R, Pan T, Chen SG, Perry G, Petersen RB, Smith MA, Melton DW, Gambetti P, Brown DR, Sy MS. Induction of HO-1 and NOS in doppel-expressing mice devoid of PrP: implications for doppel function. Molecular and Cellular Neurosciences. 17: 768-75. PMID 11312611 DOI: 10.1006/Mcne.2001.0963 |
0.696 |
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2001 |
Liu T, Li R, Wong BS, Liu D, Pan T, Petersen RB, Gambetti P, Sy MS. Normal cellular prion protein is preferentially expressed on subpopulations of murine hemopoietic cells. Journal of Immunology (Baltimore, Md. : 1950). 166: 3733-42. PMID 11238614 DOI: 10.4049/Jimmunol.166.6.3733 |
0.538 |
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2001 |
Wong BS, Liu T, Li R, Pan T, Petersen RB, Smith MA, Gambetti P, Perry G, Manson JC, Brown DR, Sy MS. Increased levels of oxidative stress markers detected in the brains of mice devoid of prion protein. Journal of Neurochemistry. 76: 565-72. PMID 11208919 DOI: 10.1046/J.1471-4159.2001.00028.X |
0.661 |
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2001 |
Li R, Liu D, Zanusso G, Liu T, Fayen JD, Huang JH, Petersen RB, Gambetti P, Sy MS. The expression and potential function of cellular prion protein in human lymphocytes. Cellular Immunology. 207: 49-58. PMID 11161453 DOI: 10.1006/Cimm.2000.1751 |
0.701 |
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2000 |
Wong BS, Vénien-Bryan C, Williamson RA, Burton DR, Gambetti P, Sy MS, Brown DR, Jones IM. Copper refolding of prion protein. Biochemical and Biophysical Research Communications. 276: 1217-24. PMID 11027613 DOI: 10.1006/BBRC.2000.3604 |
0.342 |
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2000 |
Jin T, Gu Y, Zanusso G, Sy M, Kumar A, Cohen M, Gambetti P, Singh N. The chaperone protein BiP binds to a mutant prion protein and mediates its degradation by the proteasome. The Journal of Biological Chemistry. 275: 38699-704. PMID 10970892 DOI: 10.1074/Jbc.M005543200 |
0.83 |
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2000 |
Li R, Liu T, Wong BS, Pan T, Morillas M, Swietnicki W, O'Rourke K, Gambetti P, Surewicz WK, Sy MS. Identification of an epitope in the C terminus of normal prion protein whose expression is modulated by binding events in the N terminus. Journal of Molecular Biology. 301: 567-73. PMID 10966770 DOI: 10.1006/Jmbi.2000.3986 |
0.328 |
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2000 |
Wong BS, Pan T, Liu T, Li R, Petersen RB, Jones IM, Gambetti P, Brown DR, Sy MS. Prion disease: A loss of antioxidant function? Biochemical and Biophysical Research Communications. 275: 249-52. PMID 10964653 DOI: 10.1006/Bbrc.2000.3158 |
0.644 |
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2000 |
Parchi P, Zou W, Wang W, Brown P, Capellari S, Ghetti B, Kopp N, Schulz-Schaeffer WJ, Kretzschmar HA, Head MW, Ironside JW, Gambetti P, Chen SG. Genetic influence on the structural variations of the abnormal prion protein. Proceedings of the National Academy of Sciences of the United States of America. 97: 10168-72. PMID 10963679 DOI: 10.1073/Pnas.97.18.10168 |
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2000 |
Bütefisch CM, Gambetti P, Cervenakova L, Park KY, Hallett M, Goldfarb LG. Inherited prion encephalopathy associated with the novel PRNP H187R mutation: a clinical study. Neurology. 55: 517-22. PMID 10953183 DOI: 10.1212/WNL.55.4.517 |
0.362 |
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2000 |
Capellari S, Parchi P, Russo CM, Sanford J, Sy MS, Gambetti P, Petersen RB. Effect of the E200K mutation on prion protein metabolism. Comparative study of a cell model and human brain. The American Journal of Pathology. 157: 613-22. PMID 10934164 DOI: 10.1016/S0002-9440(10)64572-5 |
0.816 |
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2000 |
Wong BS, Pan T, Liu T, Li R, Gambetti P, Sy MS. Differential contribution of superoxide dismutase activity by prion protein in vivo. Biochemical and Biophysical Research Communications. 273: 136-9. PMID 10873575 DOI: 10.1006/Bbrc.2000.2911 |
0.364 |
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2000 |
Parchi P, Capellari S, Gambetti P. Intracerebral distribution of the abnormal isoform of the prion protein in sporadic Creutzfeldt-Jakob disease and fatal insomnia. Microscopy Research and Technique. 50: 16-25. PMID 10871544 DOI: 10.1002/1097-0029(20000701)50:1<16::Aid-Jemt4>3.0.Co;2-Y |
0.77 |
|
2000 |
Russo C, Schettini G, Saido TC, Hulette C, Lippa C, Lannfelt L, Ghetti B, Gambetti P, Tabaton M, Teller JK. Presenilin-1 mutations in Alzheimer's disease. Nature. 405: 531-2. PMID 10850703 DOI: 10.1038/35014735 |
0.763 |
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2000 |
Brown DR, Iordanova IK, Wong BS, Vénien-Bryan C, Hafiz F, Glasssmith LL, Sy MS, Gambetti P, Jones IM, Clive C, Haswell SJ. Functional and structural differences between the prion protein from two alleles prnp(a) and prnp(b) of mouse. European Journal of Biochemistry / Febs. 267: 2452-9. PMID 10759872 DOI: 10.1046/J.1432-1327.2000.01275.X |
0.409 |
|
2000 |
Swietnicki W, Morillas M, Chen SG, Gambetti P, Surewicz WK. Aggregation and fibrillization of the recombinant human prion protein huPrP90-231. Biochemistry. 39: 424-31. PMID 10631004 DOI: 10.1021/Bi991967M |
0.514 |
|
2000 |
Wong B, Brown DR, Clive C, Haswell S, Sy M, Gambetti P, Williamson RA, Burton DR, Jones IM. Effect of copper on recombinant mouse prion protein Biochemical Society Transactions. 28: A36-A36. DOI: 10.1042/Bst028A036B |
0.346 |
|
2000 |
Gambetti P. Human prion diseases Neurobiology of Aging. 21: 280. DOI: 10.1016/S0197-4580(00)83208-X |
0.419 |
|
2000 |
Scaravilli F, Cordery RJ, Kretzschmar H, Gambetti P, Brink B, Fritz V, Temlett J, Kaplan C, Fish D, An SF, Schulz-Schaeffer WJ, Rossor MN. Sporadic fatal insomnia: A case study Annals of Neurology. 48: 665-669. DOI: 10.1002/1531-8249(200010)48:4<665::Aid-Ana15>3.0.Co;2-D |
0.387 |
|
1999 |
Morillas M, Swietnicki W, Gambetti P, Surewicz WK. Membrane environment alters the conformational structure of the recombinant human prion protein. Journal of Biological Chemistry. 274: 36859-36865. PMID 10601237 DOI: 10.1074/Jbc.274.52.36859 |
0.322 |
|
1999 |
Xu X, Shi YC, Wu X, Gambetti P, Sui D, Cui MZ. Identification of a novel PSD-95/Dlg/ZO-1 (PDZ)-like protein interacting with the C terminus of presenilin-1. Journal of Biological Chemistry. 274: 32543-32546. PMID 10551805 DOI: 10.1074/Jbc.274.46.32543 |
0.334 |
|
1999 |
Worrall BB, Herman ST, Capellari S, Lynch T, Chin S, Gambetti P, Parchi P. Type 1 protease resistant prion protein and valine homozygosity at codon 129 of PRNP identify a subtype of sporadic Creutzfeldt-Jakob disease. Journal of Neurology, Neurosurgery, and Psychiatry. 67: 671-4. PMID 10519879 DOI: 10.1136/Jnnp.67.5.671 |
0.734 |
|
1999 |
Parchi P, Giese A, Capellari S, Brown P, Schulz-Schaeffer W, Windl O, Zerr I, Budka H, Kopp N, Piccardo P, Poser S, Rojiani A, Streichemberger N, Julien J, Vital C, ... ... Gambetti P, et al. Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Annals of Neurology. 46: 224-33. PMID 10443888 DOI: 10.1002/1531-8249(199908)46:2<224::Aid-Ana12>3.0.Co;2-W |
0.748 |
|
1999 |
Zanusso G, Petersen RB, Jin T, Jing Y, Kanoush R, Ferrari S, Gambetti P, Singh N. Proteasomal degradation and N-terminal protease resistance of the codon 145 mutant prion protein. The Journal of Biological Chemistry. 274: 23396-404. PMID 10438517 DOI: 10.1074/Jbc.274.33.23396 |
0.821 |
|
1999 |
Cortelli P, Gambetti P, Montagna P, Lugaresi E. Fatal familial insomnia: clinical features and molecular genetics. Journal of Sleep Research. 8: 23-9. PMID 10389103 DOI: 10.1046/J.1365-2869.1999.00005.X |
0.576 |
|
1999 |
Parchi P, Capellari S, Chin S, Schwarz HB, Schecter NP, Butts JD, Hudkins P, Burns DK, Powers JM, Gambetti P. A subtype of sporadic prion disease mimicking fatal familial insomnia. Neurology. 52: 1757-63. PMID 10371520 DOI: 10.1212/Wnl.52.9.1757 |
0.757 |
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1999 |
Hainfellner JA, Parchi P, Kitamoto T, Jarius C, Gambetti P, Budka H. A novel phenotype in familial Creutzfeldt-Jakob disease: prion protein gene E200K mutation coupled with valine at codon 129 and type 2 protease-resistant prion protein. Annals of Neurology. 45: 812-6. PMID 10360778 DOI: 10.1002/1531-8249(199906)45:6<812::Aid-Ana20>3.0.Co;2-2 |
0.631 |
|
1999 |
Gambetti P, Parchi P. Insomnia in prion diseases: sporadic and familial. The New England Journal of Medicine. 340: 1675-7. PMID 10341282 DOI: 10.1056/Nejm199905273402111 |
0.575 |
|
1999 |
Gambetti P, Petersen RB, Parchi P, Chen SG, Capellari S, Goldfarb L, Gabizon R, Montagna P, Lugaresi E, Piccardo P, Ghetti B. 13 Inherited Prion Diseases Cold Spring Harbor Monograph Archive. 38: 509-583. DOI: 10.1101/087969547.38.509 |
0.81 |
|
1999 |
Gold M, Rojiani AM, Parchi P, Gambetti P, Gibbs CJ, Kenney K. SPORADIC CREUTZFELDT-JAKOB DISEASE (sCJD) - A SOUTHWEST FLORIDA EXPERIENCE Journal of Neuropathology and Experimental Neurology. 58: 552. DOI: 10.1097/00005072-199905000-00182 |
0.592 |
|
1999 |
Ghetti B, Gambetti P. Chapter 5 Human Prion Diseases Advances in Cell Aging and Gerontology. 3: 135-187. DOI: 10.1016/S1566-3124(08)60025-5 |
0.498 |
|
1998 |
Gambetti P, Russo C. Human brain amyloidoses Nephrology Dialysis Transplantation. 13: 33-40. PMID 9870435 DOI: 10.1093/Ndt/13.Suppl_7.33 |
0.581 |
|
1998 |
Russo C, Angelini G, Dapino D, Piccini A, Piombo G, Schettini G, Chen S, Teller JK, Zaccheo D, Gambetti P, Tabaton M. Opposite roles of apolipoprotein E in normal brains and in Alzheimer's disease. Proceedings of the National Academy of Sciences of the United States of America. 95: 15598-602. PMID 9861015 DOI: 10.1073/Pnas.95.26.15598 |
0.751 |
|
1998 |
Padovani A, D'Alessandro M, Parchi P, Cortelli P, Anzola GP, Montagna P, Vignolo LA, Petraroli R, Pocchiari M, Lugaresi E, Gambetti P. Fatal familial insomnia in a new Italian kindred. Neurology. 51: 1491-4. PMID 9818894 DOI: 10.1212/Wnl.51.5.1491 |
0.683 |
|
1998 |
Swietnicki W, Petersen RB, Gambetti P, Surewicz WK. Familial mutations and the thermodynamic stability of the recombinant human prion protein. The Journal of Biological Chemistry. 273: 31048-52. PMID 9813003 DOI: 10.1074/Jbc.273.47.31048 |
0.641 |
|
1998 |
Zanusso G, Liu D, Ferrari S, Hegyi I, Yin X, Aguzzi A, Hornemann S, Liemann S, Glockshuber R, Manson JC, Brown P, Petersen RB, Gambetti P, Sy MS. Prion protein expression in different species: analysis with a panel of new mAbs. Proceedings of the National Academy of Sciences of the United States of America. 95: 8812-6. PMID 9671761 DOI: 10.1073/Pnas.95.15.8812 |
0.74 |
|
1998 |
Gambetti P, Lugaresi E. Conclusions of the symposium. Brain Pathology (Zurich, Switzerland). 8: 571-5. PMID 9669714 DOI: 10.1111/J.1750-3639.1998.Tb00185.X |
0.574 |
|
1998 |
Parchi P, Petersen RB, Chen SG, Autilio-Gambetti L, Capellari S, Monari L, Cortelli P, Montagna P, Lugaresi E, Gambetti P. Molecular pathology of fatal familial insomnia. Brain Pathology (Zurich, Switzerland). 8: 539-48. PMID 9669705 DOI: 10.1111/J.1750-3639.1998.Tb00176.X |
0.827 |
|
1998 |
Dorandeu A, Wingertsmann L, Chrétien F, Delisle MB, Vital C, Parchi P, Montagna P, Lugaresi E, Ironside JW, Budka H, Gambetti P, Gray F. Neuronal apoptosis in fatal familial insomnia. Brain Pathology (Zurich, Switzerland). 8: 531-7. PMID 9669704 DOI: 10.1111/J.1750-3639.1998.Tb00175.X |
0.648 |
|
1998 |
Lugaresi E, Tobler I, Gambetti P, Montagna P. The pathophysiology of fatal familial insomnia. Brain Pathology (Zurich, Switzerland). 8: 521-6. PMID 9669702 DOI: 10.1111/J.1750-3639.1998.Tb00173.X |
0.47 |
|
1998 |
Montagna P, Cortelli P, Avoni P, Tinuper P, Plazzi G, Gallassi R, Portaluppi F, Julien J, Vital C, Delisle MB, Gambetti P, Lugaresi E. Clinical features of fatal familial insomnia: phenotypic variability in relation to a polymorphism at codon 129 of the prion protein gene. Brain Pathology (Zurich, Switzerland). 8: 515-20. PMID 9669701 DOI: 10.1111/J.1750-3639.1998.Tb00172.X |
0.574 |
|
1998 |
Vital C, Gray F, Vital A, Parchi P, Capellari S, Petersen RB, Ferrer X, Jarnier D, Julien J, Gambetti P. Prion encephalopathy with insertion of octapeptide repeats: the number of repeats determines the type of cerebellar deposits. Neuropathology and Applied Neurobiology. 24: 125-30. PMID 9634208 DOI: 10.1046/J.1365-2990.1998.00098.X |
0.746 |
|
1998 |
Smine A, Xu X, Nishiyama K, Katada T, Gambetti P, Yadav SP, Wu X, Shi Y, Yasuhara S, Homburger V, Okamoto T. Regulation of Brain G-protein Go by Alzheimer’s Disease Gene Presenilin-1 Journal of Biological Chemistry. 273: 16281-16288. PMID 9632688 DOI: 10.1074/Jbc.273.26.16281 |
0.339 |
|
1998 |
Welch WJ, Gambetti P. Chaperoning brain diseases Nature. 392: 23-24. PMID 9510241 DOI: 10.1038/32049 |
0.45 |
|
1998 |
Mizutani T, Inose T, Nakajima S, Kakimi S, Uchigata M, Ikeda K, Gambetti P, Takasu T. Familial parkinsonism and dementia with ballooned neurons, argyrophilic neuronal inclusions, atypical neurofibrillary tangles, tau-negative astrocytic fibrillary tangles, and Lewy bodies. Acta Neuropathologica. 95: 15-27. PMID 9452818 DOI: 10.1007/S004010050761 |
0.509 |
|
1997 |
Singh N, Zanusso G, Chen SG, Fujioka H, Richardson S, Gambetti P, Petersen RB. Prion protein aggregation reverted by low temperature in transfected cells carrying a prion protein gene mutation. The Journal of Biological Chemistry. 272: 28461-70. PMID 9353306 DOI: 10.1074/Jbc.272.45.28461 |
0.835 |
|
1997 |
Swietnicki W, Petersen R, Gambetti P, Surewicz WK. pH-dependent stability and conformation of the recombinant human prion protein PrP(90-231) Journal of Biological Chemistry. 272: 27517-27520. PMID 9346881 DOI: 10.1074/Jbc.272.44.27517 |
0.572 |
|
1997 |
Chen SG, Parchi P, Brown P, Capellari S, Zou W, Cochran EJ, Vnencak-Jones CL, Julien J, Vital C, Mikol J, Lugaresi E, Autilio-Gambetti L, Gambetti P. Allelic origin of the abnormal prion protein isoform in familial prion diseases. Nature Medicine. 3: 1009-15. PMID 9288728 DOI: 10.1038/Nm0997-1009 |
0.83 |
|
1997 |
Raymond GJ, Hope J, Kocisko DA, Priola SA, Raymond LD, Bossers A, Ironside J, Will RG, Chen SG, Petersen RB, Gambetti P, Rubenstein R, Smits MA, Lansbury PT, Caughey B. Molecular assessment of the potential transmissibilities of BSE and scrapie to humans. Nature. 388: 285-8. PMID 9230438 DOI: 10.1038/40876 |
0.684 |
|
1997 |
Russo C, Saido TC, DeBusk LM, Tabaton M, Gambetti P, Teller JK. Heterogeneity of water-soluble amyloid beta-peptide in Alzheimer's disease and Down's syndrome brains. Febs Letters. 409: 411-6. PMID 9224700 DOI: 10.1016/S0014-5793(97)00564-4 |
0.708 |
|
1997 |
Gambetti P. Prion in progressive subcortical gliosis revisited Neurology. 49: 309-310. PMID 9222220 DOI: 10.1212/Wnl.49.1.309-C |
0.388 |
|
1997 |
Capellari S, Vital C, Parchi P, Petersen RB, Ferrer X, Jarnier D, Pegoraro E, Gambetti P, Julien J. Familial prion disease with a novel 144-bp insertion in the prion protein gene in a Basque family. Neurology. 49: 133-41. PMID 9222181 DOI: 10.1212/Wnl.49.1.133 |
0.801 |
|
1997 |
Cortelli P, Perani D, Parchi P, Grassi F, Montagna P, De Martin M, Castellani R, Tinuper P, Gambetti P, Lugaresi E, Fazio F. Cerebral metabolism in fatal familial insomnia: relation to duration, neuropathology, and distribution of protease-resistant prion protein. Neurology. 49: 126-33. PMID 9222180 DOI: 10.1212/Wnl.49.1.126 |
0.776 |
|
1997 |
Castellani RJ, Parchi P, Madoff L, Gambetti P, McKeever P. Biopsy diagnosis of Creutzfeldt-Jakob disease by western blot: a case report. Human Pathology. 28: 623-6. PMID 9158712 DOI: 10.1016/S0046-8177(97)90086-1 |
0.772 |
|
1996 |
Telling GC, Parchi P, DeArmond SJ, Cortelli P, Montagna P, Gabizon R, Mastrianni J, Lugaresi E, Gambetti P, Prusiner SB. Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science (New York, N.Y.). 274: 2079-82. PMID 8953038 DOI: 10.1126/Science.274.5295.2079 |
0.731 |
|
1996 |
Parchi P, Castellani R, Capellari S, Ghetti B, Young K, Chen SG, Farlow M, Dickson DW, Sima AA, Trojanowski JQ, Petersen RB, Gambetti P. Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Annals of Neurology. 39: 767-78. PMID 8651649 DOI: 10.1002/Ana.410390613 |
0.839 |
|
1996 |
Castellani R, Parchi P, Stahl J, Capellari S, Cohen M, Gambetti P. Early pathologic and biochemical changes in Creutzfeldt-Jakob disease: study of brain biopsies. Neurology. 46: 1690-3. PMID 8649571 DOI: 10.1212/Wnl.46.6.1690 |
0.787 |
|
1996 |
Petersen RB, Parchi P, Richardson SL, Urig CB, Gambetti P. Effect of the D178N mutation and the codon 129 polymorphism on the metabolism of the prion protein. The Journal of Biological Chemistry. 271: 12661-8. PMID 8647879 DOI: 10.1074/Jbc.271.21.12661 |
0.741 |
|
1996 |
LeBlanc AC, Xue R, Gambetti P. Amyloid precursor protein metabolism in primary cell cultures of neurons, astrocytes, and microglia Journal of Neurochemistry. 66: 2300-2310. PMID 8632152 DOI: 10.1046/J.1471-4159.1996.66062300.X |
0.325 |
|
1996 |
Castellani R, Smith MA, Richey PL, Kalaria R, Gambetti P, Perry G. Evidence for oxidative stress in Pick disease and corticobasal degeneration. Brain Research. 696: 268-71. PMID 8574681 DOI: 10.1016/0006-8993(95)00535-X |
0.562 |
|
1996 |
Gambetti P. Approaches to Prions: Prion Diseases. Science. 273: 1052-1053. DOI: 10.1126/Science.273.5278.1052B |
0.419 |
|
1996 |
Parchi P, Petersen RB, Gambetti P. New topics in familial prion diseases Seminars in Virology. 7: 181-187. DOI: 10.1006/Smvy.1996.0023 |
0.748 |
|
1995 |
Montagna P, Cortelli P, Gambetti P, Lugaresi E. Fatal familial insomnia: sleep, neuroendocrine and vegetative alterations. Advances in Neuroimmunology. 5: 13-21. PMID 7795890 DOI: 10.1016/0960-5428(94)00042-M |
0.492 |
|
1995 |
Gambetti P, Parchi P, Petersen RB, Chen SG, Lugaresi E. Fatal familial insomnia and familial Creutzfeldt-Jakob disease: clinical, pathological and molecular features. Brain Pathology (Zurich, Switzerland). 5: 43-51. PMID 7767490 DOI: 10.1111/J.1750-3639.1995.Tb00576.X |
0.792 |
|
1995 |
Porialuppi F, Cortelli P, Avoni P, Vergnani L, Maltoni P, Pavani A, Sforza E, Manfredini R, Montagna P, Roiter I, Gambetti P, Fersini C, Lugaresi E. Dissociated 24-Hour patterns of somatotropin and prolactin in fatal familial insomnia Neuroendocrinology. 61: 731-737. PMID 7659197 DOI: 10.1159/000126901 |
0.492 |
|
1995 |
Créange A, Gray F, Cesaro P, Adle-Biassette H, Duvoux C, Cherqui D, Bell J, Parchi P, Gambetti P, Degos JD. Creutzfeldt-Jakob disease after liver transplantation. Annals of Neurology. 38: 269-72. PMID 7654078 DOI: 10.1002/Ana.410380223 |
0.578 |
|
1995 |
Chen SG, Teplow DB, Parchi P, Teller JK, Gambetti P, Autilio-Gambetti L. Truncated forms of the human prion protein in normal brain and in prion diseases. The Journal of Biological Chemistry. 270: 19173-80. PMID 7642585 DOI: 10.1074/Jbc.270.32.19173 |
0.81 |
|
1995 |
Parchi P, Gambetti P. Human prion diseases. Current Opinion in Neurology. 8: 286-93. PMID 7582044 DOI: 10.1097/00019052-199508000-00007 |
0.623 |
|
1995 |
Bethea CL, Hess DL, Widmann AA, Henningfeld JM, Kjær A, Knigge U, Warberg J, Mena F, Aguayo D, Pacheco P, Morales MT, Portaluppi F, Cortelli P, Avoni P, Vergnani L, ... ... Gambetti P, et al. Subject Index Vol. 61, 1995 Neuroendocrinology. 61: 741-742. DOI: 10.1159/000126905 |
0.444 |
|
1995 |
Bethea CL, Hess DL, Widmann AA, Henningfeld JM, Kjær A, Knigge U, Warberg J, Mena F, Aguayo D, Pacheco P, Morales MT, Portaluppi F, Cortelli P, Avoni P, Vergnani L, ... ... Gambetti P, et al. Contents, Vol. 61, 1995 Neuroendocrinology. 61. DOI: 10.1159/000126886 |
0.413 |
|
1995 |
Créange A, Gray F, Cesaro P, Bell J, Parchi P, Gambetti P, Degos J-. CREUTZFELDT-JAKOB DISEASE AFTER LIVER TRANSPLANT Journal of Neuropathology and Experimental Neurology. 54: 449. DOI: 10.1097/00005072-199505000-00168 |
0.51 |
|
1995 |
Petersen RB, Tresser NJ, Richardson SL, Gali M, Goren H, Gambetti P. A FAMILY WITH OCULOLEPTOMENINGEAL AMYLOIDOSIS AND DEMENTIA HAS A MUTATION IN THE TRANSTHYRETIN GENE Journal of Neuropathology and Experimental Neurology. 54: 413. DOI: 10.1097/00005072-199505000-00027 |
0.735 |
|
1994 |
Leblanc AC, Gambetti P. Production of Alzheimer 4-kDa β-Amyloid Peptide Requires the C-Terminal Cytosolic Domain of the Amyloid Precursor Protein Biochemical and Biophysical Research Communications. 204: 1371-1380. PMID 7980616 DOI: 10.1006/Bbrc.1994.2615 |
0.317 |
|
1994 |
Gray F, Chrétien F, Cesaro P, Chatelain J, Beaudry P, Laplanche JL, Mikol J, Bell J, Gambetti P, Degos JD. Creutzfeldt-Jakob disease and cerebral amyloid angiopathy. Acta Neuropathologica. 88: 106-11. PMID 7941967 DOI: 10.1007/Bf00294366 |
0.381 |
|
1994 |
Lanska DJ, Currier RD, Cohen M, Gambetti P, Smith EE, Bebin J, Jackson JF, Whitehouse PJ, Markesbery WR. Familial progressive subcortical gliosis. Neurology. 44: 1633-43. PMID 7936288 DOI: 10.1212/Wnl.44.9.1633 |
0.597 |
|
1994 |
Gambetti P. Structural lesions and their relationship to Alzheimer's disease Neurobiology of Aging. 15: 101-103. PMID 7700429 DOI: 10.1016/0197-4580(94)90183-X |
0.334 |
|
1993 |
Perani D, Cortelli P, Lucignani G, Montagna P, Tinuper P, Gallassi R, Gambetti P, Lenzi GL, Lugaresi E, Fazio F. [18F]FDG PET in fatal familial insomnia: the functional effects of thalamic lesions. Neurology. 43: 2565-9. PMID 8255458 DOI: 10.1212/Wnl.43.12.2565 |
0.546 |
|
1993 |
LeBlanc A, Xue R, Gambetti P. Amyloid Protein Precursor (App) Expression And Metabolism In Human Nervous System Primary Cultures From Normal And Alzheimer Disease (Ad) Individuals Journal of Neuropathology and Experimental Neurology. 52: 333. DOI: 10.1097/00005072-199305000-00293 |
0.375 |
|
1993 |
Tabaton M, Cammarata S, Mandybur T, Richey P, Kawai M, Perry G, Gambetti P. Erratum: Senile plaques in cerebral amyloid angiopathy show accumulation of amyloid precursor protein without cytoskeletal abnormalities (Brain Research, 593: 299-303 (1992)) Brain Research. 600. DOI: 10.1016/0006-8993(93)90419-N |
0.768 |
|
1992 |
Gallassi R, Morreale A, Montagna P, Gambetti P, Lugaresi E. "Fatal familial insomnia": neuropsychological study of a disease with thalamic degeneration. Cortex; a Journal Devoted to the Study of the Nervous System and Behavior. 28: 175-87. PMID 1499304 DOI: 10.1016/S0010-9452(13)80046-9 |
0.521 |
|
1992 |
Cohen M, Lanska D, Roessmann U, Karaman B, Ganz E, Whitehouse P, Gambetti P. Amyloidoma of the CNS. I. Clinical and pathologic study. Neurology. 42: 2019-23. PMID 1407586 DOI: 10.1212/Wnl.42.10.2019 |
0.71 |
|
1992 |
Montagna P, Cortelli P, Avoni P, Marchello LP, Monari L, Tinuper P, Gambetti P, Lugaresi E. Abnormal sympathetic skin responses in thalamic lesions. Electroencephalography and Clinical Neurophysiology. 85: 225-7. PMID 1376682 DOI: 10.1016/0168-5597(92)90137-Z |
0.662 |
|
1991 |
LeBlanc AC, Chen HY, Autilio-Gambetti L, Gambetti P. Differential APP gene expression in rat cerebral cortex, meninges, and primary astroglial, microglial and neuronal cultures. Febs Letters. 292: 171-8. PMID 1959603 DOI: 10.1016/0014-5793(91)80861-V |
0.61 |
|
1991 |
Bizzi A, Schaetzle B, Patton A, Gambetti P, Autilio-Gambetti L. Axonal transport of two major components of the ubiquitin system: free ubiquitin and ubiquitin carboxyl-terminal hydrolase PGP 9.5. Brain Research. 548: 292-9. PMID 1714333 DOI: 10.1016/0006-8993(91)91135-N |
0.727 |
|
1991 |
Schiffer D, Autilio-Gambetti L, Chiò A, Gambetti P, Giordana MT, Gullotta F, Migheli A, Vigliani MC. Ubiquitin in motor neuron disease: study at the light and electron microscope. Journal of Neuropathology and Experimental Neurology. 50: 463-73. PMID 1648124 DOI: 10.1097/00005072-199107000-00007 |
0.649 |
|
1991 |
Perry G, Kawai M, Tabaton M, Onorato M, Mulvihill P, Richey P, Morandi A, Connolly J, Gambetti P. Neuropil threads of Alzheimer's disease show a marked alteration of the normal cytoskeleton The Journal of Neuroscience. 11: 1748-1755. DOI: 10.1523/Jneurosci.11-06-01748.1991 |
0.759 |
|
1990 |
Migheli A, Autilio-Gambetti L, Gambetti P, Mocellini C, Vigliani MC, Schiffer D. Ubiquitinated filamentous inclusions in spinal cord of patients with motor neuron disease. Neuroscience Letters. 114: 5-10. PMID 2166261 DOI: 10.1016/0304-3940(90)90419-A |
0.625 |
|
1990 |
Schiffer D, Autilio-Gambetti L, Chio A, Gambetti P, Giordana MT, Gullotta F, Migheli A, Vigliani MC. Immunohistochemistry And Immunoelectron Microscopy Of Ubiquitin In Als: 49 Journal of Neuropathology and Experimental Neurology. 49: 277. DOI: 10.1097/00005072-199005000-00055 |
0.576 |
|
1989 |
Monaco S, Autilio-Gambetti L, Lasek RJ, Katz MJ, Gambetti P. Experimental increase of neurofilament transport rate: decreases in neurofilament number and in axon diameter. Journal of Neuropathology and Experimental Neurology. 48: 23-32. PMID 2908896 DOI: 10.1097/00005072-198901000-00003 |
0.657 |
|
1989 |
Tabaton M, Mandybur TI, Perry G, Onorato M, Autilio-Gambetti L, Gambetti P. The widespread alteration of neurites in Alzheimer's disease may be unrelated to amyloid deposition. Annals of Neurology. 26: 771-8. PMID 2557796 DOI: 10.1002/ana.410260614 |
0.768 |
|
1988 |
Tabaton M, Perry G, Autilio-Gambetti L, Manetto V, Gambetti P. Influence of neuronal location on antigenic properties of neurofibrillary tangles. Annals of Neurology. 23: 604-10. PMID 3408241 DOI: 10.1002/ana.410230613 |
0.775 |
|
1988 |
Perry G, Lipphardt S, Mulvihill P, Kancherla M, Mijares M, Gambetti P, Sharma S, Maggiora L, Cornette J, Lobl T. Amyloid precursor protein in senile plaques of Alzheimer disease. Lancet (London, England). 2: 746. PMID 2901596 DOI: 10.1016/S0140-6736(88)90219-X |
0.608 |
|
1988 |
Manetto V, Perry G, Tabaton M, Mulvihill P, Fried VA, Smith HT, Gambetti P, Autilio-Gambetti L. Ubiquitin is associated with abnormal cytoplasmic filaments characteristic of neurodegenerative diseases. Proceedings of the National Academy of Sciences of the United States of America. 85: 4501-5. PMID 2837768 DOI: 10.1073/Pnas.85.12.4501 |
0.832 |
|
1988 |
Medori R, Autilio-Gambetti L, Jenich H, Gambetti P. Changes in axon size and slow axonal transport are related in experimental diabetic neuropathy. Neurology. 38: 597-601. PMID 2451191 DOI: 10.1212/Wnl.38.4.597 |
0.723 |
|
1988 |
Medori R, Jenich H, Autilio-Gambetti L, Gambetti P. Experimental diabetic neuropathy: similar changes of slow axonal transport and axonal size in different animal models. The Journal of Neuroscience. 8: 1814-1821. DOI: 10.1523/Jneurosci.08-05-01814.1988 |
0.725 |
|
1987 |
Perry G, Friedman R, Kang DH, Manetto V, Autilio-Gambetti L, Gambetti P. Antibodies to the neuronal cytoskeleton are elicited by Alzheimer paired helical filament fractions. Brain Research. 420: 233-42. PMID 3676758 DOI: 10.1016/0006-8993(87)91243-1 |
0.802 |
|
1987 |
Morandi A, Gambetti P, Arora PK, Sayre LM. Mechanism of neurotoxic action of beta,beta'-iminodipropionitrile (IDPN): N-hydroxylation enhances neurotoxic potency. Brain Research. 437: 69-76. PMID 3427483 DOI: 10.1016/0006-8993(87)91527-7 |
0.485 |
|
1987 |
Bertholf RL, Gambetti P. Aluminum and Alzheimer's disease: perspectives for a cytoskeletal mechanism. Critical Reviews in Clinical Laboratory Sciences. 25: 195-210. PMID 3315463 DOI: 10.3109/10408368709105882 |
0.43 |
|
1987 |
Galloway PG, Perry G, Kosik KS, Gambetti P. Hirano bodies contain tau protein. Brain Research. 403: 337-40. PMID 3103867 DOI: 10.1016/0006-8993(87)90071-0 |
0.766 |
|
1987 |
Galloway PG, Perry G, Gambetti P. Hirano body filaments contain actin and actin-associated proteins. Journal of Neuropathology and Experimental Neurology. 46: 185-99. PMID 3029338 DOI: 10.1097/00005072-198703000-00006 |
0.741 |
|
1987 |
Pappolla M, Penton R, Weiss HS, Miller CH, Sahenk Z, Autilio-Gambetti L, Gambetti P. Carbon disulfide axonopathy. Another experimental model characterized by acceleration of neurofilament transport and distinct changes of axonal size. Brain Research. 424: 272-80. PMID 2445451 DOI: 10.1016/0006-8993(87)91471-5 |
0.712 |
|
1987 |
Perry G, Mulvihill P, Manetto V, Autilio-Gambetti L, Gambetti P. Immunocytochemical properties of Alzheimer straight filaments The Journal of Neuroscience. 7: 3736-3738. DOI: 10.1523/Jneurosci.07-11-03736.1987 |
0.784 |
|
1987 |
Onorato M, Gambetti P, Kosik K, Perry G. ELECTRON MICROSCOPIC LOCALIZATION OF TAU IN ALZHEIMER NFT AND PHF. Journal of Neuropathology and Experimental Neurology. 46: 334. DOI: 10.1097/00005072-198705000-00013 |
0.49 |
|
1987 |
Galloway P, Perry G, Gambetti P. Hirano body filaments contain actin and actin-associated proteins Alzheimer Disease & Associated Disorders. 1: 207-208. DOI: 10.1097/00002093-198701030-00034 |
0.723 |
|
1986 |
Mitsumoto H, Gambetti P. Impaired slow axonal transport in wobbler mouse motor neuron disease Annals of Neurology. 19: 36-43. PMID 3947038 DOI: 10.1002/Ana.410190108 |
0.302 |
|
1986 |
Lugaresi E, Medori R, Montagna P, Baruzzi A, Cortelli P, Lugaresi A, Tinuper P, Zucconi M, Gambetti P. Fatal familial insomnia and dysautonomia with selective degeneration of thalamic nuclei. The New England Journal of Medicine. 315: 997-1003. PMID 3762620 DOI: 10.1056/Nejm198610163151605 |
0.711 |
|
1986 |
Perry G, Selkoe DJ, Block BR, Stewart D, Autilio-Gambetti L, Gambetti P. Electron microscopic localization of Alzheimer neurofibrillary tangle components recognized by an antiserum to paired helical filaments. Journal of Neuropathology and Experimental Neurology. 45: 161-8. PMID 2419516 DOI: 10.1097/00005072-198603000-00006 |
0.697 |
|
1986 |
Autilio-Gambetti L, Crane R, Gambetti P. Binding of Bodian's silver and monoclonal antibodies to defined regions of human neurofilament subunits: Bodian's silver reacts with a highly charged unique domain of neurofilaments. Journal of Neurochemistry. 46: 366-70. PMID 2416873 DOI: 10.1111/J.1471-4159.1986.Tb12977.X |
0.588 |
|
1986 |
Gambetti P, Perry G, Autilio-Gambetti L. Paired helical filaments: Do they contain neurofilament epitopes? Neurobiology of Aging. 7: 451-452. DOI: 10.1016/0197-4580(86)90066-7 |
0.694 |
|
1985 |
Perry G, Rizzuto N, Autilio-Gambetti L, Gambetti P. Paired helical filaments from Alzheimer disease patients contain cytoskeletal components. Proceedings of the National Academy of Sciences of the United States of America. 82: 3916-20. PMID 3889918 DOI: 10.1097/00002093-198701030-00023 |
0.773 |
|
1985 |
Monaco S, Autilio-Gambetti L, Zabel D, Gambetti P. Giant axonal neuropathy: acceleration of neurofilament transport in optic axons. Proceedings of the National Academy of Sciences of the United States of America. 82: 920-4. PMID 2579382 DOI: 10.1073/Pnas.82.3.920 |
0.755 |
|
1985 |
Sayre LM, Autilio-Gambetti L, Gambetti P. Pathogenesis of experimental giant neurofilamentous axonopathies: a unified hypothesis based on chemical modification of neurofilaments. Brain Research. 357: 69-83. PMID 2412663 DOI: 10.1016/0165-0173(85)90008-6 |
0.615 |
|
1984 |
Pappolla M, Monaco S, Weiss H, Miller C, Sahenk Z, Autillo-Gambetti L, Gambetti P. 38 Slow Axonal Transport In Carbon Disulfide (Cs2) Giant Axonopathy Journal of Neuropathology and Experimental Neurology. 43: 305. DOI: 10.1097/00005072-198405000-00047 |
0.543 |
|
1983 |
Ghetti B, Gambetti P. Comparative immunocytochemical characterization of neurofibrillary tangles in experimental maytansine and aluminum encephalopathies Brain Research. 276: 388-393. PMID 6354362 DOI: 10.1016/0006-8993(83)90754-0 |
0.301 |
|
1983 |
Gambetti P, Shecket G, Ghetti B, Hirano A, Dahl D. Neurofibrillary changes in human brain. An immunocytochemical study with a neurofilament antiserum. Journal of Neuropathology and Experimental Neurology. 42: 69-79. PMID 6337236 DOI: 10.1097/00005072-198301000-00006 |
0.821 |
|
1983 |
Papasozomenos SC, Autilio-Gambetti L, Gambetti P. Distribution of proteins migrating with fast axonal transport. Their relationship to smooth endoplasmic reticulum. Brain Research. 278: 232-5. PMID 6196088 DOI: 10.1016/0006-8993(83)90243-3 |
0.77 |
|
1982 |
Velasco ME, Roessmann U, Gambetti P. The presence of glial fibrillary acidic protein in the human pituitary gland. Journal of Neuropathology and Experimental Neurology. 41: 150-63. PMID 7062085 DOI: 10.1097/00005072-198203000-00005 |
0.71 |
|
1982 |
Autilio-Gambetti L, Sipple J, Sudilovsky O, Gambetti P. Intermediate filaments of Schwann cells. Journal of Neurochemistry. 38: 774-80. PMID 7035618 DOI: 10.1111/j.1471-4159.1982.tb08698.x |
0.596 |
|
1982 |
Papasozomenos SC, Yoon M, Crane R, Autilio-Gambetti L, Gambetti P. Redistribution of proteins of fast axonal transport following administration of beta,beta'-iminodipropionitrile: a quantitative autoradiographic study. The Journal of Cell Biology. 95: 672-5. PMID 6183280 DOI: 10.1083/jcb.95.2.672 |
0.767 |
|
1981 |
Papasozomenos SC, Autilio-Gambetti L, Gambetti P. Reorganization of axoplasmic organelles following beta, beta'-iminodipropionitrile administration. The Journal of Cell Biology. 91: 866-71. PMID 7199048 DOI: 10.1083/Jcb.91.3.866 |
0.76 |
|
1981 |
Autilio-Gambetti L, Velasco ME, Sipple J, Gambetti P. Immunochemical characterization of antisera to rat neurofilament subunits. Journal of Neurochemistry. 37: 1260-5. PMID 7028920 DOI: 10.1111/j.1471-4159.1981.tb04676.x |
0.708 |
|
1981 |
Gambetti P, Autilio Gambetti L, Papasozomenos SC. Bodian's silver method stains neurofilament polypeptides. Science (New York, N.Y.). 213: 1521-2. PMID 6169146 DOI: 10.1126/Science.6169146 |
0.663 |
|
1980 |
Boller F, Mizutani T, Roessmann U, Gambetti P. Parkinson disease, dementia, and Alzheimer disease: clinicopathological correlations. Annals of Neurology. 7: 329-35. PMID 7377758 DOI: 10.1002/Ana.410070408 |
0.627 |
|
1980 |
Roessmann U, Velasco ME, Sindely SD, Gambetti P. Glial fibrillary acidic protein (GFAP) in ependymal cells during development. An immunocytochemical study. Brain Research. 200: 13-21. PMID 6998542 DOI: 10.1016/0006-8993(80)91090-2 |
0.708 |
|
1980 |
Gambetti P, Roessmann U, Velasco ME. Immunofluorescence technique for rapid diagnosis of glial tumors. The American Journal of Surgical Pathology. 4: 277-80. PMID 6994513 DOI: 10.1097/00000478-198006000-00009 |
0.7 |
|
1980 |
Velasco ME, Dahl D, Roessmann U, Gambetti P. Immunohistochemical localization of glial fibrillary acidic protein in human glial neoplasms. Cancer. 45: 484-94. PMID 6243508 DOI: 10.1002/1097-0142(19800201)45:3<484::Aid-Cncr2820450312>3.0.Co;2-9 |
0.723 |
|
1980 |
Gambetti P, Autilio-Gambetti L, Peck K. Lack of glia-axon transfer of proteins in the normal optic system of goldfish. Brain Research. 200: 59-68. PMID 6158361 DOI: 10.1016/0006-8993(80)91094-X |
0.602 |
|
1980 |
Papasozomenos S, Autilio-Gambetti L, Gambetti P. 129 Axonal Transport Of Dna During Regeneration Journal of Neuropathology and Experimental Neurology. 39: 380. DOI: 10.1097/00005072-198005000-00137 |
0.578 |
|
1977 |
Peck K, Gambetti P, Autilio-Gambetti L. Glio-Axonal Transfer Of Protein In Regenerating Goldfish Optic System: 96 Journal of Neuropathology and Experimental Neurology. 36: 622. DOI: 10.1097/00005072-197705000-00112 |
0.597 |
|
1974 |
Gonatas NK, Stieber A, Gonatas J, Gambetti P, Antoine JC, Avrameas S. Ultrastructural autoradiographic detection of intracellular immunoglobulins with iodinated Fab fragments of antibody. The combined use of ultrastructural autoradiography and peroxidase cytochemistry for the detection of two antigens (double labeling). The Journal of Histochemistry and Cytochemistry : Official Journal of the Histochemistry Society. 22: 999-1009. PMID 4427074 DOI: 10.1177/22.11.999 |
0.509 |
|
1971 |
Gambetti P, DiMauro S, Baker L. Nervous system in Pompe's disease. Ultrastructure and biochemistry. Journal of Neuropathology and Experimental Neurology. 30: 412-430. PMID 5284681 DOI: 10.1097/00005072-197107000-00008 |
0.385 |
|
1969 |
Gonatas NK, Gambetti P, Tucker SH, Evangelista I, Baird HW. Cytoplasmic inclusions in juvenile amaurotic idiocy. The Journal of Pediatrics. 75: 796-805. PMID 5347429 DOI: 10.1016/S0022-3476(69)80302-1 |
0.521 |
|
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